METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA
Autor(a) principal: | |
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Data de Publicação: | 2013 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.29021/spdv.70.3.19 |
Resumo: | Introduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary. |
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METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMAPLASMOCITOMA CUTÂNEO METASTÁTICO EM DOENTE COM MIELOMA MÚLTIPLOIntroduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary.Introdução: No mieloma múltiplo as lesões cutâneas são raras e ocorrem em fases tardias da doença, como um reflexo da elevada carga tumoral. Caso clínico: Os autores relatam o caso de uma doente de 66 anos com mieloma múltiplo IgG lambda que, após 16 meses de evolução e aparentemente sob controlo hematológico, desenvolveu uma placa eritemato-violácea, dolorosa e de consistência dura, atingindo a face posterior da coxa direita. A biopsia cutânea confirmou o diagnóstico de plasmocitoma cutâneo. Radioterapia local induziu regressão completa da lesão cutânea, no entanto a doente faleceu 4 meses depois. Discussão: O plasmocitoma cutâneo secundário surge habitualmente por contiguidade a partir de lesões ósseas subjacentes, manifesta-se por placas ou nódulos eritemato-violáceos infiltrados, são extremamente raros e indicam um prognóstico desfavorável como no nosso caso. A apresentação da lesão como erisipela-like sem doença óssea subjacente é ainda mais raro.PALAVRAS-CHAVE – Mieloma múltiplo; Plasmacitoma; Neoplasias da pele.Sociedade Portuguesa de Dermatologia e Venereologia2013-01-13T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.70.3.19oai:ojs.revista.spdv.com.pt:article/19Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 3 (2012): Julho - Setembro; 387Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 3 (2012): Julho - Setembro; 3872182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/19https://doi.org/10.29021/spdv.70.3.19https://revista.spdv.com.pt/index.php/spdv/article/view/19/19Pereira, NeideBrinca, AnaTellechea, ÓscarGonçalo, Margaridainfo:eu-repo/semantics/openAccess2022-10-06T12:34:35Zoai:ojs.revista.spdv.com.pt:article/19Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:10:37.541866Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA PLASMOCITOMA CUTÂNEO METASTÁTICO EM DOENTE COM MIELOMA MÚLTIPLO |
title |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
spellingShingle |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA Pereira, Neide |
title_short |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
title_full |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
title_fullStr |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
title_full_unstemmed |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
title_sort |
METASTATIC CUTANEOUS PLASMOCYTOMA IN A PATIENT WITH MULTIPLE MYELOMA |
author |
Pereira, Neide |
author_facet |
Pereira, Neide Brinca, Ana Tellechea, Óscar Gonçalo, Margarida |
author_role |
author |
author2 |
Brinca, Ana Tellechea, Óscar Gonçalo, Margarida |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Pereira, Neide Brinca, Ana Tellechea, Óscar Gonçalo, Margarida |
description |
Introduction: In multiple myeloma, the cutaneous lesions are rare and usually occur in late stages of MM as a reflection of increased tumour cell burden. Case report: The authors present the case of a 66 year-old woman with IgG lambda multiple myeloma that, after 16 months and apparently under control haematological, developed a tender and firm erythemato-violaceous plaque, on the back of the right thigh. A diagnosis of cutaneous plasmocytoma was confirmed by skin biopsy. Local radiotherapy induced a complete regression of skin lesion, but the patient died 4 months later, duo to uncontrolled multiple myeloma. Discussion: Secondary cutaneous plasmocytoma usually arise from direct spread from underlying bone, manifest as erythematous to violaceous infiltrated nodules or plaques, are extremely rare and indicate a poor prognosis, as in our case. The presentation as an erysipela-like lesion with no underlying bone disease is even rarer.KEYWORDS – Multiple myeloma; Plasmacytoma; Skin neoplasms/secondary. |
publishDate |
2013 |
dc.date.none.fl_str_mv |
2013-01-13T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.70.3.19 oai:ojs.revista.spdv.com.pt:article/19 |
url |
https://doi.org/10.29021/spdv.70.3.19 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/19 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/19 https://doi.org/10.29021/spdv.70.3.19 https://revista.spdv.com.pt/index.php/spdv/article/view/19/19 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 70 No 3 (2012): Julho - Setembro; 387 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 70 n. 3 (2012): Julho - Setembro; 387 2182-2409 2182-2395 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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