Foix-Alajouanine syndrome mimicking a spinal cord tumor
Main Author: | |
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Publication Date: | 2017 |
Other Authors: | , , , |
Format: | Article |
Language: | eng |
Source: | Revista da Associação Médica Brasileira (Online) |
Download full: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564 |
Summary: | Summary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor. |
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Foix-Alajouanine syndrome mimicking a spinal cord tumordural arteriovenous fistulaFoix-Alajouanine syndromespinal cord gliomasubacute necrotizing myelopathySummary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.Associação Médica Brasileira2017-07-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564Revista da Associação Médica Brasileira v.63 n.7 2017reponame:Revista da Associação Médica Brasileira (Online)instname:Associação Médica Brasileira (AMB)instacron:AMB10.1590/1806-9282.63.07.564info:eu-repo/semantics/openAccessSalomão,RenanCanêdo,Nathalie Henriques SilvaAbrão,Guilherme P.Lima,CarlosAcioly,Marcus Andréeng2017-09-25T00:00:00Zoai:scielo:S0104-42302017000700564Revistahttps://ramb.amb.org.br/ultimas-edicoes/#https://old.scielo.br/oai/scielo-oai.php||ramb@amb.org.br1806-92820104-4230opendoar:2017-09-25T00:00Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB)false |
dc.title.none.fl_str_mv |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
title |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
spellingShingle |
Foix-Alajouanine syndrome mimicking a spinal cord tumor Salomão,Renan dural arteriovenous fistula Foix-Alajouanine syndrome spinal cord glioma subacute necrotizing myelopathy |
title_short |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
title_full |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
title_fullStr |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
title_full_unstemmed |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
title_sort |
Foix-Alajouanine syndrome mimicking a spinal cord tumor |
author |
Salomão,Renan |
author_facet |
Salomão,Renan Canêdo,Nathalie Henriques Silva Abrão,Guilherme P. Lima,Carlos Acioly,Marcus André |
author_role |
author |
author2 |
Canêdo,Nathalie Henriques Silva Abrão,Guilherme P. Lima,Carlos Acioly,Marcus André |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Salomão,Renan Canêdo,Nathalie Henriques Silva Abrão,Guilherme P. Lima,Carlos Acioly,Marcus André |
dc.subject.por.fl_str_mv |
dural arteriovenous fistula Foix-Alajouanine syndrome spinal cord glioma subacute necrotizing myelopathy |
topic |
dural arteriovenous fistula Foix-Alajouanine syndrome spinal cord glioma subacute necrotizing myelopathy |
description |
Summary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-07-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/1806-9282.63.07.564 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Associação Médica Brasileira |
publisher.none.fl_str_mv |
Associação Médica Brasileira |
dc.source.none.fl_str_mv |
Revista da Associação Médica Brasileira v.63 n.7 2017 reponame:Revista da Associação Médica Brasileira (Online) instname:Associação Médica Brasileira (AMB) instacron:AMB |
instname_str |
Associação Médica Brasileira (AMB) |
instacron_str |
AMB |
institution |
AMB |
reponame_str |
Revista da Associação Médica Brasileira (Online) |
collection |
Revista da Associação Médica Brasileira (Online) |
repository.name.fl_str_mv |
Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB) |
repository.mail.fl_str_mv |
||ramb@amb.org.br |
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1754212832801456128 |