Juvenile xantogranuloma with íris involvement

Detalhes bibliográficos
Autor(a) principal: Augusto,Karine Lustosa
Data de Publicação: 2018
Outros Autores: Freire,Bárbara Araújo Oliveira, Dietrich,Helena Luiza Douat, Torres,Virgínia Laura Lucas
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Revista Brasileira de Oftalmologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0034-72802018000600353
Resumo: Abstract Herein we report a case of juvenile xantogranuloma, an inflammatory disease more commonly diagnosed during childhood and is characterized by cutaneous and ocular manifestations. Iris is the main target, presenting as local or diffuse yellowish lesions. Iris involvement may precipitate not only glaucoma but also amblyopia. Treatment is based on corticosteroids therapy, either local or systemic aiming disease control.