METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA

Detalhes bibliográficos
Autor(a) principal: Pereira, Neide
Data de Publicação: 2013
Outros Autores: Brinca, Ana, Tellechea, Óscar, Gonçalo, Margarida
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.29021/spdv.70.3.19
Resumo: Introduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary.
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spelling METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMAPLASMOCITOMA CUTÂNEO METASTÁTICO EM DOENTE COM MIELOMA MÚLTIPLOIntroduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary.Introdução: No mieloma múltiplo as lesões cutâneas são raras e ocorrem em fases tardias da doença, como um reflexo da elevada carga tumoral. Caso clínico: Os autores relatam o caso de uma doente de 66 anos com mieloma múltiplo IgG lambda que, após 16 meses de evolução e aparentemente sob controlo hematológico, desenvolveu uma placa eritemato-violácea, dolorosa e de consistência dura, atingindo a face posterior da coxa direita. A biopsia cutânea confirmou o diagnóstico de plasmocitoma cutâneo. Radioterapia local induziu regressão completa da lesão cutânea, no entanto a doente faleceu 4 meses depois. Discussão: O plasmocitoma cutâneo secundário surge habitualmente por contiguidade a partir de lesões ósseas subjacentes, manifesta-se por placas ou nódulos eritemato-violáceos infiltrados, são extremamente raros e indicam um prognóstico desfavorável como no nosso caso. A apresentação da lesão como erisipela-like sem doença óssea subjacente é ainda mais raro.PALAVRAS-CHAVE – Mieloma múltiplo; Plasmacitoma; Neoplasias da pele.Sociedade Portuguesa de Dermatologia e Venereologia2013-01-13T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.70.3.19oai:ojs.revista.spdv.com.pt:article/19Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 3 (2012): Julho - Setembro; 387Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 3 (2012): Julho - Setembro; 3872182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/19https://doi.org/10.29021/spdv.70.3.19https://revista.spdv.com.pt/index.php/spdv/article/view/19/19Pereira, NeideBrinca, AnaTellechea, ÓscarGonçalo, Margaridainfo:eu-repo/semantics/openAccess2022-10-06T12:34:35Zoai:ojs.revista.spdv.com.pt:article/19Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:10:37.541866Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
PLASMOCITOMA CUTÂNEO METASTÁTICO EM DOENTE COM MIELOMA MÚLTIPLO
title METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
spellingShingle METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
Pereira, Neide
title_short METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
title_full METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
title_fullStr METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
title_full_unstemmed METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
title_sort METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
author Pereira, Neide
author_facet Pereira, Neide
Brinca, Ana
Tellechea, Óscar
Gonçalo, Margarida
author_role author
author2 Brinca, Ana
Tellechea, Óscar
Gonçalo, Margarida
author2_role author
author
author
dc.contributor.author.fl_str_mv Pereira, Neide
Brinca, Ana
Tellechea, Óscar
Gonçalo, Margarida
description Introduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary.
publishDate 2013
dc.date.none.fl_str_mv 2013-01-13T00:00:00Z
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https://doi.org/10.29021/spdv.70.3.19
https://revista.spdv.com.pt/index.php/spdv/article/view/19/19
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publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
dc.source.none.fl_str_mv Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 3 (2012): Julho - Setembro; 387
Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 3 (2012): Julho - Setembro; 387
2182-2409
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