Biventricular Arrhythmogenic Cardiomyopathy: A New Paradigm?

• Main Author: Augusto,João
• Publication Date: 2018
• Other Authors: Abecasis,João, Gil,Victor
• Format: Report
• Language: eng
• Source: International Journal of Cardiovascular Sciences (Online)
• Download full: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S2359-56472018000600667
• topic: Cardiomyopathies; Arrhythmogenic Right Ventricular Dysplasia; Arrhythmias, Cardiac; Magnetic Resonance Imaging; Death, Sudden, Cardiac

Abstract Arrhythmogenic right ventricular dysplasia is a classic form of chronic myocardial disease with a broad phenotypical spectrum. We report an atypical case of a patient with biventricular arrhythmogenic cardiomyopathy. Although the current diagnosis criteria are the most widely accepted ones, they focus solely on the right ventricular phenotype. The use of late gadolinium enhancement in cardiac magnetic resonance in this patient was essential for the diagnosis and assessment of the left ventricular involvement extent. This tool allows a broader use of current diagnosis criteria for this disease.