Disability assessment in people with sickle cell

Detalhes bibliográficos
Autor(a) principal: Borges, Carine de Lima
Data de Publicação: 2024
Outros Autores: Jesus, Gilmar Mercês de, Silva, Lea Barbetta Pereira da, Carvalho, Evanilda Souza de Santana
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista Baiana de Saúde Pública (Online)
DOI: 10.22278/2318-2660.2024.v47.n4.a3978
Texto Completo: https://rbsp.sesab.ba.gov.br/index.php/rbsp/article/view/3978
Resumo: Life expectancy of people living with sickle cell disease (SCD) is in general low and the worsening of their health condition is frequent, resulting in disabilities. However, knowledge about those disabilities based on the International Classification of Functioning, Disability and Health (ICF) is scarce. Thus, this study aimed to describe the disabilities of adults with SCD. A descriptive cross-sectional study was carried out with 60 adults with SCD of both sexes. Sociodemographic and clinical factors related to the type of SCD were self-reported by the participants. Disabilities were assessed by the World Health Organization Disability Assessment Schedule (WHODAS 2.0), in the following domains: cognition, mobility, selfcare, getting along with people, life activities, and participation in society. In each domain, disability was defined when the participant self-reported light, moderate, severe, extreme difficulty, or inability to perform the task. Data analysis included descriptive statistics (relative frequencies). The results showed high values in all domains evaluated, with emphasis on difficulties on concentrating (90%) and performing household chores (93.3%) and on the impact of health condition on subject/family’s financial situation (96.7%). The data from this study shows that adults with SCD present high disability levels, especially on the cognitive domain, on life activities, and on social participation.
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spelling Disability assessment in people with sickle cell Evaluación de la discapacidad en personas con enfermedad de células falciformes Avaliação de incapacidade em pessoas com doença falciformePessoas com IncapacidadesAdultosDoença FalciformeDoença FalciformeAvaliação de incapacidadeFuncionalidadeCIFPersonas con DiscapacidadAdultosEnfermedad de Células Falciformesenfermedad de Células Falciformesevaluación de discapacidadfuncionalidadC.I.F.Disabled PersonsAdultsSickle Cell Diseasesickle cell diseasedisability assessmentFunctionalityICFLife expectancy of people living with sickle cell disease (SCD) is in general low and the worsening of their health condition is frequent, resulting in disabilities. However, knowledge about those disabilities based on the International Classification of Functioning, Disability and Health (ICF) is scarce. Thus, this study aimed to describe the disabilities of adults with SCD. A descriptive cross-sectional study was carried out with 60 adults with SCD of both sexes. Sociodemographic and clinical factors related to the type of SCD were self-reported by the participants. Disabilities were assessed by the World Health Organization Disability Assessment Schedule (WHODAS 2.0), in the following domains: cognition, mobility, selfcare, getting along with people, life activities, and participation in society. In each domain, disability was defined when the participant self-reported light, moderate, severe, extreme difficulty, or inability to perform the task. Data analysis included descriptive statistics (relative frequencies). The results showed high values in all domains evaluated, with emphasis on difficulties on concentrating (90%) and performing household chores (93.3%) and on the impact of health condition on subject/family’s financial situation (96.7%). The data from this study shows that adults with SCD present high disability levels, especially on the cognitive domain, on life activities, and on social participation.Las personas con enfermedad de células falciformes (ECF) tienen una baja esperanza de vida, y el empeoramiento de su estado de salud es frecuente, generando discapacidades. Sin embargo, estas discapacidades son poco conocidas según la Clasificación Internacional del Funcionamiento, de la Discapacidad y de la Salud (CIF). El objetivo de este estudio fue describir las discapacidades de adultos con ECF . Se realizó un estudio transversal, descriptivo, con 60 adultos con ECF, de ambos sexos. Los factores sociodemográficos y clínicos relacionados con el tipo de ECF fueron autoinformados. Las discapacidades se evaluaron mediante la Escala de Evaluación de la Discapacidad de la Organización Mundial de la Salud (WHODAS 2.0), en los dominios de cognición, movilidad, autocuidado, convivencia con personas, actividades de la vida y participación en la sociedad. La discapacidad se definió mediante un reporte de dificultad o incapacidad leve, moderada, grave, extrema del individuo para realizar una tarea. Los datos fueron analizados por estadística descriptiva (frecuencias relativas). Los resultados mostraron altos valores de discapacidad en todos los dominios evaluados, con énfasis en las dificultades de concentración (90%), el desempeño en las tareas domésticas (93,3%) y el impacto de la situación de salud en las finanzas del sujeto/familia (96,7%). Los datos de este estudio mostraron que los adultos con ECF tienen altas tasas de discapacidad, especialmente en los dominios cognitivo, actividades de la vida y participación social.A expectativa de vida das pessoas com doença falciforme (DF) é baixa, e o agravamento da condição de saúde é frequente, gerando incapacidades. Todavia, pouco é conhecido sobre tais incapacidades com base na Classificação Internacional de Funcionalidade, Incapacidade e Saúde (CIF). Assim, o objetivo do estudo foi descrever as incapacidades de adultos com DF. Realizou-se um estudo transversal descritivo, com 60 adultos com DF, de ambos os sexos. Informações sociodemográficas, fatores clínicos relacionados ao tipo de DF foram autorreferidos pelos participantes. As incapacidades foram avaliadas por meio da Escala de Avaliação de Incapacidade da Organização Mundial da Saúde (WHODAS 2.0) nos seguintes domínios: cognição, mobilidade, autocuidado, relações interpessoais (convivência com as pessoas), atividades de vida e participação na sociedade. Em cada domínio, foi definida incapacidade quando o sujeito relatou dificuldade leve, moderada, grave ou extrema de desempenhar a tarefa. Os dados foram analisados por estatística descritiva (frequências relativas). Os resultados mostraram valores elevados em todos os domínios avaliados, com destaque para dificuldades de concentração (90%) e desempenho nas tarefas domésticas (93,3%) e impacto da situação de saúde nas finanças do sujeito/família (96,7%). Os dados deste estudo mostraram que adultos com DF apresentam elevados índices de incapacidade, especialmente no domínio cognitivo, nas atividades de vida e na participação social.SESAB2024-04-02info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rbsp.sesab.ba.gov.br/index.php/rbsp/article/view/397810.22278/2318-2660.2024.v47.n4.a3978Revista Baiana de Saúde Pública; v. 47 n. 4 (2023); 81-982318-26600100-023310.22278/2318-2660.2024.v47.N4reponame:Revista Baiana de Saúde Pública (Online)instname:Secretaria da Saúde do Estado da Bahia (Sesab)instacron:IBICTporhttps://rbsp.sesab.ba.gov.br/index.php/rbsp/article/view/3978/3280Copyright (c) 2024 Revista Baiana de Saúde Públicainfo:eu-repo/semantics/openAccessBorges, Carine de Lima Jesus, Gilmar Mercês de Silva, Lea Barbetta Pereira daCarvalho, Evanilda Souza de Santana2024-04-02T13:52:28Zoai:ojs.pkp.sfu.ca:article/3978Revistahttps://rbsp.sesab.ba.gov.br/index.php/rbspPUBhttps://rbsp.sesab.ba.gov.br/index.php/rbsp/oai||saude.revista@saude.ba.gov.br|| rbsp.saude@saude.ba.gov.br2318-26600100-0233opendoar:2024-04-02T13:52:28Revista Baiana de Saúde Pública (Online) - Secretaria da Saúde do Estado da Bahia (Sesab)false
dc.title.none.fl_str_mv Disability assessment in people with sickle cell
Evaluación de la discapacidad en personas con enfermedad de células falciformes
Avaliação de incapacidade em pessoas com doença falciforme
title Disability assessment in people with sickle cell
spellingShingle Disability assessment in people with sickle cell
Disability assessment in people with sickle cell
Borges, Carine de Lima
Pessoas com Incapacidades
Adultos
Doença Falciforme
Doença Falciforme
Avaliação de incapacidade
Funcionalidade
CIF
Personas con Discapacidad
Adultos
Enfermedad de Células Falciformes
enfermedad de Células Falciformes
evaluación de discapacidad
funcionalidad
C.I.F.
Disabled Persons
Adults
Sickle Cell Disease
sickle cell disease
disability assessment
Functionality
ICF
Borges, Carine de Lima
Pessoas com Incapacidades
Adultos
Doença Falciforme
Doença Falciforme
Avaliação de incapacidade
Funcionalidade
CIF
Personas con Discapacidad
Adultos
Enfermedad de Células Falciformes
enfermedad de Células Falciformes
evaluación de discapacidad
funcionalidad
C.I.F.
Disabled Persons
Adults
Sickle Cell Disease
sickle cell disease
disability assessment
Functionality
ICF
title_short Disability assessment in people with sickle cell
title_full Disability assessment in people with sickle cell
title_fullStr Disability assessment in people with sickle cell
Disability assessment in people with sickle cell
title_full_unstemmed Disability assessment in people with sickle cell
Disability assessment in people with sickle cell
title_sort Disability assessment in people with sickle cell
author Borges, Carine de Lima
author_facet Borges, Carine de Lima
Borges, Carine de Lima
Jesus, Gilmar Mercês de
Silva, Lea Barbetta Pereira da
Carvalho, Evanilda Souza de Santana
Jesus, Gilmar Mercês de
Silva, Lea Barbetta Pereira da
Carvalho, Evanilda Souza de Santana
author_role author
author2 Jesus, Gilmar Mercês de
Silva, Lea Barbetta Pereira da
Carvalho, Evanilda Souza de Santana
author2_role author
author
author
dc.contributor.author.fl_str_mv Borges, Carine de Lima
Jesus, Gilmar Mercês de
Silva, Lea Barbetta Pereira da
Carvalho, Evanilda Souza de Santana
dc.subject.por.fl_str_mv Pessoas com Incapacidades
Adultos
Doença Falciforme
Doença Falciforme
Avaliação de incapacidade
Funcionalidade
CIF
Personas con Discapacidad
Adultos
Enfermedad de Células Falciformes
enfermedad de Células Falciformes
evaluación de discapacidad
funcionalidad
C.I.F.
Disabled Persons
Adults
Sickle Cell Disease
sickle cell disease
disability assessment
Functionality
ICF
topic Pessoas com Incapacidades
Adultos
Doença Falciforme
Doença Falciforme
Avaliação de incapacidade
Funcionalidade
CIF
Personas con Discapacidad
Adultos
Enfermedad de Células Falciformes
enfermedad de Células Falciformes
evaluación de discapacidad
funcionalidad
C.I.F.
Disabled Persons
Adults
Sickle Cell Disease
sickle cell disease
disability assessment
Functionality
ICF
description Life expectancy of people living with sickle cell disease (SCD) is in general low and the worsening of their health condition is frequent, resulting in disabilities. However, knowledge about those disabilities based on the International Classification of Functioning, Disability and Health (ICF) is scarce. Thus, this study aimed to describe the disabilities of adults with SCD. A descriptive cross-sectional study was carried out with 60 adults with SCD of both sexes. Sociodemographic and clinical factors related to the type of SCD were self-reported by the participants. Disabilities were assessed by the World Health Organization Disability Assessment Schedule (WHODAS 2.0), in the following domains: cognition, mobility, selfcare, getting along with people, life activities, and participation in society. In each domain, disability was defined when the participant self-reported light, moderate, severe, extreme difficulty, or inability to perform the task. Data analysis included descriptive statistics (relative frequencies). The results showed high values in all domains evaluated, with emphasis on difficulties on concentrating (90%) and performing household chores (93.3%) and on the impact of health condition on subject/family’s financial situation (96.7%). The data from this study shows that adults with SCD present high disability levels, especially on the cognitive domain, on life activities, and on social participation.
publishDate 2024
dc.date.none.fl_str_mv 2024-04-02
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10.22278/2318-2660.2024.v47.n4.a3978
url https://rbsp.sesab.ba.gov.br/index.php/rbsp/article/view/3978
identifier_str_mv 10.22278/2318-2660.2024.v47.n4.a3978
dc.language.iso.fl_str_mv por
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dc.relation.none.fl_str_mv https://rbsp.sesab.ba.gov.br/index.php/rbsp/article/view/3978/3280
dc.rights.driver.fl_str_mv Copyright (c) 2024 Revista Baiana de Saúde Pública
info:eu-repo/semantics/openAccess
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eu_rights_str_mv openAccess
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dc.publisher.none.fl_str_mv SESAB
publisher.none.fl_str_mv SESAB
dc.source.none.fl_str_mv Revista Baiana de Saúde Pública; v. 47 n. 4 (2023); 81-98
2318-2660
0100-0233
10.22278/2318-2660.2024.v47.N4
reponame:Revista Baiana de Saúde Pública (Online)
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instacron_str IBICT
institution IBICT
reponame_str Revista Baiana de Saúde Pública (Online)
collection Revista Baiana de Saúde Pública (Online)
repository.name.fl_str_mv Revista Baiana de Saúde Pública (Online) - Secretaria da Saúde do Estado da Bahia (Sesab)
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dc.identifier.doi.none.fl_str_mv 10.22278/2318-2660.2024.v47.n4.a3978