Congenital Supravalvar Mitral Ring - A Case Report
Main Author: | |
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Publication Date: | 2020 |
Other Authors: | , , |
Format: | Report |
Language: | eng |
Source: | Brazilian Journal of Cardiovascular Surgery (Online) |
Download full: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382020000100117 |
Summary: | Abstract Congenital mitral valve stenosis is a rare and severe disease, usually associated with other heart defects. The appropriate intervention depends on the site and mechanism of valvular obstruction and the aim is to avoid or delay valve replacement since it is associated with significant morbidity and mortality. Early single-stage complete repair is associated with better prognosis. We report the case of a 20-month-old child with a supravalvar mitral ring combined with a ventricular septal defect; pulmonary arterial systolic pressure before the surgery was 79 mmHg. The patient underwent a successful surgical repair with good clinical resolution. |
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Congenital Supravalvar Mitral Ring - A Case ReportMitral Valve Stenosis. Heart DefectsCongenital. Systole. Arteries. Mitral Valve Stenosis. Blood Pressure. PrognosisAbstract Congenital mitral valve stenosis is a rare and severe disease, usually associated with other heart defects. The appropriate intervention depends on the site and mechanism of valvular obstruction and the aim is to avoid or delay valve replacement since it is associated with significant morbidity and mortality. Early single-stage complete repair is associated with better prognosis. We report the case of a 20-month-old child with a supravalvar mitral ring combined with a ventricular septal defect; pulmonary arterial systolic pressure before the surgery was 79 mmHg. The patient underwent a successful surgical repair with good clinical resolution.Sociedade Brasileira de Cirurgia Cardiovascular2020-01-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382020000100117Brazilian Journal of Cardiovascular Surgery v.35 n.1 2020reponame:Brazilian Journal of Cardiovascular Surgery (Online)instname:Sociedade Brasileira de Cirurgia Cardiovascular (SBCCV)instacron:SBCCV10.21470/1678-9741-2018-0403info:eu-repo/semantics/openAccessSoares,Raquel ReisFerber,LeonardoFerber,MatheusMata,Daniel Soareseng2020-03-17T00:00:00Zoai:scielo:S0102-76382020000100117Revistahttp://www.rbccv.org.br/https://old.scielo.br/oai/scielo-oai.php||rosangela.monteiro@incor.usp.br|| domingo@braile.com.br|| brandau@braile.com.br1678-97410102-7638opendoar:2020-03-17T00:00Brazilian Journal of Cardiovascular Surgery (Online) - Sociedade Brasileira de Cirurgia Cardiovascular (SBCCV)false |
dc.title.none.fl_str_mv |
Congenital Supravalvar Mitral Ring - A Case Report |
title |
Congenital Supravalvar Mitral Ring - A Case Report |
spellingShingle |
Congenital Supravalvar Mitral Ring - A Case Report Soares,Raquel Reis Mitral Valve Stenosis. Heart Defects Congenital. Systole. Arteries. Mitral Valve Stenosis. Blood Pressure. Prognosis |
title_short |
Congenital Supravalvar Mitral Ring - A Case Report |
title_full |
Congenital Supravalvar Mitral Ring - A Case Report |
title_fullStr |
Congenital Supravalvar Mitral Ring - A Case Report |
title_full_unstemmed |
Congenital Supravalvar Mitral Ring - A Case Report |
title_sort |
Congenital Supravalvar Mitral Ring - A Case Report |
author |
Soares,Raquel Reis |
author_facet |
Soares,Raquel Reis Ferber,Leonardo Ferber,Matheus Mata,Daniel Soares |
author_role |
author |
author2 |
Ferber,Leonardo Ferber,Matheus Mata,Daniel Soares |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Soares,Raquel Reis Ferber,Leonardo Ferber,Matheus Mata,Daniel Soares |
dc.subject.por.fl_str_mv |
Mitral Valve Stenosis. Heart Defects Congenital. Systole. Arteries. Mitral Valve Stenosis. Blood Pressure. Prognosis |
topic |
Mitral Valve Stenosis. Heart Defects Congenital. Systole. Arteries. Mitral Valve Stenosis. Blood Pressure. Prognosis |
description |
Abstract Congenital mitral valve stenosis is a rare and severe disease, usually associated with other heart defects. The appropriate intervention depends on the site and mechanism of valvular obstruction and the aim is to avoid or delay valve replacement since it is associated with significant morbidity and mortality. Early single-stage complete repair is associated with better prognosis. We report the case of a 20-month-old child with a supravalvar mitral ring combined with a ventricular septal defect; pulmonary arterial systolic pressure before the surgery was 79 mmHg. The patient underwent a successful surgical repair with good clinical resolution. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-01-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382020000100117 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0102-76382020000100117 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.21470/1678-9741-2018-0403 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Cirurgia Cardiovascular |
publisher.none.fl_str_mv |
Sociedade Brasileira de Cirurgia Cardiovascular |
dc.source.none.fl_str_mv |
Brazilian Journal of Cardiovascular Surgery v.35 n.1 2020 reponame:Brazilian Journal of Cardiovascular Surgery (Online) instname:Sociedade Brasileira de Cirurgia Cardiovascular (SBCCV) instacron:SBCCV |
instname_str |
Sociedade Brasileira de Cirurgia Cardiovascular (SBCCV) |
instacron_str |
SBCCV |
institution |
SBCCV |
reponame_str |
Brazilian Journal of Cardiovascular Surgery (Online) |
collection |
Brazilian Journal of Cardiovascular Surgery (Online) |
repository.name.fl_str_mv |
Brazilian Journal of Cardiovascular Surgery (Online) - Sociedade Brasileira de Cirurgia Cardiovascular (SBCCV) |
repository.mail.fl_str_mv |
||rosangela.monteiro@incor.usp.br|| domingo@braile.com.br|| brandau@braile.com.br |
_version_ |
1752126601155313664 |