Oral manifestations of primary hyperoxaluria in adult patient

Detalhes bibliográficos
Autor(a) principal: Sacchetto, Marina Sena Lopes da Silva
Data de Publicação: 2021
Outros Autores: Silva, Maísa Pereira da, Tonello, Roberta da Silva D'Alessandro, Castro, Wagner Henriques de
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/15432
Resumo: Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations.
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spelling Oral manifestations of primary hyperoxaluria in adult patientManifestaciones orales de la hiperoxaluria primaria en paciente adultaManifestação oral da hiperoxalúria primária em paciente adultoHyperoxaluriaOxalatesTransplantsTherapeutics.HiperoxaluriaOxalatosTransplantesTerapéutica.HiperoxalúriaOxalatosTransplantesTerapêutica.Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations.La hiperoxaluria primaria (HP) es una enfermedad rara, un trastorno hereditario autosómico recesivo. Esta enfermedad conduce a la sobreproducción de oxalatos y la incapacidad de excreción da como resultado el depósito de cristales de oxalato de calcio en casi todos los tejidos que presentan la condición de oxalosis. El tratamiento es un trasplante combinado de hígado y riñón (TCHR), que permite una mejor supervivencia del paciente. Debido a esta supervivencia los pacientes pudieron presentar diversas manifestaciones bucales como enfermedad periodontal, reabsorción radicular, dolor dentario y aumento de la movilidad dentaria. Sin embargo, hasta la fecha, existe una falta de información en la literatura sobre todas las manifestaciones bucales que puede presentar este paciente. Además de esto, tengo una duda y un desafío sobre los tratamientos a este paciente en estas diferentes manifestaciones orales. El presente estudio tiene como objetivo reportar el caso de un paciente con hiperoxaluria tipo I con manifestaciones orales de oxalosis.A hiperoxalúria primária (HP) é uma doença rara de herança autossômica recessiva. Essa doença leva à superprodução de oxalatos, e a incapacidade de excreção resulta na deposição de cristais de oxalato de cálcio em quase todos os tecidos que apresentam a condição de oxalose. O tratamento é o transplante combinado de fígado e rim (TCFR), que permite melhor sobrevida do paciente. Devido a esta sobrevida os pacientes puderam apresentar diversas manifestações bucais como doença periodontal, reabsorção radicular, dor dentária e aumento da mobilidade dentária. Porém, até o momento, faltam informações na literatura sobre todas as manifestações orais que esse paciente pode apresentar. Ao lado disso temos uma dúvida e um desafio quanto aos tratamentos a esse paciente nessas diferentes manifestações orais. O presente trabalho tem como objetivo relatar um caso de uma paciente com hiperoxalúria tipo I, apresentando manifestações orais de oxalose.Research, Society and Development2021-05-21info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/1543210.33448/rsd-v10i6.15432Research, Society and Development; Vol. 10 No. 6; e8310615432Research, Society and Development; Vol. 10 Núm. 6; e8310615432Research, Society and Development; v. 10 n. 6; e83106154322525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIenghttps://rsdjournal.org/index.php/rsd/article/view/15432/14448Copyright (c) 2021 Marina Sena Lopes da Silva Sacchetto; Maísa Pereira da Silva; Roberta da Silva D'Alessandro Tonello; Wagner Henriques de Castrohttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessSacchetto, Marina Sena Lopes da SilvaSilva, Maísa Pereira daTonello, Roberta da Silva D'Alessandro Castro, Wagner Henriques de2021-06-10T22:51:46Zoai:ojs.pkp.sfu.ca:article/15432Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:36:15.382176Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Oral manifestations of primary hyperoxaluria in adult patient
Manifestaciones orales de la hiperoxaluria primaria en paciente adulta
Manifestação oral da hiperoxalúria primária em paciente adulto
title Oral manifestations of primary hyperoxaluria in adult patient
spellingShingle Oral manifestations of primary hyperoxaluria in adult patient
Sacchetto, Marina Sena Lopes da Silva
Hyperoxaluria
Oxalates
Transplants
Therapeutics.
Hiperoxaluria
Oxalatos
Transplantes
Terapéutica.
Hiperoxalúria
Oxalatos
Transplantes
Terapêutica.
title_short Oral manifestations of primary hyperoxaluria in adult patient
title_full Oral manifestations of primary hyperoxaluria in adult patient
title_fullStr Oral manifestations of primary hyperoxaluria in adult patient
title_full_unstemmed Oral manifestations of primary hyperoxaluria in adult patient
title_sort Oral manifestations of primary hyperoxaluria in adult patient
author Sacchetto, Marina Sena Lopes da Silva
author_facet Sacchetto, Marina Sena Lopes da Silva
Silva, Maísa Pereira da
Tonello, Roberta da Silva D'Alessandro
Castro, Wagner Henriques de
author_role author
author2 Silva, Maísa Pereira da
Tonello, Roberta da Silva D'Alessandro
Castro, Wagner Henriques de
author2_role author
author
author
dc.contributor.author.fl_str_mv Sacchetto, Marina Sena Lopes da Silva
Silva, Maísa Pereira da
Tonello, Roberta da Silva D'Alessandro
Castro, Wagner Henriques de
dc.subject.por.fl_str_mv Hyperoxaluria
Oxalates
Transplants
Therapeutics.
Hiperoxaluria
Oxalatos
Transplantes
Terapéutica.
Hiperoxalúria
Oxalatos
Transplantes
Terapêutica.
topic Hyperoxaluria
Oxalates
Transplants
Therapeutics.
Hiperoxaluria
Oxalatos
Transplantes
Terapéutica.
Hiperoxalúria
Oxalatos
Transplantes
Terapêutica.
description Primary hyperoxaluria (PH) is a rare disease, autosomal recessive inheritance disorder. This disease leads to overproduction of oxalates, and the excretation inability results in deposition of calcium oxalate crystals in almost all tissues presenting the oxalosis condition. The treatment is a combined liver and kidney transplantation (CLKT), which enables a better patient survival. Due to this survival, the patients had could present a several oral manifestations such as periodontal disease, root resorption, dental pain and increased tooth mobility. However, currently, there is a lack of information in the literature about all oral manifestations that this patient can present. Beside this, there are doubt and challenge about treatments to this patient in these different oral manifestations. The present study aims to report a case of a patient with hyperoxaluria type I with oxalosis oral manifestations.
publishDate 2021
dc.date.none.fl_str_mv 2021-05-21
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/15432
10.33448/rsd-v10i6.15432
url https://rsdjournal.org/index.php/rsd/article/view/15432
identifier_str_mv 10.33448/rsd-v10i6.15432
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/15432/14448
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 10 No. 6; e8310615432
Research, Society and Development; Vol. 10 Núm. 6; e8310615432
Research, Society and Development; v. 10 n. 6; e8310615432
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
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instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
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reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
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