Caroli’s syndrome and peritoneal carcinomatosis

Detalhes bibliográficos
Autor(a) principal: Fornari, Fernando
Data de Publicação: 2022
Outros Autores: P. Breyer, Helenice, L. Waechter, Fábio, T. Cerski, Carlos, F. Francisconi, Carlos, Magüilnik, Ismael, R. Alvares-da-Silva, Mário, M. Pereira-Lima, Luis, R. da Silveira, Themis, G.S. Barros, Sérgio
Tipo de documento: Artigo
Idioma: por
Título da fonte: Clinical and Biomedical Research
Texto Completo: https://seer.ufrgs.br/index.php/hcpa/article/view/125025
Resumo: Caroli’s syndrome is an uncommon disease, and it is characterized by the presenceof cystic dilation of the intrahepatic biliary tree, and of congenital fibrosis. It may act asa premalignant condition, and in some cases it may develop into cholangiocarcinoma.We report a case of Caroli’s syndrome that was diagnosed in a 37 year old male, andwich was diagnosed along with the development of peritoneal carcinomatosis ofunknown origin. The relevant literature is reviewed as well.
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spelling Caroli’s syndrome and peritoneal carcinomatosisSíndrome de Caroli e carcinomatose peritonealCaroli’s syndromecholangiocarcinomaperitoneal carcinomatosisSíndrome de carolicolangiocarcinomacarcinomatose peritoneaCaroli’s syndrome is an uncommon disease, and it is characterized by the presenceof cystic dilation of the intrahepatic biliary tree, and of congenital fibrosis. It may act asa premalignant condition, and in some cases it may develop into cholangiocarcinoma.We report a case of Caroli’s syndrome that was diagnosed in a 37 year old male, andwich was diagnosed along with the development of peritoneal carcinomatosis ofunknown origin. The relevant literature is reviewed as well.A Síndrome de Caroli é uma entidade incomum caracterizada pela presença dedilatações císticas da árvore biliar intra-hepática e fibrose hepática congênita. Podecomportar-se como condição pré-maligna, evoluindo em alguns casos paracolangiocarcinoma. Relatamos um caso diagnosticado em paciente do sexo masculinode 37 anos de idade, complicado por carcinomatose peritoneal de sítio desconhecidoe revisamos a literatura.HCPA/FAMED/UFRGS2022-06-02info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed ArticleAvaliado por paresapplication/pdfhttps://seer.ufrgs.br/index.php/hcpa/article/view/125025Clinical & Biomedical Research; Vol. 18 No. 3 (1998): Periodical HCPAClinical and Biomedical Research; v. 18 n. 3 (1998): Revista HCPA2357-9730reponame:Clinical and Biomedical Researchinstname:Universidade Federal do Rio Grande do Sul (UFRGS)instacron:UFRGSporhttps://seer.ufrgs.br/index.php/hcpa/article/view/125025/85103http://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessFornari, Fernando P. Breyer, Helenice L. Waechter, Fábio T. Cerski, Carlos F. Francisconi, Carlos Magüilnik, Ismael R. Alvares-da-Silva, Mário M. Pereira-Lima, Luis R. da Silveira, Themis G.S. Barros, Sérgio 2022-09-16T16:32:29Zoai:seer.ufrgs.br:article/125025Revistahttps://www.seer.ufrgs.br/index.php/hcpaPUBhttps://seer.ufrgs.br/index.php/hcpa/oai||cbr@hcpa.edu.br2357-97302357-9730opendoar:2022-09-16T16:32:29Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)false
dc.title.none.fl_str_mv Caroli’s syndrome and peritoneal carcinomatosis
Síndrome de Caroli e carcinomatose peritoneal
title Caroli’s syndrome and peritoneal carcinomatosis
spellingShingle Caroli’s syndrome and peritoneal carcinomatosis
Fornari, Fernando
Caroli’s syndrome
cholangiocarcinoma
peritoneal carcinomatosis
Síndrome de caroli
colangiocarcinoma
carcinomatose peritonea
title_short Caroli’s syndrome and peritoneal carcinomatosis
title_full Caroli’s syndrome and peritoneal carcinomatosis
title_fullStr Caroli’s syndrome and peritoneal carcinomatosis
title_full_unstemmed Caroli’s syndrome and peritoneal carcinomatosis
title_sort Caroli’s syndrome and peritoneal carcinomatosis
author Fornari, Fernando
author_facet Fornari, Fernando
P. Breyer, Helenice
L. Waechter, Fábio
T. Cerski, Carlos
F. Francisconi, Carlos
Magüilnik, Ismael
R. Alvares-da-Silva, Mário
M. Pereira-Lima, Luis
R. da Silveira, Themis
G.S. Barros, Sérgio
author_role author
author2 P. Breyer, Helenice
L. Waechter, Fábio
T. Cerski, Carlos
F. Francisconi, Carlos
Magüilnik, Ismael
R. Alvares-da-Silva, Mário
M. Pereira-Lima, Luis
R. da Silveira, Themis
G.S. Barros, Sérgio
author2_role author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Fornari, Fernando
P. Breyer, Helenice
L. Waechter, Fábio
T. Cerski, Carlos
F. Francisconi, Carlos
Magüilnik, Ismael
R. Alvares-da-Silva, Mário
M. Pereira-Lima, Luis
R. da Silveira, Themis
G.S. Barros, Sérgio
dc.subject.por.fl_str_mv Caroli’s syndrome
cholangiocarcinoma
peritoneal carcinomatosis
Síndrome de caroli
colangiocarcinoma
carcinomatose peritonea
topic Caroli’s syndrome
cholangiocarcinoma
peritoneal carcinomatosis
Síndrome de caroli
colangiocarcinoma
carcinomatose peritonea
description Caroli’s syndrome is an uncommon disease, and it is characterized by the presenceof cystic dilation of the intrahepatic biliary tree, and of congenital fibrosis. It may act asa premalignant condition, and in some cases it may develop into cholangiocarcinoma.We report a case of Caroli’s syndrome that was diagnosed in a 37 year old male, andwich was diagnosed along with the development of peritoneal carcinomatosis ofunknown origin. The relevant literature is reviewed as well.
publishDate 2022
dc.date.none.fl_str_mv 2022-06-02
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed Article
Avaliado por pares
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/125025
url https://seer.ufrgs.br/index.php/hcpa/article/view/125025
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://seer.ufrgs.br/index.php/hcpa/article/view/125025/85103
dc.rights.driver.fl_str_mv http://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv http://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv HCPA/FAMED/UFRGS
publisher.none.fl_str_mv HCPA/FAMED/UFRGS
dc.source.none.fl_str_mv Clinical & Biomedical Research; Vol. 18 No. 3 (1998): Periodical HCPA
Clinical and Biomedical Research; v. 18 n. 3 (1998): Revista HCPA
2357-9730
reponame:Clinical and Biomedical Research
instname:Universidade Federal do Rio Grande do Sul (UFRGS)
instacron:UFRGS
instname_str Universidade Federal do Rio Grande do Sul (UFRGS)
instacron_str UFRGS
institution UFRGS
reponame_str Clinical and Biomedical Research
collection Clinical and Biomedical Research
repository.name.fl_str_mv Clinical and Biomedical Research - Universidade Federal do Rio Grande do Sul (UFRGS)
repository.mail.fl_str_mv ||cbr@hcpa.edu.br
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