Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy
Autor(a) principal: | |
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Data de Publicação: | 2021 |
Outros Autores: | , , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Revista brasileira de ginecologia e obstetrícia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032021000300220 |
Resumo: | Abstract Acute pancreatitis is a rare condition in pregnancy, associated with a high mortality rate. Hypertriglyceridemia represents its second most common cause.We present the case of a 38-year-old woman in the 24th week of gestation with a history of hypertriglyceridemia and recurrent episodes of pancreatitis. She was admitted to our hospital with acute pancreatitis due to severe hypertriglyceridemia. She was stabilized and treated with fibrates. Despite her favorable clinical course, she developed a second episode of acute pancreatitis complicated by multi-organ dysfunction and pancreatic necrosis, requiring a necrosectomy. The pregnancy was ended by cesarean section, after which three plasmapheresis sessions were performed. She is currently asymptomatic with stable triglyceride levels. Acute pancreatitis due to hypertriglyceridemia represents a diagnostic and therapeutic challenge in pregnant women, associated with serious maternal and fetal complications. When primary hypertriglyceridemia is suspected, such as familial chylomicronemia syndrome, the most important objective is preventing the onset of pancreatitis. |
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Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancyfamilial chylomicronemianecrotizing pancreatitispregnancyAbstract Acute pancreatitis is a rare condition in pregnancy, associated with a high mortality rate. Hypertriglyceridemia represents its second most common cause.We present the case of a 38-year-old woman in the 24th week of gestation with a history of hypertriglyceridemia and recurrent episodes of pancreatitis. She was admitted to our hospital with acute pancreatitis due to severe hypertriglyceridemia. She was stabilized and treated with fibrates. Despite her favorable clinical course, she developed a second episode of acute pancreatitis complicated by multi-organ dysfunction and pancreatic necrosis, requiring a necrosectomy. The pregnancy was ended by cesarean section, after which three plasmapheresis sessions were performed. She is currently asymptomatic with stable triglyceride levels. Acute pancreatitis due to hypertriglyceridemia represents a diagnostic and therapeutic challenge in pregnant women, associated with serious maternal and fetal complications. When primary hypertriglyceridemia is suspected, such as familial chylomicronemia syndrome, the most important objective is preventing the onset of pancreatitis.Federação Brasileira das Sociedades de Ginecologia e Obstetrícia2021-03-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032021000300220Revista Brasileira de Ginecologia e Obstetrícia v.43 n.3 2021reponame:Revista brasileira de ginecologia e obstetrícia (Online)instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)instacron:FEBRASGO10.1055/s-0040-1722173info:eu-repo/semantics/openAccessArroyo,Julia Cristina CoronadoZavaleta,Marcio José ConcepciónVillasante,Eilhart Jorge GarcíaLam,Mikaela KcomtUrteaga,Luis Alberto ConcepciónGutiérrez,Francisca Elena Zavaletaeng2021-05-21T00:00:00Zoai:scielo:S0100-72032021000300220Revistahttp://www.scielo.br/rbgohttps://old.scielo.br/oai/scielo-oai.phppublicações@febrasgo.org.br||rbgo@fmrp.usp.br1806-93390100-7203opendoar:2021-05-21T00:00Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO)false |
dc.title.none.fl_str_mv |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
title |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
spellingShingle |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy Arroyo,Julia Cristina Coronado familial chylomicronemia necrotizing pancreatitis pregnancy |
title_short |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
title_full |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
title_fullStr |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
title_full_unstemmed |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
title_sort |
Familial Chylomicronemia Syndrome-Induced Acute Necrotizing Pancreatitis during Pregnancy |
author |
Arroyo,Julia Cristina Coronado |
author_facet |
Arroyo,Julia Cristina Coronado Zavaleta,Marcio José Concepción Villasante,Eilhart Jorge García Lam,Mikaela Kcomt Urteaga,Luis Alberto Concepción Gutiérrez,Francisca Elena Zavaleta |
author_role |
author |
author2 |
Zavaleta,Marcio José Concepción Villasante,Eilhart Jorge García Lam,Mikaela Kcomt Urteaga,Luis Alberto Concepción Gutiérrez,Francisca Elena Zavaleta |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Arroyo,Julia Cristina Coronado Zavaleta,Marcio José Concepción Villasante,Eilhart Jorge García Lam,Mikaela Kcomt Urteaga,Luis Alberto Concepción Gutiérrez,Francisca Elena Zavaleta |
dc.subject.por.fl_str_mv |
familial chylomicronemia necrotizing pancreatitis pregnancy |
topic |
familial chylomicronemia necrotizing pancreatitis pregnancy |
description |
Abstract Acute pancreatitis is a rare condition in pregnancy, associated with a high mortality rate. Hypertriglyceridemia represents its second most common cause.We present the case of a 38-year-old woman in the 24th week of gestation with a history of hypertriglyceridemia and recurrent episodes of pancreatitis. She was admitted to our hospital with acute pancreatitis due to severe hypertriglyceridemia. She was stabilized and treated with fibrates. Despite her favorable clinical course, she developed a second episode of acute pancreatitis complicated by multi-organ dysfunction and pancreatic necrosis, requiring a necrosectomy. The pregnancy was ended by cesarean section, after which three plasmapheresis sessions were performed. She is currently asymptomatic with stable triglyceride levels. Acute pancreatitis due to hypertriglyceridemia represents a diagnostic and therapeutic challenge in pregnant women, associated with serious maternal and fetal complications. When primary hypertriglyceridemia is suspected, such as familial chylomicronemia syndrome, the most important objective is preventing the onset of pancreatitis. |
publishDate |
2021 |
dc.date.none.fl_str_mv |
2021-03-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032021000300220 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-72032021000300220 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1055/s-0040-1722173 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Federação Brasileira das Sociedades de Ginecologia e Obstetrícia |
publisher.none.fl_str_mv |
Federação Brasileira das Sociedades de Ginecologia e Obstetrícia |
dc.source.none.fl_str_mv |
Revista Brasileira de Ginecologia e Obstetrícia v.43 n.3 2021 reponame:Revista brasileira de ginecologia e obstetrícia (Online) instname:Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO) instacron:FEBRASGO |
instname_str |
Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO) |
instacron_str |
FEBRASGO |
institution |
FEBRASGO |
reponame_str |
Revista brasileira de ginecologia e obstetrícia (Online) |
collection |
Revista brasileira de ginecologia e obstetrícia (Online) |
repository.name.fl_str_mv |
Revista brasileira de ginecologia e obstetrícia (Online) - Federação Brasileira das Sociedades de Ginecologia e Obstetrícia (FEBRASGO) |
repository.mail.fl_str_mv |
publicações@febrasgo.org.br||rbgo@fmrp.usp.br |
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1754115945490546688 |