Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Jornal Brasileiro de Nefrologia |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002020000300370 |
Resumo: | Abstract Encapsulating Peritoneal Sclerosis (EPS) is a severe and rare condition frequently associated with peritoneal dialysis, characterized by bowel obstruction, with lethal consequences in 20% of the patients. The disease presents as a mass of fibrous tissue encapsulating visceral organs that may potentially compromise digestive tract function. This report describes the case of a patient under peritoneal dialysis (PD) due to chronic kidney disease secondary to focal segmental glomerulosclerosis diagnosed with EPS. The patient had undergone two living-donor kidney transplant procedures. Surgical techniques and clinical measures employed to unravel bowel obstruction are described, which have been shown to ameliorate EPS secondary complications. Parenteral nutrition has significantly contributed to afford adequate nutrition, improving tissue healing as well as serum protein levels, vitamins and electrolytes. Therapy with tamoxifen and sodium thiosulfate effectively delayed the development of EPS. |
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Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case ReportPeritonitisPeritoneal DialysisOrgan TransplantationKidney TransplantationPeritoneal FibrosisAbstract Encapsulating Peritoneal Sclerosis (EPS) is a severe and rare condition frequently associated with peritoneal dialysis, characterized by bowel obstruction, with lethal consequences in 20% of the patients. The disease presents as a mass of fibrous tissue encapsulating visceral organs that may potentially compromise digestive tract function. This report describes the case of a patient under peritoneal dialysis (PD) due to chronic kidney disease secondary to focal segmental glomerulosclerosis diagnosed with EPS. The patient had undergone two living-donor kidney transplant procedures. Surgical techniques and clinical measures employed to unravel bowel obstruction are described, which have been shown to ameliorate EPS secondary complications. Parenteral nutrition has significantly contributed to afford adequate nutrition, improving tissue healing as well as serum protein levels, vitamins and electrolytes. Therapy with tamoxifen and sodium thiosulfate effectively delayed the development of EPS.Sociedade Brasileira de Nefrologia2020-09-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002020000300370Brazilian Journal of Nephrology v.42 n.3 2020reponame:Jornal Brasileiro de Nefrologiainstname:Sociedade Brasileira de Nefrologia (SBN)instacron:SBN10.1590/2175-8239-jbn-2019-0193info:eu-repo/semantics/openAccessRibeiro,Bruno Henrique DantasTakenaka,Vanessa SuemiBorges,Felipe SbroliniAndrade,Thales Franco deLessa,Sibele BragaMancero,Jorge Marcelo PadillaNoronha,Irene L.David,André Ibrahimeng2020-11-20T00:00:00Zoai:scielo:S0101-28002020000300370Revistahttp://www.bjn.org.br/ONGhttps://old.scielo.br/oai/scielo-oai.php||jbn@sbn.org.br2175-82390101-2800opendoar:2020-11-20T00:00Jornal Brasileiro de Nefrologia - Sociedade Brasileira de Nefrologia (SBN)false |
dc.title.none.fl_str_mv |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
title |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
spellingShingle |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report Ribeiro,Bruno Henrique Dantas Peritonitis Peritoneal Dialysis Organ Transplantation Kidney Transplantation Peritoneal Fibrosis |
title_short |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
title_full |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
title_fullStr |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
title_full_unstemmed |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
title_sort |
Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report |
author |
Ribeiro,Bruno Henrique Dantas |
author_facet |
Ribeiro,Bruno Henrique Dantas Takenaka,Vanessa Suemi Borges,Felipe Sbrolini Andrade,Thales Franco de Lessa,Sibele Braga Mancero,Jorge Marcelo Padilla Noronha,Irene L. David,André Ibrahim |
author_role |
author |
author2 |
Takenaka,Vanessa Suemi Borges,Felipe Sbrolini Andrade,Thales Franco de Lessa,Sibele Braga Mancero,Jorge Marcelo Padilla Noronha,Irene L. David,André Ibrahim |
author2_role |
author author author author author author author |
dc.contributor.author.fl_str_mv |
Ribeiro,Bruno Henrique Dantas Takenaka,Vanessa Suemi Borges,Felipe Sbrolini Andrade,Thales Franco de Lessa,Sibele Braga Mancero,Jorge Marcelo Padilla Noronha,Irene L. David,André Ibrahim |
dc.subject.por.fl_str_mv |
Peritonitis Peritoneal Dialysis Organ Transplantation Kidney Transplantation Peritoneal Fibrosis |
topic |
Peritonitis Peritoneal Dialysis Organ Transplantation Kidney Transplantation Peritoneal Fibrosis |
description |
Abstract Encapsulating Peritoneal Sclerosis (EPS) is a severe and rare condition frequently associated with peritoneal dialysis, characterized by bowel obstruction, with lethal consequences in 20% of the patients. The disease presents as a mass of fibrous tissue encapsulating visceral organs that may potentially compromise digestive tract function. This report describes the case of a patient under peritoneal dialysis (PD) due to chronic kidney disease secondary to focal segmental glomerulosclerosis diagnosed with EPS. The patient had undergone two living-donor kidney transplant procedures. Surgical techniques and clinical measures employed to unravel bowel obstruction are described, which have been shown to ameliorate EPS secondary complications. Parenteral nutrition has significantly contributed to afford adequate nutrition, improving tissue healing as well as serum protein levels, vitamins and electrolytes. Therapy with tamoxifen and sodium thiosulfate effectively delayed the development of EPS. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-09-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002020000300370 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002020000300370 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/2175-8239-jbn-2019-0193 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Brasileira de Nefrologia |
publisher.none.fl_str_mv |
Sociedade Brasileira de Nefrologia |
dc.source.none.fl_str_mv |
Brazilian Journal of Nephrology v.42 n.3 2020 reponame:Jornal Brasileiro de Nefrologia instname:Sociedade Brasileira de Nefrologia (SBN) instacron:SBN |
instname_str |
Sociedade Brasileira de Nefrologia (SBN) |
instacron_str |
SBN |
institution |
SBN |
reponame_str |
Jornal Brasileiro de Nefrologia |
collection |
Jornal Brasileiro de Nefrologia |
repository.name.fl_str_mv |
Jornal Brasileiro de Nefrologia - Sociedade Brasileira de Nefrologia (SBN) |
repository.mail.fl_str_mv |
||jbn@sbn.org.br |
_version_ |
1752122066147999744 |