ATYPICAL FIBROXANTHOMA – RARE TUMOR ARISING IN A BURN SCAR

• Autor(a) principal: Gameiro, Ana
• Data de Publicação: 2016
• Outros Autores: Gouveia, Miguel, Brinca, Ana, Cardoso, José Carlos, Vieira, Ricardo
• Tipo de documento: Artigo
• Idioma: por
• Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
• Texto Completo: https://doi.org/10.29021/spdv.73.4.494
• topic: Atypical Fibroxanthoma; Undifferentiated Pleomorphic Sarcoma; Skin Tumors; Scar; Burn; Fibroxantoma Atípico; Sarcoma Pleomórfico Indiferenciado; Cancro Cutâneo; Cicatriz; Queimadura

Atypical fibroxanthoma (AFX) is a relatively rare cutaneous tumor, characteristically presenting as a rapidly growing solitary nodule in photo-exposed areas of elderly patients. In spite of worrisome histological features, like pleomorphism and high mitotic rate, prognosis is favorable. Case report: A 62-year-old woman, with cicatricial alopecia on the parietal area, secondary to a thermal burn in her childhood, presented an ulcero-vegetant tumor, on the alopecia area, evolving for 1 year. Histology and immunohistochemistry showed features suggestive of AF. The tumor was completely excised, and a double transposition flap was used for closure, achieving local tumor control. The risk factors for AFX are not completely defined. Nevertheless, chronic exposition to ultraviolet radiation is a primordial factor. Other risk factors are radiotherapy and immunosuppression. Burn scars were only sporadically described in association to AF.