Foix-Alajouanine syndrome mimicking a spinal cord tumor

Detalhes bibliográficos
Autor(a) principal: Salomão,Renan
Data de Publicação: 2017
Outros Autores: Canêdo,Nathalie Henriques Silva, Abrão,Guilherme P., Lima,Carlos, Acioly,Marcus André
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Revista da Associação Médica Brasileira (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564
Resumo: Summary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.
id AMB-1_a90fa76727151f53c4f8bd6e71a3f360
oai_identifier_str oai:scielo:S0104-42302017000700564
network_acronym_str AMB-1
network_name_str Revista da Associação Médica Brasileira (Online)
repository_id_str
spelling Foix-Alajouanine syndrome mimicking a spinal cord tumordural arteriovenous fistulaFoix-Alajouanine syndromespinal cord gliomasubacute necrotizing myelopathySummary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.Associação Médica Brasileira2017-07-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564Revista da Associação Médica Brasileira v.63 n.7 2017reponame:Revista da Associação Médica Brasileira (Online)instname:Associação Médica Brasileira (AMB)instacron:AMB10.1590/1806-9282.63.07.564info:eu-repo/semantics/openAccessSalomão,RenanCanêdo,Nathalie Henriques SilvaAbrão,Guilherme P.Lima,CarlosAcioly,Marcus Andréeng2017-09-25T00:00:00Zoai:scielo:S0104-42302017000700564Revistahttps://ramb.amb.org.br/ultimas-edicoes/#https://old.scielo.br/oai/scielo-oai.php||ramb@amb.org.br1806-92820104-4230opendoar:2017-09-25T00:00Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB)false
dc.title.none.fl_str_mv Foix-Alajouanine syndrome mimicking a spinal cord tumor
title Foix-Alajouanine syndrome mimicking a spinal cord tumor
spellingShingle Foix-Alajouanine syndrome mimicking a spinal cord tumor
Salomão,Renan
dural arteriovenous fistula
Foix-Alajouanine syndrome
spinal cord glioma
subacute necrotizing myelopathy
title_short Foix-Alajouanine syndrome mimicking a spinal cord tumor
title_full Foix-Alajouanine syndrome mimicking a spinal cord tumor
title_fullStr Foix-Alajouanine syndrome mimicking a spinal cord tumor
title_full_unstemmed Foix-Alajouanine syndrome mimicking a spinal cord tumor
title_sort Foix-Alajouanine syndrome mimicking a spinal cord tumor
author Salomão,Renan
author_facet Salomão,Renan
Canêdo,Nathalie Henriques Silva
Abrão,Guilherme P.
Lima,Carlos
Acioly,Marcus André
author_role author
author2 Canêdo,Nathalie Henriques Silva
Abrão,Guilherme P.
Lima,Carlos
Acioly,Marcus André
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Salomão,Renan
Canêdo,Nathalie Henriques Silva
Abrão,Guilherme P.
Lima,Carlos
Acioly,Marcus André
dc.subject.por.fl_str_mv dural arteriovenous fistula
Foix-Alajouanine syndrome
spinal cord glioma
subacute necrotizing myelopathy
topic dural arteriovenous fistula
Foix-Alajouanine syndrome
spinal cord glioma
subacute necrotizing myelopathy
description Summary Subacute necrotizing myelopathy (SNM) or Foix-Alajouanine syndrome is a rare disease characterized by progressive neurological dysfunction caused by a spinal dural arteriovenous fistula (AVF). Radiological diagnosis is usually suspected when there is intramedullary nonspecific enhancement and perimedullary flow voids. Ring-enhancement is rarely reported in the scope of AVF, which poses a diagnostic challenge and raises the suspicion of a spinal cord tumor. In such situations, biopsy can be required and delay proper diagnosis. We report the case of a patient with SNM, who underwent biopsy on the assumption of it being a spinal cord tumor.
publishDate 2017
dc.date.none.fl_str_mv 2017-07-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302017000700564
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1806-9282.63.07.564
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Associação Médica Brasileira
publisher.none.fl_str_mv Associação Médica Brasileira
dc.source.none.fl_str_mv Revista da Associação Médica Brasileira v.63 n.7 2017
reponame:Revista da Associação Médica Brasileira (Online)
instname:Associação Médica Brasileira (AMB)
instacron:AMB
instname_str Associação Médica Brasileira (AMB)
instacron_str AMB
institution AMB
reponame_str Revista da Associação Médica Brasileira (Online)
collection Revista da Associação Médica Brasileira (Online)
repository.name.fl_str_mv Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB)
repository.mail.fl_str_mv ||ramb@amb.org.br
_version_ 1754212832801456128