Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report

Detalhes bibliográficos
Autor(a) principal: Bittencourt,Maraya de Jesus Semblano
Data de Publicação: 2013
Outros Autores: Dias,Carolina Moraes, Lage,Thaiane Lima, Barros,Renata Silva, Paz,Otavio Augusto Gomes, Vieira,Waldonio de Brito
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300448
Resumo: Behçet's disease is a chronic inflammatory disease of unknown aetiology, characterized by recurrent oral and genital aphthous ulcerations, uveitis, skin lesions and other multisystem affections associated with vasculitis. Different types of vessels, predominantly veins, can be affected in Behçet's disease. The frequency of vascular lesions in Behçet's disease, such as superficial and deep venous thromboses, arterial aneurysms and occlusions, ranges between 7-29%. Budd-Chiari syndrome is a rare and serious complication of Behçet's disease and implies thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. We report a case of a 25-year-old man with Behçet's disease that developed Budd-Chiari syndrome. The correlation of dermatological, pathological and imaging studies confirmed the diagnosis.
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spelling Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case reportBehcet diseaseBudd-Chiari SyndromeThrombosisBehçet's disease is a chronic inflammatory disease of unknown aetiology, characterized by recurrent oral and genital aphthous ulcerations, uveitis, skin lesions and other multisystem affections associated with vasculitis. Different types of vessels, predominantly veins, can be affected in Behçet's disease. The frequency of vascular lesions in Behçet's disease, such as superficial and deep venous thromboses, arterial aneurysms and occlusions, ranges between 7-29%. Budd-Chiari syndrome is a rare and serious complication of Behçet's disease and implies thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. We report a case of a 25-year-old man with Behçet's disease that developed Budd-Chiari syndrome. The correlation of dermatological, pathological and imaging studies confirmed the diagnosis.Sociedade Brasileira de Dermatologia2013-06-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300448Anais Brasileiros de Dermatologia v.88 n.3 2013reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20131930info:eu-repo/semantics/openAccessBittencourt,Maraya de Jesus SemblanoDias,Carolina MoraesLage,Thaiane LimaBarros,Renata SilvaPaz,Otavio Augusto GomesVieira,Waldonio de Britoeng2013-06-26T00:00:00Zoai:scielo:S0365-05962013000300448Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2013-06-26T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
title Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
spellingShingle Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
Bittencourt,Maraya de Jesus Semblano
Behcet disease
Budd-Chiari Syndrome
Thrombosis
title_short Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
title_full Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
title_fullStr Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
title_full_unstemmed Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
title_sort Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
author Bittencourt,Maraya de Jesus Semblano
author_facet Bittencourt,Maraya de Jesus Semblano
Dias,Carolina Moraes
Lage,Thaiane Lima
Barros,Renata Silva
Paz,Otavio Augusto Gomes
Vieira,Waldonio de Brito
author_role author
author2 Dias,Carolina Moraes
Lage,Thaiane Lima
Barros,Renata Silva
Paz,Otavio Augusto Gomes
Vieira,Waldonio de Brito
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Bittencourt,Maraya de Jesus Semblano
Dias,Carolina Moraes
Lage,Thaiane Lima
Barros,Renata Silva
Paz,Otavio Augusto Gomes
Vieira,Waldonio de Brito
dc.subject.por.fl_str_mv Behcet disease
Budd-Chiari Syndrome
Thrombosis
topic Behcet disease
Budd-Chiari Syndrome
Thrombosis
description Behçet's disease is a chronic inflammatory disease of unknown aetiology, characterized by recurrent oral and genital aphthous ulcerations, uveitis, skin lesions and other multisystem affections associated with vasculitis. Different types of vessels, predominantly veins, can be affected in Behçet's disease. The frequency of vascular lesions in Behçet's disease, such as superficial and deep venous thromboses, arterial aneurysms and occlusions, ranges between 7-29%. Budd-Chiari syndrome is a rare and serious complication of Behçet's disease and implies thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. We report a case of a 25-year-old man with Behçet's disease that developed Budd-Chiari syndrome. The correlation of dermatological, pathological and imaging studies confirmed the diagnosis.
publishDate 2013
dc.date.none.fl_str_mv 2013-06-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300448
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962013000300448
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20131930
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.88 n.3 2013
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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