Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis

Detalhes bibliográficos
Autor(a) principal: Zielinsky,Paulo
Data de Publicação: 2000
Outros Autores: Pilla,Carlo B.
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Arquivos Brasileiros de Cardiologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006
Resumo: Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality.
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spelling Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosisEbstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality.Sociedade Brasileira de Cardiologia - SBC2000-07-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006Arquivos Brasileiros de Cardiologia v.75 n.1 2000reponame:Arquivos Brasileiros de Cardiologia (Online)instname:Sociedade Brasileira de Cardiologia (SBC)instacron:SBC10.1590/S0066-782X2000000700006info:eu-repo/semantics/openAccessZielinsky,PauloPilla,Carlo B.eng2002-01-08T00:00:00Zoai:scielo:S0066-782X2000000700006Revistahttp://www.arquivosonline.com.br/https://old.scielo.br/oai/scielo-oai.php||arquivos@cardiol.br1678-41700066-782Xopendoar:2002-01-08T00:00Arquivos Brasileiros de Cardiologia (Online) - Sociedade Brasileira de Cardiologia (SBC)false
dc.title.none.fl_str_mv Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
title Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
spellingShingle Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
Zielinsky,Paulo
title_short Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
title_full Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
title_fullStr Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
title_full_unstemmed Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
title_sort Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
author Zielinsky,Paulo
author_facet Zielinsky,Paulo
Pilla,Carlo B.
author_role author
author2 Pilla,Carlo B.
author2_role author
dc.contributor.author.fl_str_mv Zielinsky,Paulo
Pilla,Carlo B.
description Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality.
publishDate 2000
dc.date.none.fl_str_mv 2000-07-01
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dc.language.iso.fl_str_mv eng
language eng
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dc.publisher.none.fl_str_mv Sociedade Brasileira de Cardiologia - SBC
publisher.none.fl_str_mv Sociedade Brasileira de Cardiologia - SBC
dc.source.none.fl_str_mv Arquivos Brasileiros de Cardiologia v.75 n.1 2000
reponame:Arquivos Brasileiros de Cardiologia (Online)
instname:Sociedade Brasileira de Cardiologia (SBC)
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