Syndrome in Question

Detalhes bibliográficos
Autor(a) principal: Meireles,Sheila Itamara Ferreira do Couto
Data de Publicação: 2014
Outros Autores: Andrade,Sônia Maria Fonseca de, Gomes,Maria Fernanda, Castro,Fernanda Aalmeida Nunes, Tebcherani,Antonio José
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Anais brasileiros de dermatologia (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000400679
Resumo: Rendu-Osler-Weber Syndrome also known as Hereditary Hemorrhagic Telangiectasia is a rare systemic fibrovascular dysplasia, with dominant autosomal inheritance. It is characterized by recurrent epistaxis, mucocutaneous telangiectasia, visceral arteriovenous malformation and positive family history. There may be hematologic, neurologic, dermatologic and gastrointestinal complications. Therapy is supportive and aimed at preventing complications. In this article we report a case of Rendu-Osler-Weber in a 64 year-old man, with history of mucocutaneous telangiectasia since the third decade of life, recurrent epistaxis, positive family history and vascular ectasia in the gastrointestinal tract.
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spelling Syndrome in QuestionArteriovenous fistulaEpistaxisGastrointestinal hemorrhageSkin abnormalitiesSkin diseases, vascularRendu-Osler-Weber Syndrome also known as Hereditary Hemorrhagic Telangiectasia is a rare systemic fibrovascular dysplasia, with dominant autosomal inheritance. It is characterized by recurrent epistaxis, mucocutaneous telangiectasia, visceral arteriovenous malformation and positive family history. There may be hematologic, neurologic, dermatologic and gastrointestinal complications. Therapy is supportive and aimed at preventing complications. In this article we report a case of Rendu-Osler-Weber in a 64 year-old man, with history of mucocutaneous telangiectasia since the third decade of life, recurrent epistaxis, positive family history and vascular ectasia in the gastrointestinal tract.Sociedade Brasileira de Dermatologia2014-08-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000400679Anais Brasileiros de Dermatologia v.89 n.4 2014reponame:Anais brasileiros de dermatologia (Online)instname:Sociedade Brasileira de Dermatologia (SBD)instacron:SBD10.1590/abd1806-4841.20142646info:eu-repo/semantics/openAccessMeireles,Sheila Itamara Ferreira do CoutoAndrade,Sônia Maria Fonseca deGomes,Maria FernandaCastro,Fernanda Aalmeida NunesTebcherani,Antonio Joséeng2014-07-23T00:00:00Zoai:scielo:S0365-05962014000400679Revistahttp://www.anaisdedermatologia.org.br/https://old.scielo.br/oai/scielo-oai.phpabd@sbd.org.br||revista@sbd.org.br1806-48410365-0596opendoar:2014-07-23T00:00Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)false
dc.title.none.fl_str_mv Syndrome in Question
title Syndrome in Question
spellingShingle Syndrome in Question
Meireles,Sheila Itamara Ferreira do Couto
Arteriovenous fistula
Epistaxis
Gastrointestinal hemorrhage
Skin abnormalities
Skin diseases, vascular
title_short Syndrome in Question
title_full Syndrome in Question
title_fullStr Syndrome in Question
title_full_unstemmed Syndrome in Question
title_sort Syndrome in Question
author Meireles,Sheila Itamara Ferreira do Couto
author_facet Meireles,Sheila Itamara Ferreira do Couto
Andrade,Sônia Maria Fonseca de
Gomes,Maria Fernanda
Castro,Fernanda Aalmeida Nunes
Tebcherani,Antonio José
author_role author
author2 Andrade,Sônia Maria Fonseca de
Gomes,Maria Fernanda
Castro,Fernanda Aalmeida Nunes
Tebcherani,Antonio José
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Meireles,Sheila Itamara Ferreira do Couto
Andrade,Sônia Maria Fonseca de
Gomes,Maria Fernanda
Castro,Fernanda Aalmeida Nunes
Tebcherani,Antonio José
dc.subject.por.fl_str_mv Arteriovenous fistula
Epistaxis
Gastrointestinal hemorrhage
Skin abnormalities
Skin diseases, vascular
topic Arteriovenous fistula
Epistaxis
Gastrointestinal hemorrhage
Skin abnormalities
Skin diseases, vascular
description Rendu-Osler-Weber Syndrome also known as Hereditary Hemorrhagic Telangiectasia is a rare systemic fibrovascular dysplasia, with dominant autosomal inheritance. It is characterized by recurrent epistaxis, mucocutaneous telangiectasia, visceral arteriovenous malformation and positive family history. There may be hematologic, neurologic, dermatologic and gastrointestinal complications. Therapy is supportive and aimed at preventing complications. In this article we report a case of Rendu-Osler-Weber in a 64 year-old man, with history of mucocutaneous telangiectasia since the third decade of life, recurrent epistaxis, positive family history and vascular ectasia in the gastrointestinal tract.
publishDate 2014
dc.date.none.fl_str_mv 2014-08-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000400679
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0365-05962014000400679
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/abd1806-4841.20142646
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
publisher.none.fl_str_mv Sociedade Brasileira de Dermatologia
dc.source.none.fl_str_mv Anais Brasileiros de Dermatologia v.89 n.4 2014
reponame:Anais brasileiros de dermatologia (Online)
instname:Sociedade Brasileira de Dermatologia (SBD)
instacron:SBD
instname_str Sociedade Brasileira de Dermatologia (SBD)
instacron_str SBD
institution SBD
reponame_str Anais brasileiros de dermatologia (Online)
collection Anais brasileiros de dermatologia (Online)
repository.name.fl_str_mv Anais brasileiros de dermatologia (Online) - Sociedade Brasileira de Dermatologia (SBD)
repository.mail.fl_str_mv abd@sbd.org.br||revista@sbd.org.br
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