Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis
Autor(a) principal: | |
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Data de Publicação: | 2000 |
Outros Autores: | |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Arquivos Brasileiros de Cardiologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006 |
Resumo: | Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality. |
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Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosisEbstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality.Sociedade Brasileira de Cardiologia - SBC2000-07-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006Arquivos Brasileiros de Cardiologia v.75 n.1 2000reponame:Arquivos Brasileiros de Cardiologia (Online)instname:Sociedade Brasileira de Cardiologia (SBC)instacron:SBC10.1590/S0066-782X2000000700006info:eu-repo/semantics/openAccessZielinsky,PauloPilla,Carlo B.eng2002-01-08T00:00:00Zoai:scielo:S0066-782X2000000700006Revistahttp://www.arquivosonline.com.br/https://old.scielo.br/oai/scielo-oai.php||arquivos@cardiol.br1678-41700066-782Xopendoar:2002-01-08T00:00Arquivos Brasileiros de Cardiologia (Online) - Sociedade Brasileira de Cardiologia (SBC)false |
dc.title.none.fl_str_mv |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
title |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
spellingShingle |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis Zielinsky,Paulo |
title_short |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
title_full |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
title_fullStr |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
title_full_unstemmed |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
title_sort |
Ebstein's anomaly with imperforate tricuspid valve. Prenatal diagnosis |
author |
Zielinsky,Paulo |
author_facet |
Zielinsky,Paulo Pilla,Carlo B. |
author_role |
author |
author2 |
Pilla,Carlo B. |
author2_role |
author |
dc.contributor.author.fl_str_mv |
Zielinsky,Paulo Pilla,Carlo B. |
description |
Ebstein's anomaly is an uncommon congenital heart defect, with a prevalence of 0.3-0.5%. Its association with an imperforate tricuspid valve is an even more rare situation (less than 10% of cases). Prenatal diagnosis of this association by means of fetal echocardiography has not been reported. We describe here this association diagnosed before birth and confirmed after birth. The diagnostic potential and importance of fetal echocardiography during prenatal evaluation of cardiac malformations allows for adequate perinatal planning and management, with an obvious impact on morbidity and mortality. |
publishDate |
2000 |
dc.date.none.fl_str_mv |
2000-07-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2000000700006 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S0066-782X2000000700006 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Cardiologia - SBC |
publisher.none.fl_str_mv |
Sociedade Brasileira de Cardiologia - SBC |
dc.source.none.fl_str_mv |
Arquivos Brasileiros de Cardiologia v.75 n.1 2000 reponame:Arquivos Brasileiros de Cardiologia (Online) instname:Sociedade Brasileira de Cardiologia (SBC) instacron:SBC |
instname_str |
Sociedade Brasileira de Cardiologia (SBC) |
instacron_str |
SBC |
institution |
SBC |
reponame_str |
Arquivos Brasileiros de Cardiologia (Online) |
collection |
Arquivos Brasileiros de Cardiologia (Online) |
repository.name.fl_str_mv |
Arquivos Brasileiros de Cardiologia (Online) - Sociedade Brasileira de Cardiologia (SBC) |
repository.mail.fl_str_mv |
||arquivos@cardiol.br |
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1752126551288184832 |