Moebius sequence and the oral health condition: Case report

Detalhes bibliográficos
Autor(a) principal: Brischke, Jeani Aparecida Petrik
Data de Publicação: 2021
Outros Autores: Rodrigues, Célia Patrícia Müller, Lindenberg, Juliana Marques, Nassar , Carlos Augusto, Baltazar, Mariângela Monteiro de Melo
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/24182
Resumo: Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important.
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spelling Moebius sequence and the oral health condition: Case reportSecuencia de Moebius y estado de salud bucal: Reporte de casoSequência de Moebius e a condição de saúde bucal: Relato de casoSíndrome de MöbiusOdontologiaParalisia facialAssistência odontológica para pessoas com deficiências.Mobius SyndromeDentistryFacial ParalysisDental care for disabled.Síndrome de MobiusOdontologíaParálisis FacialAtención dental para personas con discapacidades.Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important.El síndrome de Moebius es un trastorno neurológico congénito poco común, con una prevalencia de 1: 250.000 individuos, sin etiología definida. La característica principal del síndrome es la parálisis del nervio facial (VII par de pares craneales), que puede comprometer otros nervios, el diagnóstico se puede hacer en la infancia. El tratamiento debe ser realizado por un equipo multidisciplinar con seguimiento periódico. El objetivo de este trabajo fue reportar el caso de un paciente afectado por el Síndrome de Moebius, enfatizando la condición de salud bucal. Este trabajo se llevó a cabo en el Centro de Atención e Investigación en Anomalías Craneofaciales - CEAPAC ubicado en la ciudad de Cascavel-PR. La paciente M.C.S.R. de diecinueve años, mujer, fue remitida a CEAPAC para tratamiento dental. El examen físico mostró características típicas de los pacientes con Síndrome de Moebius y el examen intraoral reveló un estado precario de los dientes y tejidos adyacentes. El tratamiento dental se realizó en un entorno clínico y bajo anestesia local. Teniendo en cuenta las graves implicaciones que desencadena el síndrome, es de suma importancia el seguimiento precoz y periódico del paciente por parte de un equipo multidisciplinar.A Síndrome de Moebius é uma desordem congênita neurológica rara, com prevalência de 1:250.000 indivíduos, sem etiologia definida. A principal característica da síndrome é a paralisia do nervo facial (VII par de nervo craniano), podendo comprometer outros nervos, o diagnóstico pode ser dado ainda na infância. O tratamento deve ser realizado por uma equipe multiprofissional com acompanhamento periódico. O objetivo desse trabalho foi relatar o caso de uma paciente acometida pela Síndrome de Moebius dando ênfase à condição de saúde bucal. Este trabalho foi realizado no Centro de Atenção e Pesquisa em Anomalias Craniofaciais - CEAPAC localizado na cidade de Cascavel- PR. Paciente M. C. S. R. com dezenove anos de idade, sexo feminino, foi encaminhada ao CEAPAC para realização de tratamento odontológico. Ao exame físico observou-se características típicas de portadores da Síndrome de Moebius e o exame intraoral revelou precária condição dentária e dos tecidos adjacentes. O tratamento odontológico foi realizado em ambiente clínico e sob anestesia local. Considerando as graves implicações desencadeadas pela síndrome é de extrema importância o acompanhamento do paciente por uma equipe multiprofissional de maneira precoce e periódica.Research, Society and Development2021-12-22info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/2418210.33448/rsd-v10i17.24182Research, Society and Development; Vol. 10 No. 17; e120101724182Research, Society and Development; Vol. 10 Núm. 17; e120101724182Research, Society and Development; v. 10 n. 17; e1201017241822525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/24182/22643Copyright (c) 2021 Jeani Aparecida Petrik Brischke; Célia Patrícia Müller Rodrigues; Juliana Marques Lindenberg; Carlos Augusto Nassar ; Mariângela Monteiro de Melo Baltazarhttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessBrischke, Jeani Aparecida PetrikRodrigues, Célia Patrícia MüllerLindenberg, Juliana MarquesNassar , Carlos Augusto Baltazar, Mariângela Monteiro de Melo2022-01-01T11:11:08Zoai:ojs.pkp.sfu.ca:article/24182Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:42:49.640666Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Moebius sequence and the oral health condition: Case report
Secuencia de Moebius y estado de salud bucal: Reporte de caso
Sequência de Moebius e a condição de saúde bucal: Relato de caso
title Moebius sequence and the oral health condition: Case report
spellingShingle Moebius sequence and the oral health condition: Case report
Brischke, Jeani Aparecida Petrik
Síndrome de Möbius
Odontologia
Paralisia facial
Assistência odontológica para pessoas com deficiências.
Mobius Syndrome
Dentistry
Facial Paralysis
Dental care for disabled.
Síndrome de Mobius
Odontología
Parálisis Facial
Atención dental para personas con discapacidades.
title_short Moebius sequence and the oral health condition: Case report
title_full Moebius sequence and the oral health condition: Case report
title_fullStr Moebius sequence and the oral health condition: Case report
title_full_unstemmed Moebius sequence and the oral health condition: Case report
title_sort Moebius sequence and the oral health condition: Case report
author Brischke, Jeani Aparecida Petrik
author_facet Brischke, Jeani Aparecida Petrik
Rodrigues, Célia Patrícia Müller
Lindenberg, Juliana Marques
Nassar , Carlos Augusto
Baltazar, Mariângela Monteiro de Melo
author_role author
author2 Rodrigues, Célia Patrícia Müller
Lindenberg, Juliana Marques
Nassar , Carlos Augusto
Baltazar, Mariângela Monteiro de Melo
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Brischke, Jeani Aparecida Petrik
Rodrigues, Célia Patrícia Müller
Lindenberg, Juliana Marques
Nassar , Carlos Augusto
Baltazar, Mariângela Monteiro de Melo
dc.subject.por.fl_str_mv Síndrome de Möbius
Odontologia
Paralisia facial
Assistência odontológica para pessoas com deficiências.
Mobius Syndrome
Dentistry
Facial Paralysis
Dental care for disabled.
Síndrome de Mobius
Odontología
Parálisis Facial
Atención dental para personas con discapacidades.
topic Síndrome de Möbius
Odontologia
Paralisia facial
Assistência odontológica para pessoas com deficiências.
Mobius Syndrome
Dentistry
Facial Paralysis
Dental care for disabled.
Síndrome de Mobius
Odontología
Parálisis Facial
Atención dental para personas con discapacidades.
description Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important.
publishDate 2021
dc.date.none.fl_str_mv 2021-12-22
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/24182
10.33448/rsd-v10i17.24182
url https://rsdjournal.org/index.php/rsd/article/view/24182
identifier_str_mv 10.33448/rsd-v10i17.24182
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/24182/22643
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 10 No. 17; e120101724182
Research, Society and Development; Vol. 10 Núm. 17; e120101724182
Research, Society and Development; v. 10 n. 17; e120101724182
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
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instname_str Universidade Federal de Itajubá (UNIFEI)
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institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
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