Langerhans cell histiocytosis
| Autor(a) principal: | |
|---|---|
| Data de Publicação: | 1998 |
| Outros Autores: | , , , , , , , , , |
| Tipo de documento: | Artigo |
| Idioma: | eng |
| Título da fonte: | São Paulo medical journal (Online) |
| Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000100006 |
Resumo: | The authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations. Skin biopsy immunohistochemistry presented positive S100 protein and vimentine, but the diagnosis was done with the demonstration of Birbeck granules with eletronic mucroscopy. The treatment was based on systemical chemotherapy although vulvar lesion has a bad response to chemotherapy. |
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Langerhans cell histiocytosisHistiocytosis XLangerhans cellDiabetes insipidusThe authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations. Skin biopsy immunohistochemistry presented positive S100 protein and vimentine, but the diagnosis was done with the demonstration of Birbeck granules with eletronic mucroscopy. The treatment was based on systemical chemotherapy although vulvar lesion has a bad response to chemotherapy.Associação Paulista de Medicina - APM1998-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000100006Sao Paulo Medical Journal v.116 n.1 1998reponame:São Paulo medical journal (Online)instname:Associação Paulista de Medicinainstacron:APM10.1590/S1516-31801998000100006info:eu-repo/semantics/openAccessChauffaille,Maria de Lourdes L. F.Valério,Rosana M.Diniz,Cybelle Maria CostaSimões,Milvia MariaEnokihara,SilvaMichalany,NylceoFerreira,Karin VenturaMartinez,José Antonio BaddiniHassun,Karine MarquesAtallah,Álvaro NagibKerbauy,Joséeng2008-10-16T00:00:00Zoai:scielo:S1516-31801998000100006Revistahttp://www.scielo.br/spmjhttps://old.scielo.br/oai/scielo-oai.phprevistas@apm.org.br1806-94601516-3180opendoar:2008-10-16T00:00São Paulo medical journal (Online) - Associação Paulista de Medicinafalse |
| dc.title.none.fl_str_mv |
Langerhans cell histiocytosis |
| title |
Langerhans cell histiocytosis |
| spellingShingle |
Langerhans cell histiocytosis Chauffaille,Maria de Lourdes L. F. Histiocytosis X Langerhans cell Diabetes insipidus |
| title_short |
Langerhans cell histiocytosis |
| title_full |
Langerhans cell histiocytosis |
| title_fullStr |
Langerhans cell histiocytosis |
| title_full_unstemmed |
Langerhans cell histiocytosis |
| title_sort |
Langerhans cell histiocytosis |
| author |
Chauffaille,Maria de Lourdes L. F. |
| author_facet |
Chauffaille,Maria de Lourdes L. F. Valério,Rosana M. Diniz,Cybelle Maria Costa Simões,Milvia Maria Enokihara,Silva Michalany,Nylceo Ferreira,Karin Ventura Martinez,José Antonio Baddini Hassun,Karine Marques Atallah,Álvaro Nagib Kerbauy,José |
| author_role |
author |
| author2 |
Valério,Rosana M. Diniz,Cybelle Maria Costa Simões,Milvia Maria Enokihara,Silva Michalany,Nylceo Ferreira,Karin Ventura Martinez,José Antonio Baddini Hassun,Karine Marques Atallah,Álvaro Nagib Kerbauy,José |
| author2_role |
author author author author author author author author author author |
| dc.contributor.author.fl_str_mv |
Chauffaille,Maria de Lourdes L. F. Valério,Rosana M. Diniz,Cybelle Maria Costa Simões,Milvia Maria Enokihara,Silva Michalany,Nylceo Ferreira,Karin Ventura Martinez,José Antonio Baddini Hassun,Karine Marques Atallah,Álvaro Nagib Kerbauy,José |
| dc.subject.por.fl_str_mv |
Histiocytosis X Langerhans cell Diabetes insipidus |
| topic |
Histiocytosis X Langerhans cell Diabetes insipidus |
| description |
The authors present a rare case of Langerhans cell histiocytosis in a 31 year old female patient with vulvar, peri-anal and oral lesions, diabetes insipidus, pulmonary skin and bone infiltrations. Skin biopsy immunohistochemistry presented positive S100 protein and vimentine, but the diagnosis was done with the demonstration of Birbeck granules with eletronic mucroscopy. The treatment was based on systemical chemotherapy although vulvar lesion has a bad response to chemotherapy. |
| publishDate |
1998 |
| dc.date.none.fl_str_mv |
1998-02-01 |
| dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
| dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
| format |
article |
| status_str |
publishedVersion |
| dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000100006 |
| url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-31801998000100006 |
| dc.language.iso.fl_str_mv |
eng |
| language |
eng |
| dc.relation.none.fl_str_mv |
10.1590/S1516-31801998000100006 |
| dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
| eu_rights_str_mv |
openAccess |
| dc.format.none.fl_str_mv |
text/html |
| dc.publisher.none.fl_str_mv |
Associação Paulista de Medicina - APM |
| publisher.none.fl_str_mv |
Associação Paulista de Medicina - APM |
| dc.source.none.fl_str_mv |
Sao Paulo Medical Journal v.116 n.1 1998 reponame:São Paulo medical journal (Online) instname:Associação Paulista de Medicina instacron:APM |
| instname_str |
Associação Paulista de Medicina |
| instacron_str |
APM |
| institution |
APM |
| reponame_str |
São Paulo medical journal (Online) |
| collection |
São Paulo medical journal (Online) |
| repository.name.fl_str_mv |
São Paulo medical journal (Online) - Associação Paulista de Medicina |
| repository.mail.fl_str_mv |
revistas@apm.org.br |
| _version_ |
1754209259607818240 |