Oral manifestations of primary hyperoxaluria in adult patient
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Research, Society and Development |
Texto Completo: | https://rsdjournal.org/index.php/rsd/article/view/15432 |
Resumo: | Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations. |
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Oral manifestations of primary hyperoxaluria in adult patientManifestaciones orales de la hiperoxaluria primaria en paciente adultaManifestação oral da hiperoxalúria primária em paciente adultoHyperoxaluriaOxalatesTransplantsTherapeutics.HiperoxaluriaOxalatosTransplantesTerapéutica.HiperoxalúriaOxalatosTransplantesTerapêutica.Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations.La hiperoxaluria primaria (HP) es una enfermedad rara, un trastorno hereditario autosómico recesivo. Esta enfermedad conduce a la sobreproducción de oxalatos y la incapacidad de excreción da como resultado el depósito de cristales de oxalato de calcio en casi todos los tejidos que presentan la condición de oxalosis. El tratamiento es un trasplante combinado de hígado y riñón (TCHR), que permite una mejor supervivencia del paciente. Debido a esta supervivencia los pacientes pudieron presentar diversas manifestaciones bucales como enfermedad periodontal, reabsorción radicular, dolor dentario y aumento de la movilidad dentaria. Sin embargo, hasta la fecha, existe una falta de información en la literatura sobre todas las manifestaciones bucales que puede presentar este paciente. Además de esto, tengo una duda y un desafío sobre los tratamientos a este paciente en estas diferentes manifestaciones orales. El presente estudio tiene como objetivo reportar el caso de un paciente con hiperoxaluria tipo I con manifestaciones orales de oxalosis.A hiperoxalúria primária (HP) é uma doença rara de herança autossômica recessiva. Essa doença leva à superprodução de oxalatos, e a incapacidade de excreção resulta na deposição de cristais de oxalato de cálcio em quase todos os tecidos que apresentam a condição de oxalose. O tratamento é o transplante combinado de fígado e rim (TCFR), que permite melhor sobrevida do paciente. Devido a esta sobrevida os pacientes puderam apresentar diversas manifestações bucais como doença periodontal, reabsorção radicular, dor dentária e aumento da mobilidade dentária. Porém, até o momento, faltam informações na literatura sobre todas as manifestações orais que esse paciente pode apresentar. Ao lado disso temos uma dúvida e um desafio quanto aos tratamentos a esse paciente nessas diferentes manifestações orais. O presente trabalho tem como objetivo relatar um caso de uma paciente com hiperoxalúria tipo I, apresentando manifestações orais de oxalose.Research, Society and Development2021-05-21info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/1543210.33448/rsd-v10i6.15432Research, Society and Development; Vol. 10 No. 6; e8310615432Research, Society and Development; Vol. 10 Núm. 6; e8310615432Research, Society and Development; v. 10 n. 6; e83106154322525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIenghttps://rsdjournal.org/index.php/rsd/article/view/15432/14448Copyright (c) 2021 Marina Sena Lopes da Silva Sacchetto; Maísa Pereira da Silva; Roberta da Silva D'Alessandro Tonello; Wagner Henriques de Castrohttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessSacchetto, Marina Sena Lopes da SilvaSilva, Maísa Pereira daTonello, Roberta da Silva D'Alessandro Castro, Wagner Henriques de2021-06-10T22:51:46Zoai:ojs.pkp.sfu.ca:article/15432Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:36:15.382176Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false |
dc.title.none.fl_str_mv |
Oral manifestations of primary hyperoxaluria in adult patient Manifestaciones orales de la hiperoxaluria primaria en paciente adulta Manifestação oral da hiperoxalúria primária em paciente adulto |
title |
Oral manifestations of primary hyperoxaluria in adult patient |
spellingShingle |
Oral manifestations of primary hyperoxaluria in adult patient Sacchetto, Marina Sena Lopes da Silva Hyperoxaluria Oxalates Transplants Therapeutics. Hiperoxaluria Oxalatos Transplantes Terapéutica. Hiperoxalúria Oxalatos Transplantes Terapêutica. |
title_short |
Oral manifestations of primary hyperoxaluria in adult patient |
title_full |
Oral manifestations of primary hyperoxaluria in adult patient |
title_fullStr |
Oral manifestations of primary hyperoxaluria in adult patient |
title_full_unstemmed |
Oral manifestations of primary hyperoxaluria in adult patient |
title_sort |
Oral manifestations of primary hyperoxaluria in adult patient |
author |
Sacchetto, Marina Sena Lopes da Silva |
author_facet |
Sacchetto, Marina Sena Lopes da Silva Silva, Maísa Pereira da Tonello, Roberta da Silva D'Alessandro Castro, Wagner Henriques de |
author_role |
author |
author2 |
Silva, Maísa Pereira da Tonello, Roberta da Silva D'Alessandro Castro, Wagner Henriques de |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Sacchetto, Marina Sena Lopes da Silva Silva, Maísa Pereira da Tonello, Roberta da Silva D'Alessandro Castro, Wagner Henriques de |
dc.subject.por.fl_str_mv |
Hyperoxaluria Oxalates Transplants Therapeutics. Hiperoxaluria Oxalatos Transplantes Terapéutica. Hiperoxalúria Oxalatos Transplantes Terapêutica. |
topic |
Hyperoxaluria Oxalates Transplants Therapeutics. Hiperoxaluria Oxalatos Transplantes Terapéutica. Hiperoxalúria Oxalatos Transplantes Terapêutica. |
description |
Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-05-21 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/15432 10.33448/rsd-v10i6.15432 |
url |
https://rsdjournal.org/index.php/rsd/article/view/15432 |
identifier_str_mv |
10.33448/rsd-v10i6.15432 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/15432/14448 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Research, Society and Development |
publisher.none.fl_str_mv |
Research, Society and Development |
dc.source.none.fl_str_mv |
Research, Society and Development; Vol. 10 No. 6; e8310615432 Research, Society and Development; Vol. 10 Núm. 6; e8310615432 Research, Society and Development; v. 10 n. 6; e8310615432 2525-3409 reponame:Research, Society and Development instname:Universidade Federal de Itajubá (UNIFEI) instacron:UNIFEI |
instname_str |
Universidade Federal de Itajubá (UNIFEI) |
instacron_str |
UNIFEI |
institution |
UNIFEI |
reponame_str |
Research, Society and Development |
collection |
Research, Society and Development |
repository.name.fl_str_mv |
Research, Society and Development - Universidade Federal de Itajubá (UNIFEI) |
repository.mail.fl_str_mv |
rsd.articles@gmail.com |
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