Henoch-Schönlein Purpura (IgA Vasculitis) in Adults

Detalhes bibliográficos
Autor(a) principal: Gouveia, Ana Isabel
Data de Publicação: 2016
Outros Autores: Lopes, Leonor, Freitas, João Pedro
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://doi.org/10.29021/spdv.74.3.596
Resumo: Henoch-Schönlein purpura is a small vessel vasculitis mediated by the deposition of IgA immune complexes. It is characterized by palpable purpura, arthralgia / arthritis, abdominal and renal involvement. Its etiology remains unknown, but various stimuli have been proposed to trigger this pathology, namely infectious agents, drugs and tumor antigens. There is also a possible association with malignancy and auto-immune diseases. Henoch-Schönlein purpura occurs mostly in children and is rare in adults. In the pediatric population the disease is generally self-limited, whereas in adults it is associated with a worse prognosis and a greater number of complications. This article reviews the main aspects of adult Henoch-Schönlein purpura, highlighting its particularities and specificities.
id RCAP_8e132d750bb0a56c362ce5139704f46e
oai_identifier_str oai:ojs.revista.spdv.com.pt:article/596
network_acronym_str RCAP
network_name_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository_id_str
spelling Henoch-Schönlein Purpura (IgA Vasculitis) in AdultsPúrpura de Henoch-Schönlein (Vasculite por IgA) no AdultoAdultImmunoglobulin APurpuraSchoenlein-HenochVasculitisLeukocytoclasticCutaneousAdultoImunoglobulina APúrpura Henoch-SchönleinVasculite Leucocitoclástica CutâneaHenoch-Schönlein purpura is a small vessel vasculitis mediated by the deposition of IgA immune complexes. It is characterized by palpable purpura, arthralgia / arthritis, abdominal and renal involvement. Its etiology remains unknown, but various stimuli have been proposed to trigger this pathology, namely infectious agents, drugs and tumor antigens. There is also a possible association with malignancy and auto-immune diseases. Henoch-Schönlein purpura occurs mostly in children and is rare in adults. In the pediatric population the disease is generally self-limited, whereas in adults it is associated with a worse prognosis and a greater number of complications. This article reviews the main aspects of adult Henoch-Schönlein purpura, highlighting its particularities and specificities.A Púrpura de Henoch-Schönlein é uma vasculite de pequenos vasos com deposição de imunocomplexos IgA. Caracteriza- se por púrpura palpável, artralgias/artrite, envolvimento abdominal e renal. A sua etiologia permanece desconhecida, mas vários estímulos têm sido propostos como possíveis fatores desencadeantes, entre eles, agentes infeciosos, fármacos, antígenos tumorais, havendo possível associação a malignidade e doenças autoimunes. Ocorre maioritariamente em crianças, sendo rara nos adultos. Na população pediátrica a doença é, na maioria das vezes, autolimitada, enquanto nos adultos está associada a um pior prognóstico e a um maior número de complicações. Neste artigo abordam-se os principais aspetos da PHS nos adultos, salientando-se as suas particularidades e especificidades.Sociedade Portuguesa de Dermatologia e Venereologia2016-10-15T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.74.3.596oai:ojs.revista.spdv.com.pt:article/596Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 3 (2016): Julho / Setembro; 265-271Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 3 (2016): Julho / Setembro; 265-2712182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://revista.spdv.com.pt/index.php/spdv/article/view/596https://doi.org/10.29021/spdv.74.3.596https://revista.spdv.com.pt/index.php/spdv/article/view/596/419Gouveia, Ana IsabelLopes, LeonorFreitas, João Pedroinfo:eu-repo/semantics/openAccess2022-10-06T12:34:58ZPortal AgregadorONG
dc.title.none.fl_str_mv Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
Púrpura de Henoch-Schönlein (Vasculite por IgA) no Adulto
title Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
spellingShingle Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
Gouveia, Ana Isabel
Adult
Immunoglobulin A
Purpura
Schoenlein-Henoch
Vasculitis
Leukocytoclastic
Cutaneous
Adulto
Imunoglobulina A
Púrpura Henoch-Schönlein
Vasculite Leucocitoclástica Cutânea
title_short Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
title_full Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
title_fullStr Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
title_full_unstemmed Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
title_sort Henoch-Schönlein Purpura (IgA Vasculitis) in Adults
author Gouveia, Ana Isabel
author_facet Gouveia, Ana Isabel
Lopes, Leonor
Freitas, João Pedro
author_role author
author2 Lopes, Leonor
Freitas, João Pedro
author2_role author
author
dc.contributor.author.fl_str_mv Gouveia, Ana Isabel
Lopes, Leonor
Freitas, João Pedro
dc.subject.por.fl_str_mv Adult
Immunoglobulin A
Purpura
Schoenlein-Henoch
Vasculitis
Leukocytoclastic
Cutaneous
Adulto
Imunoglobulina A
Púrpura Henoch-Schönlein
Vasculite Leucocitoclástica Cutânea
topic Adult
Immunoglobulin A
Purpura
Schoenlein-Henoch
Vasculitis
Leukocytoclastic
Cutaneous
Adulto
Imunoglobulina A
Púrpura Henoch-Schönlein
Vasculite Leucocitoclástica Cutânea
description Henoch-Schönlein purpura is a small vessel vasculitis mediated by the deposition of IgA immune complexes. It is characterized by palpable purpura, arthralgia / arthritis, abdominal and renal involvement. Its etiology remains unknown, but various stimuli have been proposed to trigger this pathology, namely infectious agents, drugs and tumor antigens. There is also a possible association with malignancy and auto-immune diseases. Henoch-Schönlein purpura occurs mostly in children and is rare in adults. In the pediatric population the disease is generally self-limited, whereas in adults it is associated with a worse prognosis and a greater number of complications. This article reviews the main aspects of adult Henoch-Schönlein purpura, highlighting its particularities and specificities.
publishDate 2016
dc.date.none.fl_str_mv 2016-10-15T00:00:00Z
dc.type.driver.fl_str_mv journal article
info:eu-repo/semantics/article
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://doi.org/10.29021/spdv.74.3.596
oai:ojs.revista.spdv.com.pt:article/596
url https://doi.org/10.29021/spdv.74.3.596
identifier_str_mv oai:ojs.revista.spdv.com.pt:article/596
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://revista.spdv.com.pt/index.php/spdv/article/view/596
https://doi.org/10.29021/spdv.74.3.596
https://revista.spdv.com.pt/index.php/spdv/article/view/596/419
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
publisher.none.fl_str_mv Sociedade Portuguesa de Dermatologia e Venereologia
dc.source.none.fl_str_mv Journal of the Portuguese Society of Dermatology and Venereology; Vol 74 No 3 (2016): Julho / Setembro; 265-271
Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 74 n. 3 (2016): Julho / Setembro; 265-271
2182-2409
2182-2395
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv
repository.mail.fl_str_mv
_version_ 1777301588031832064

Registros relacionados