Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis?
Autor(a) principal: | |
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Data de Publicação: | 2017 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Anais brasileiros de dermatologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000300410 |
Resumo: | Abstract Cutaneous and systemic plasmacytosis is a rare disorder characterized by cutaneous polyclonal plasma cell infiltration frequently associated with polyclonal hypergammaglobulinemia and lymphadenopathy. We report a case of a 67-year-old woman with an inflammatory ulcerated plaque in the left masseter region. A skin biopsy showed dense perivascular infiltrate of mature plasma cells in the dermis without atypia and immunoglobulin light chain restriction. After physical examination and further investigation, we ruled out systemic disease. Our patient was successfully treated only with hydrocortisone cream application. Few cases of isolated benign primary cutaneous plasmacytosis have been described, particularly in children. After excluding the diagnosis of a reactive process to an infection, which is unlikely in this case, we suspected of a rare manifestation of primary cutaneous plasmacytosis in adults with distinct presentation and clinical course. |
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Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis?Immunoglobulin light chainsHypergammaglobulinemiaPlasmacytomaAbstract Cutaneous and systemic plasmacytosis is a rare disorder characterized by cutaneous polyclonal plasma cell infiltration frequently associated with polyclonal hypergammaglobulinemia and lymphadenopathy. We report a case of a 67-year-old woman with an inflammatory ulcerated plaque in the left masseter region. A skin biopsy showed dense perivascular infiltrate of mature plasma cells in the dermis without atypia and immunoglobulin light chain restriction. After physical examination and further investigation, we ruled out systemic disease. Our patient was successfully treated only with hydrocortisone cream application. Few cases of isolated benign primary cutaneous plasmacytosis have been described, particularly in children. After excluding the diagnosis of a reactive process to an infection, which is unlikely in this case, we suspected of a rare manifestation of primary cutaneous plasmacytosis in adults with distinct presentation and clinical course.Sociedade Brasileira de Dermatologia2017-06-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000300410Anais Brasileiros de Dermatologia v.92 n.3 2017reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20175355info:eu-repo/semantics/openAccessAntónio,Ana MartaAlves,João VitorCoelho,RicardoBártolo,Elviraeng2017-09-13T00:00:00Zoai:scielo:S0365-05962017000300410Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2017-09-13T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false |
dc.title.none.fl_str_mv |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
title |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
spellingShingle |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? António,Ana Marta Immunoglobulin light chains Hypergammaglobulinemia Plasmacytoma |
title_short |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
title_full |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
title_fullStr |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
title_full_unstemmed |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
title_sort |
Solitary ulcerated plaque on the face - an unusual presentation of cutaneous plasmacytosis? |
author |
António,Ana Marta |
author_facet |
António,Ana Marta Alves,João Vitor Coelho,Ricardo Bártolo,Elvira |
author_role |
author |
author2 |
Alves,João Vitor Coelho,Ricardo Bártolo,Elvira |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
António,Ana Marta Alves,João Vitor Coelho,Ricardo Bártolo,Elvira |
dc.subject.por.fl_str_mv |
Immunoglobulin light chains Hypergammaglobulinemia Plasmacytoma |
topic |
Immunoglobulin light chains Hypergammaglobulinemia Plasmacytoma |
description |
Abstract Cutaneous and systemic plasmacytosis is a rare disorder characterized by cutaneous polyclonal plasma cell infiltration frequently associated with polyclonal hypergammaglobulinemia and lymphadenopathy. We report a case of a 67-year-old woman with an inflammatory ulcerated plaque in the left masseter region. A skin biopsy showed dense perivascular infiltrate of mature plasma cells in the dermis without atypia and immunoglobulin light chain restriction. After physical examination and further investigation, we ruled out systemic disease. Our patient was successfully treated only with hydrocortisone cream application. Few cases of isolated benign primary cutaneous plasmacytosis have been described, particularly in children. After excluding the diagnosis of a reactive process to an infection, which is unlikely in this case, we suspected of a rare manifestation of primary cutaneous plasmacytosis in adults with distinct presentation and clinical course. |
publishDate |
2017 |
dc.date.none.fl_str_mv |
2017-06-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000300410 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962017000300410 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/abd1806-4841.20175355 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Dermatologia |
dc.source.none.fl_str_mv |
Anais Brasileiros de Dermatologia v.92 n.3 2017 reponame:Anais brasileiros de dermatologia (Online) instname:Sociedade Brasileira de Dermatologia (SBD) instacron:SBD |
instname_str |
Sociedade Brasileira de Dermatologia (SBD) |
instacron_str |
SBD |
institution |
SBD |
reponame_str |
Anais brasileiros de dermatologia (Online) |
collection |
Anais brasileiros de dermatologia (Online) |
repository.name.fl_str_mv |
Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD) |
repository.mail.fl_str_mv |
abd@sbd.org.br||revista@sbd.org.br |
_version_ |
1752126422119350272 |