Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases

Detalhes bibliográficos
Autor(a) principal: Valente,Alan Peres
Data de Publicação: 2015
Outros Autores: Pinho,Paula da Cunha, Lucato,Leandro Tavares
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Dementia & Neuropsychologia
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424
Resumo: ABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD.
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spelling Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two casesCreutzfeldt-Jakob diseaseprionic diseaseprionprionic diseaserapidly progressive dementiaMRIdiffusionDWIbasal gangliacortexABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD.Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento2015-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424Dementia & Neuropsychologia v.9 n.4 2015reponame:Dementia & Neuropsychologiainstname:Associação de Neurologia Cognitiva e do Comportamento (ANCC)instacron:ANCC10.1590/1980-57642015DN94000424info:eu-repo/semantics/openAccessValente,Alan PeresPinho,Paula da CunhaLucato,Leandro Tavareseng2015-12-17T00:00:00Zoai:scielo:S1980-57642015000400424Revistahttp://www.demneuropsy.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.php||demneuropsy@uol.com.br1980-57641980-5764opendoar:2015-12-17T00:00Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC)false
dc.title.none.fl_str_mv Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
title Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
spellingShingle Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
Valente,Alan Peres
Creutzfeldt-Jakob disease
prionic disease
prion
prionic disease
rapidly progressive dementia
MRI
diffusion
DWI
basal ganglia
cortex
title_short Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
title_full Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
title_fullStr Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
title_full_unstemmed Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
title_sort Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
author Valente,Alan Peres
author_facet Valente,Alan Peres
Pinho,Paula da Cunha
Lucato,Leandro Tavares
author_role author
author2 Pinho,Paula da Cunha
Lucato,Leandro Tavares
author2_role author
author
dc.contributor.author.fl_str_mv Valente,Alan Peres
Pinho,Paula da Cunha
Lucato,Leandro Tavares
dc.subject.por.fl_str_mv Creutzfeldt-Jakob disease
prionic disease
prion
prionic disease
rapidly progressive dementia
MRI
diffusion
DWI
basal ganglia
cortex
topic Creutzfeldt-Jakob disease
prionic disease
prion
prionic disease
rapidly progressive dementia
MRI
diffusion
DWI
basal ganglia
cortex
description ABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD.
publishDate 2015
dc.date.none.fl_str_mv 2015-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1980-57642015DN94000424
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
publisher.none.fl_str_mv Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
dc.source.none.fl_str_mv Dementia & Neuropsychologia v.9 n.4 2015
reponame:Dementia & Neuropsychologia
instname:Associação de Neurologia Cognitiva e do Comportamento (ANCC)
instacron:ANCC
instname_str Associação de Neurologia Cognitiva e do Comportamento (ANCC)
instacron_str ANCC
institution ANCC
reponame_str Dementia & Neuropsychologia
collection Dementia & Neuropsychologia
repository.name.fl_str_mv Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC)
repository.mail.fl_str_mv ||demneuropsy@uol.com.br
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