Hereditary protein C deficiency and portal vein thrombosis.

Detalhes bibliográficos
Autor(a) principal: dos Santos, J N
Data de Publicação: 1990
Outros Autores: Mello e Silva, A, Alexandrino, P, Saldanha, T, Carreira, M O, Ferreira, E, de Pádua, F
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531
Resumo: Inherited defects of the natural coagulation inhibitors predispose patients to thrombosis. These disorders have similar clinical presentations with a strong family of thrombosis, episodes of recurrent venous thromboembolism, beginning in early adulthood. We report a case of upper gastrointestinal bleeding in a patient with portal hypertension due to portal-vein thrombosis secondary to hereditary protein C deficiency, an association that has seldom been reported. We conclude that protein C deficiency should be investigated in thrombotic states, namely after more frequent causes have been excluded.
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spelling Hereditary protein C deficiency and portal vein thrombosis.Deficiência hereditária de proteína C e trombose da veia porta.Inherited defects of the natural coagulation inhibitors predispose patients to thrombosis. These disorders have similar clinical presentations with a strong family of thrombosis, episodes of recurrent venous thromboembolism, beginning in early adulthood. We report a case of upper gastrointestinal bleeding in a patient with portal hypertension due to portal-vein thrombosis secondary to hereditary protein C deficiency, an association that has seldom been reported. We conclude that protein C deficiency should be investigated in thrombotic states, namely after more frequent causes have been excluded.Inherited defects of the natural coagulation inhibitors predispose patients to thrombosis. These disorders have similar clinical presentations with a strong family of thrombosis, episodes of recurrent venous thromboembolism, beginning in early adulthood. We report a case of upper gastrointestinal bleeding in a patient with portal hypertension due to portal-vein thrombosis secondary to hereditary protein C deficiency, an association that has seldom been reported. We conclude that protein C deficiency should be investigated in thrombotic states, namely after more frequent causes have been excluded.Ordem dos Médicos1990-02-27info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531oai:ojs.www.actamedicaportuguesa.com:article/4531Acta Médica Portuguesa; Vol. 3 No. 1 (1990): Janeiro - Fevereiro; 27-30Acta Médica Portuguesa; Vol. 3 N.º 1 (1990): Janeiro - Fevereiro; 27-301646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531/3549dos Santos, J NMello e Silva, AAlexandrino, PSaldanha, TCarreira, M OFerreira, Ede Pádua, Finfo:eu-repo/semantics/openAccess2022-12-20T11:03:44Zoai:ojs.www.actamedicaportuguesa.com:article/4531Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:18:53.151285Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Hereditary protein C deficiency and portal vein thrombosis.
Deficiência hereditária de proteína C e trombose da veia porta.
title Hereditary protein C deficiency and portal vein thrombosis.
spellingShingle Hereditary protein C deficiency and portal vein thrombosis.
dos Santos, J N
title_short Hereditary protein C deficiency and portal vein thrombosis.
title_full Hereditary protein C deficiency and portal vein thrombosis.
title_fullStr Hereditary protein C deficiency and portal vein thrombosis.
title_full_unstemmed Hereditary protein C deficiency and portal vein thrombosis.
title_sort Hereditary protein C deficiency and portal vein thrombosis.
author dos Santos, J N
author_facet dos Santos, J N
Mello e Silva, A
Alexandrino, P
Saldanha, T
Carreira, M O
Ferreira, E
de Pádua, F
author_role author
author2 Mello e Silva, A
Alexandrino, P
Saldanha, T
Carreira, M O
Ferreira, E
de Pádua, F
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv dos Santos, J N
Mello e Silva, A
Alexandrino, P
Saldanha, T
Carreira, M O
Ferreira, E
de Pádua, F
description Inherited defects of the natural coagulation inhibitors predispose patients to thrombosis. These disorders have similar clinical presentations with a strong family of thrombosis, episodes of recurrent venous thromboembolism, beginning in early adulthood. We report a case of upper gastrointestinal bleeding in a patient with portal hypertension due to portal-vein thrombosis secondary to hereditary protein C deficiency, an association that has seldom been reported. We conclude that protein C deficiency should be investigated in thrombotic states, namely after more frequent causes have been excluded.
publishDate 1990
dc.date.none.fl_str_mv 1990-02-27
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dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.language.iso.fl_str_mv por
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dc.relation.none.fl_str_mv https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/4531/3549
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
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dc.publisher.none.fl_str_mv Ordem dos Médicos
publisher.none.fl_str_mv Ordem dos Médicos
dc.source.none.fl_str_mv Acta Médica Portuguesa; Vol. 3 No. 1 (1990): Janeiro - Fevereiro; 27-30
Acta Médica Portuguesa; Vol. 3 N.º 1 (1990): Janeiro - Fevereiro; 27-30
1646-0758
0870-399X
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