Moebius sequence and the oral health condition: Case report
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Research, Society and Development |
Texto Completo: | https://rsdjournal.org/index.php/rsd/article/view/24182 |
Resumo: | Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important. |
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Moebius sequence and the oral health condition: Case reportSecuencia de Moebius y estado de salud bucal: Reporte de casoSequência de Moebius e a condição de saúde bucal: Relato de casoSíndrome de MöbiusOdontologiaParalisia facialAssistência odontológica para pessoas com deficiências.Mobius SyndromeDentistryFacial ParalysisDental care for disabled.Síndrome de MobiusOdontologíaParálisis FacialAtención dental para personas con discapacidades.Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important.El síndrome de Moebius es un trastorno neurológico congénito poco común, con una prevalencia de 1: 250.000 individuos, sin etiología definida. La característica principal del síndrome es la parálisis del nervio facial (VII par de pares craneales), que puede comprometer otros nervios, el diagnóstico se puede hacer en la infancia. El tratamiento debe ser realizado por un equipo multidisciplinar con seguimiento periódico. El objetivo de este trabajo fue reportar el caso de un paciente afectado por el Síndrome de Moebius, enfatizando la condición de salud bucal. Este trabajo se llevó a cabo en el Centro de Atención e Investigación en Anomalías Craneofaciales - CEAPAC ubicado en la ciudad de Cascavel-PR. La paciente M.C.S.R. de diecinueve años, mujer, fue remitida a CEAPAC para tratamiento dental. El examen físico mostró características típicas de los pacientes con Síndrome de Moebius y el examen intraoral reveló un estado precario de los dientes y tejidos adyacentes. El tratamiento dental se realizó en un entorno clínico y bajo anestesia local. Teniendo en cuenta las graves implicaciones que desencadena el síndrome, es de suma importancia el seguimiento precoz y periódico del paciente por parte de un equipo multidisciplinar.A Síndrome de Moebius é uma desordem congênita neurológica rara, com prevalência de 1:250.000 indivíduos, sem etiologia definida. A principal característica da síndrome é a paralisia do nervo facial (VII par de nervo craniano), podendo comprometer outros nervos, o diagnóstico pode ser dado ainda na infância. O tratamento deve ser realizado por uma equipe multiprofissional com acompanhamento periódico. O objetivo desse trabalho foi relatar o caso de uma paciente acometida pela Síndrome de Moebius dando ênfase à condição de saúde bucal. Este trabalho foi realizado no Centro de Atenção e Pesquisa em Anomalias Craniofaciais - CEAPAC localizado na cidade de Cascavel- PR. Paciente M. C. S. R. com dezenove anos de idade, sexo feminino, foi encaminhada ao CEAPAC para realização de tratamento odontológico. Ao exame físico observou-se características típicas de portadores da Síndrome de Moebius e o exame intraoral revelou precária condição dentária e dos tecidos adjacentes. O tratamento odontológico foi realizado em ambiente clínico e sob anestesia local. Considerando as graves implicações desencadeadas pela síndrome é de extrema importância o acompanhamento do paciente por uma equipe multiprofissional de maneira precoce e periódica.Research, Society and Development2021-12-22info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/2418210.33448/rsd-v10i17.24182Research, Society and Development; Vol. 10 No. 17; e120101724182Research, Society and Development; Vol. 10 Núm. 17; e120101724182Research, Society and Development; v. 10 n. 17; e1201017241822525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/24182/22643Copyright (c) 2021 Jeani Aparecida Petrik Brischke; Célia Patrícia Müller Rodrigues; Juliana Marques Lindenberg; Carlos Augusto Nassar ; Mariângela Monteiro de Melo Baltazarhttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessBrischke, Jeani Aparecida PetrikRodrigues, Célia Patrícia MüllerLindenberg, Juliana MarquesNassar , Carlos Augusto Baltazar, Mariângela Monteiro de Melo2022-01-01T11:11:08Zoai:ojs.pkp.sfu.ca:article/24182Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:42:49.640666Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false |
dc.title.none.fl_str_mv |
Moebius sequence and the oral health condition: Case report Secuencia de Moebius y estado de salud bucal: Reporte de caso Sequência de Moebius e a condição de saúde bucal: Relato de caso |
title |
Moebius sequence and the oral health condition: Case report |
spellingShingle |
Moebius sequence and the oral health condition: Case report Brischke, Jeani Aparecida Petrik Síndrome de Möbius Odontologia Paralisia facial Assistência odontológica para pessoas com deficiências. Mobius Syndrome Dentistry Facial Paralysis Dental care for disabled. Síndrome de Mobius Odontología Parálisis Facial Atención dental para personas con discapacidades. |
title_short |
Moebius sequence and the oral health condition: Case report |
title_full |
Moebius sequence and the oral health condition: Case report |
title_fullStr |
Moebius sequence and the oral health condition: Case report |
title_full_unstemmed |
Moebius sequence and the oral health condition: Case report |
title_sort |
Moebius sequence and the oral health condition: Case report |
author |
Brischke, Jeani Aparecida Petrik |
author_facet |
Brischke, Jeani Aparecida Petrik Rodrigues, Célia Patrícia Müller Lindenberg, Juliana Marques Nassar , Carlos Augusto Baltazar, Mariângela Monteiro de Melo |
author_role |
author |
author2 |
Rodrigues, Célia Patrícia Müller Lindenberg, Juliana Marques Nassar , Carlos Augusto Baltazar, Mariângela Monteiro de Melo |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Brischke, Jeani Aparecida Petrik Rodrigues, Célia Patrícia Müller Lindenberg, Juliana Marques Nassar , Carlos Augusto Baltazar, Mariângela Monteiro de Melo |
dc.subject.por.fl_str_mv |
Síndrome de Möbius Odontologia Paralisia facial Assistência odontológica para pessoas com deficiências. Mobius Syndrome Dentistry Facial Paralysis Dental care for disabled. Síndrome de Mobius Odontología Parálisis Facial Atención dental para personas con discapacidades. |
topic |
Síndrome de Möbius Odontologia Paralisia facial Assistência odontológica para pessoas com deficiências. Mobius Syndrome Dentistry Facial Paralysis Dental care for disabled. Síndrome de Mobius Odontología Parálisis Facial Atención dental para personas con discapacidades. |
description |
Moebius Syndrome is a rare congenital neurological disorder, with a prevalence of 1:250,000 individuals, with no defined etiology. The main feature of the syndrome is facial nerve palsy (VII pair of cranial nerve), which can compromise other nerves, the diagnosis can be made in childhood. Treatment must be carried out by a multidisciplinary team with periodic monitoring. The objective of this work was to report the case of a patient affected by Moebius Syndrome, emphasizing the oral health condition. This work was carried out at the Center for Attention and Research in Craniofacial Anomalies - CEAPAC located in the city of Cascavel-PR. Patient M.C.S.R. nineteen years old, female, was referred to CEAPAC for dental treatment. On physical examination, typical characteristics of patients with Moebius Syndrome were observed, and the intraoral examination revealed a precarious condition of the teeth and adjacent tissues. Dental treatment was performed in a clinical setting and under local anesthesia. Considering the serious implications triggered by the syndrome, early and periodic monitoring of the patient by a multidisciplinary team is extremely important. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-12-22 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/24182 10.33448/rsd-v10i17.24182 |
url |
https://rsdjournal.org/index.php/rsd/article/view/24182 |
identifier_str_mv |
10.33448/rsd-v10i17.24182 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://rsdjournal.org/index.php/rsd/article/view/24182/22643 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Research, Society and Development |
publisher.none.fl_str_mv |
Research, Society and Development |
dc.source.none.fl_str_mv |
Research, Society and Development; Vol. 10 No. 17; e120101724182 Research, Society and Development; Vol. 10 Núm. 17; e120101724182 Research, Society and Development; v. 10 n. 17; e120101724182 2525-3409 reponame:Research, Society and Development instname:Universidade Federal de Itajubá (UNIFEI) instacron:UNIFEI |
instname_str |
Universidade Federal de Itajubá (UNIFEI) |
instacron_str |
UNIFEI |
institution |
UNIFEI |
reponame_str |
Research, Society and Development |
collection |
Research, Society and Development |
repository.name.fl_str_mv |
Research, Society and Development - Universidade Federal de Itajubá (UNIFEI) |
repository.mail.fl_str_mv |
rsd.articles@gmail.com |
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1797052791657594880 |