Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases
Autor(a) principal: | |
---|---|
Data de Publicação: | 2015 |
Outros Autores: | , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Dementia & Neuropsychologia |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424 |
Resumo: | ABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD. |
id |
ANCC-1_e04919e423dda897734643a937c5c3cd |
---|---|
oai_identifier_str |
oai:scielo:S1980-57642015000400424 |
network_acronym_str |
ANCC-1 |
network_name_str |
Dementia & Neuropsychologia |
repository_id_str |
|
spelling |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two casesCreutzfeldt-Jakob diseaseprionic diseaseprionprionic diseaserapidly progressive dementiaMRIdiffusionDWIbasal gangliacortexABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD.Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento2015-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424Dementia & Neuropsychologia v.9 n.4 2015reponame:Dementia & Neuropsychologiainstname:Associação de Neurologia Cognitiva e do Comportamento (ANCC)instacron:ANCC10.1590/1980-57642015DN94000424info:eu-repo/semantics/openAccessValente,Alan PeresPinho,Paula da CunhaLucato,Leandro Tavareseng2015-12-17T00:00:00Zoai:scielo:S1980-57642015000400424Revistahttp://www.demneuropsy.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.php||demneuropsy@uol.com.br1980-57641980-5764opendoar:2015-12-17T00:00Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC)false |
dc.title.none.fl_str_mv |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
title |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
spellingShingle |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases Valente,Alan Peres Creutzfeldt-Jakob disease prionic disease prion prionic disease rapidly progressive dementia MRI diffusion DWI basal ganglia cortex |
title_short |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
title_full |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
title_fullStr |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
title_full_unstemmed |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
title_sort |
Magnetic ressonance imaging in the diagnosis of Creutzfeldt-Jakob disease: report of two cases |
author |
Valente,Alan Peres |
author_facet |
Valente,Alan Peres Pinho,Paula da Cunha Lucato,Leandro Tavares |
author_role |
author |
author2 |
Pinho,Paula da Cunha Lucato,Leandro Tavares |
author2_role |
author author |
dc.contributor.author.fl_str_mv |
Valente,Alan Peres Pinho,Paula da Cunha Lucato,Leandro Tavares |
dc.subject.por.fl_str_mv |
Creutzfeldt-Jakob disease prionic disease prion prionic disease rapidly progressive dementia MRI diffusion DWI basal ganglia cortex |
topic |
Creutzfeldt-Jakob disease prionic disease prion prionic disease rapidly progressive dementia MRI diffusion DWI basal ganglia cortex |
description |
ABSTRACT Creutzfeldt-Jacob disease (CJD) is a rare condition caused by a pathogenic prion protein that evolves with rapidly progressive dementia and death. The clinical presentation may sometimes be misleading. Magnetic Resonance Imaging (MRI) aids diagnosis with patterns that can guide or confirm clinical hypotheses. Two cases of rapidly progressive dementia with ataxia, myoclonus and restricted diffusion on MRI in cortical/basal ganglia are presented to draw attention to CJD. |
publishDate |
2015 |
dc.date.none.fl_str_mv |
2015-12-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642015000400424 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/1980-57642015DN94000424 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento |
publisher.none.fl_str_mv |
Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento |
dc.source.none.fl_str_mv |
Dementia & Neuropsychologia v.9 n.4 2015 reponame:Dementia & Neuropsychologia instname:Associação de Neurologia Cognitiva e do Comportamento (ANCC) instacron:ANCC |
instname_str |
Associação de Neurologia Cognitiva e do Comportamento (ANCC) |
instacron_str |
ANCC |
institution |
ANCC |
reponame_str |
Dementia & Neuropsychologia |
collection |
Dementia & Neuropsychologia |
repository.name.fl_str_mv |
Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC) |
repository.mail.fl_str_mv |
||demneuropsy@uol.com.br |
_version_ |
1754212931106504704 |