Encapsulating Peritoneal Sclerosis in a kidney transplant recipient - Case Report

Detalhes bibliográficos
Autor(a) principal: Ribeiro,Bruno Henrique Dantas
Data de Publicação: 2020
Outros Autores: Takenaka,Vanessa Suemi, Borges,Felipe Sbrolini, Andrade,Thales Franco de, Lessa,Sibele Braga, Mancero,Jorge Marcelo Padilla, Noronha,Irene L., David,André Ibrahim
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Jornal Brasileiro de Nefrologia
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002020000300370
Resumo: Abstract Encapsulating Peritoneal Sclerosis (EPS) is a severe and rare condition frequently associated with peritoneal dialysis, characterized by bowel obstruction, with lethal consequences in 20% of the patients. The disease presents as a mass of fibrous tissue encapsulating visceral organs that may potentially compromise digestive tract function. This report describes the case of a patient under peritoneal dialysis (PD) due to chronic kidney disease secondary to focal segmental glomerulosclerosis diagnosed with EPS. The patient had undergone two living-donor kidney transplant procedures. Surgical techniques and clinical measures employed to unravel bowel obstruction are described, which have been shown to ameliorate EPS secondary complications. Parenteral nutrition has significantly contributed to afford adequate nutrition, improving tissue healing as well as serum protein levels, vitamins and electrolytes. Therapy with tamoxifen and sodium thiosulfate effectively delayed the development of EPS.