Adult nesidioblastosis.
Autor(a) principal: | |
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Data de Publicação: | 2003 |
Outros Autores: | , , , , , , |
Tipo de documento: | Artigo |
Idioma: | por |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211 |
Resumo: | In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed. |
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Adult nesidioblastosis.Nesidioblastose do adulto.In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed.In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed.Ordem dos Médicos2003-12-31info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211oai:ojs.www.actamedicaportuguesa.com:article/1211Acta Médica Portuguesa; Vol. 16 No. 6 (2003): November-December; 465-70Acta Médica Portuguesa; Vol. 16 N.º 6 (2003): Novembro-Dezembro; 465-701646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211/863Branco, Vítor ASantos, Rui MCipriano, M AugustaTralhão, GuilhermeOtero, MMoura, José ASousa, F CastroPorto, Armandoinfo:eu-repo/semantics/openAccess2022-12-20T10:57:38ZPortal AgregadorONG |
dc.title.none.fl_str_mv |
Adult nesidioblastosis. Nesidioblastose do adulto. |
title |
Adult nesidioblastosis. |
spellingShingle |
Adult nesidioblastosis. Branco, Vítor A |
title_short |
Adult nesidioblastosis. |
title_full |
Adult nesidioblastosis. |
title_fullStr |
Adult nesidioblastosis. |
title_full_unstemmed |
Adult nesidioblastosis. |
title_sort |
Adult nesidioblastosis. |
author |
Branco, Vítor A |
author_facet |
Branco, Vítor A Santos, Rui M Cipriano, M Augusta Tralhão, Guilherme Otero, M Moura, José A Sousa, F Castro Porto, Armando |
author_role |
author |
author2 |
Santos, Rui M Cipriano, M Augusta Tralhão, Guilherme Otero, M Moura, José A Sousa, F Castro Porto, Armando |
author2_role |
author author author author author author author |
dc.contributor.author.fl_str_mv |
Branco, Vítor A Santos, Rui M Cipriano, M Augusta Tralhão, Guilherme Otero, M Moura, José A Sousa, F Castro Porto, Armando |
description |
In adults, endogenous hyperinsulinemic hypoglycaemia is almost invariably due to insulinoma. The authors describe a 29 year old patient with repeated postprandial symptomatic hypoglycaemias and negative prolonged fast test. Distal pancreatectomy was performed, directed by positive arteriographic testing. Histological examination revealed pancreatic nesidioblastosis and no tumoral lesion. Distinct pathogenetic, clinical, diagnostic and therapeutic aspects of this rare disease in the adult are reviewed. |
publishDate |
2003 |
dc.date.none.fl_str_mv |
2003-12-31 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211 oai:ojs.www.actamedicaportuguesa.com:article/1211 |
url |
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211 |
identifier_str_mv |
oai:ojs.www.actamedicaportuguesa.com:article/1211 |
dc.language.iso.fl_str_mv |
por |
language |
por |
dc.relation.none.fl_str_mv |
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211 https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/1211/863 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Ordem dos Médicos |
publisher.none.fl_str_mv |
Ordem dos Médicos |
dc.source.none.fl_str_mv |
Acta Médica Portuguesa; Vol. 16 No. 6 (2003): November-December; 465-70 Acta Médica Portuguesa; Vol. 16 N.º 6 (2003): Novembro-Dezembro; 465-70 1646-0758 0870-399X reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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1777301630704680960 |