Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia

Detalhes bibliográficos
Autor(a) principal: Silva, Ruanna Caribé Ribeiro da
Data de Publicação: 2021
Outros Autores: Barbosa, Suane Pereira de Oliveira Rios, Silva, Maria Emília Cirqueira, Galvão, Caroline Ramalho, Oliveira, Ana Clara Silva, Dantas, Bruna Matos Santos, Sampaio, Lorena Moura de Assis, Monção, Maurício Mitsuo da, Mercês, Magno Conceição das, Conceição, Sarah dos Santos, Silva, Roberta Borges, França, Lyvia Mirelle Carneiro de, Coelho, Julita Maria Freitas
Tipo de documento: Artigo
Idioma: por
Título da fonte: Research, Society and Development
Texto Completo: https://rsdjournal.org/index.php/rsd/article/view/16510
Resumo: Sickle cell disease (SCD) is a hemoglobinopathy of predominance of hemoglobin S in red blood cells, of a genetic character. The objective of this study was to describe the epidemiological and clinical profile of 64 users with DF from the Municipal Reference Center for people with DF in the municipality of Feira de Santana / BA, from November 2016 to March 2017. The present study was submitted and approved by a research ethics committee. The predominance was female, race / color was brown / black, education less than 8 years of study, income less than or equal to a minimum wage and without occupation. As for clinical conditions, most had a medical diagnosis of sickle cell anemia and the disease was discovered through the heel prick test. Although the majority did not have comorbidities, a high number of participants presented some type of complication related to the disease, with more frequent pain attacks, pneumonia, acute chest syndrome and splenic sequestration. The results presented can be used by the service as an instrument to outline a care plan for this population according to the epidemiological and clinical profile of users, as well as reinforcing the importance of strategies such as health education, to minimize the occurrence of complications.
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spelling Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/BahiaPerfil Epidemiológico y Clínico de los Usuarios del Centro Municipal de Referencia para Personas con Drepanocitosis en Feira de Santana / BahiaPerfil epidemiológico e clínico de usuários do centro municipal de referência de indivíduos com doença falciforme em Feira de Santana/BahiaAnemia Falciforme;Hemoglobina FalciformeTraço FalciformeEpidemiologia.DrepanocitoEl rasgo de células falciformesAnemiaEpidemiología.AnemiaSickle cellSickle cell traitEpidemiology.Sickle cell disease (SCD) is a hemoglobinopathy of predominance of hemoglobin S in red blood cells, of a genetic character. The objective of this study was to describe the epidemiological and clinical profile of 64 users with DF from the Municipal Reference Center for people with DF in the municipality of Feira de Santana / BA, from November 2016 to March 2017. The present study was submitted and approved by a research ethics committee. The predominance was female, race / color was brown / black, education less than 8 years of study, income less than or equal to a minimum wage and without occupation. As for clinical conditions, most had a medical diagnosis of sickle cell anemia and the disease was discovered through the heel prick test. Although the majority did not have comorbidities, a high number of participants presented some type of complication related to the disease, with more frequent pain attacks, pneumonia, acute chest syndrome and splenic sequestration. The results presented can be used by the service as an instrument to outline a care plan for this population according to the epidemiological and clinical profile of users, as well as reinforcing the importance of strategies such as health education, to minimize the occurrence of complications.La anemia de células falciformes (ECF) es una hemoglobinopatía de predominio de la hemoglobina S en los glóbulos rojos, de carácter genético. El objetivo de este estudio fue describir el perfil epidemiológico y clínico de 64 usuarios con FD del Centro Municipal de Referencia para personas con FD en el municipio de Feira de Santana / BA, de noviembre de 2016 a marzo de 2017. El presente estudio fue presentado y aprobado por un comité de ética en investigación. El predominio fue femenino, raza / color marrón / negro, educación menor a 8 años de estudio, ingreso menor o igual al salario mínimo y sin ocupación. En cuanto a las condiciones clínicas, la mayoría tenía un diagnóstico médico de anemia de células falciformes y la enfermedad se descubrió mediante la prueba de punción del talón. Aunque la mayoría no presentaba comorbilidades, un elevado número de participantes presentó algún tipo de complicación relacionada con la enfermedad, con más frecuentes crisis de dolor, neumonía, síndrome torácico agudo y secuestro esplénico. Los resultados presentados pueden ser utilizados por el servicio como instrumento para delinear un plan de atención a esta población de acuerdo al perfil epidemiológico y clínico de los usuarios, así como reforzar la importancia de estrategias como la educación en salud, para minimizar la ocurrencia de complicaciones.A Doença Falciforme (DF) é uma hemoglobinopatia de predominância da hemoglobina S nas hemácias, de caráter genético. O objetivo deste trabalho foi descrever o perfil epidemiológico e clínico de 64 usuários com DF do Centro Municipal de Referência à pessoa com DF no município de Feira de Santana/BA, no período de novembro de 2016 a março de 2017. O presente estudo foi submetido e aprovado por um comitê de ética em pesquisa. A predominância foi do sexo feminino, raça/cor foi parda/preta, escolaridade menor que 8 anos de estudo, renda menor ou igual um salário mínimo e sem ocupação. Quanto às condições clínicas, a maioria teve diagnóstico médico de anemia falciforme e a descoberta da doença ocorreu via teste do pezinho. Embora a maioria não possuísse comorbidades, um elevado número de participantes apresentou algum tipo de complicação referente à doença, sendo mais frequentes as crises álgicas, pneumonia, síndrome torácica aguda e sequestro esplênico. Os resultados apresentados podem ser usados pelo serviço como instrumento para traçar um plano de cuidado para essa população de acordo com o perfil epidemiológico e clínico dos usuários, bem como, reforça a importância de estratégias como a educação em saúde, para minimizar a ocorrência das complicações.Research, Society and Development2021-06-18info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://rsdjournal.org/index.php/rsd/article/view/1651010.33448/rsd-v10i7.16510Research, Society and Development; Vol. 10 No. 7; e22510716510Research, Society and Development; Vol. 10 Núm. 7; e22510716510Research, Society and Development; v. 10 n. 7; e225107165102525-3409reponame:Research, Society and Developmentinstname:Universidade Federal de Itajubá (UNIFEI)instacron:UNIFEIporhttps://rsdjournal.org/index.php/rsd/article/view/16510/18116Copyright (c) 2021 Ruanna Caribé Ribeiro da Silva; Suane Pereira de Oliveira Rios Barbosa; Maria Emília Cirqueira Silva; Caroline Ramalho Galvão; Ana Clara Silva Oliveira; Bruna Matos Santos Dantas; Lorena Moura de Assis Sampaio; Maurício Mitsuo da Monção; Magno Conceição das Mercês; Sarah dos Santos Conceição; Roberta Borges Silva; Lyvia Mirelle Carneiro de França; Julita Maria Freitas Coelhohttps://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccess Silva, Ruanna Caribé Ribeiro da Barbosa, Suane Pereira de Oliveira RiosSilva, Maria Emília CirqueiraGalvão, Caroline RamalhoOliveira, Ana Clara SilvaDantas, Bruna Matos Santos Sampaio, Lorena Moura de AssisMonção, Maurício Mitsuo da Mercês, Magno Conceição das Conceição, Sarah dos SantosSilva, Roberta Borges França, Lyvia Mirelle Carneiro de Coelho, Julita Maria Freitas2021-07-18T21:07:03Zoai:ojs.pkp.sfu.ca:article/16510Revistahttps://rsdjournal.org/index.php/rsd/indexPUBhttps://rsdjournal.org/index.php/rsd/oairsd.articles@gmail.com2525-34092525-3409opendoar:2024-01-17T09:37:02.354300Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)false
dc.title.none.fl_str_mv Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
Perfil Epidemiológico y Clínico de los Usuarios del Centro Municipal de Referencia para Personas con Drepanocitosis en Feira de Santana / Bahia
Perfil epidemiológico e clínico de usuários do centro municipal de referência de indivíduos com doença falciforme em Feira de Santana/Bahia
title Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
spellingShingle Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
Silva, Ruanna Caribé Ribeiro da
Anemia Falciforme;
Hemoglobina Falciforme
Traço Falciforme
Epidemiologia.
Drepanocito
El rasgo de células falciformes
Anemia
Epidemiología.
Anemia
Sickle cell
Sickle cell trait
Epidemiology.
title_short Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
title_full Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
title_fullStr Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
title_full_unstemmed Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
title_sort Epidemiological and Clinical Profile of Users of the Municipal Reference Center for Individuals With Sickle Cell Disease in Feira de Santana/Bahia
author Silva, Ruanna Caribé Ribeiro da
author_facet Silva, Ruanna Caribé Ribeiro da
Barbosa, Suane Pereira de Oliveira Rios
Silva, Maria Emília Cirqueira
Galvão, Caroline Ramalho
Oliveira, Ana Clara Silva
Dantas, Bruna Matos Santos
Sampaio, Lorena Moura de Assis
Monção, Maurício Mitsuo da
Mercês, Magno Conceição das
Conceição, Sarah dos Santos
Silva, Roberta Borges
França, Lyvia Mirelle Carneiro de
Coelho, Julita Maria Freitas
author_role author
author2 Barbosa, Suane Pereira de Oliveira Rios
Silva, Maria Emília Cirqueira
Galvão, Caroline Ramalho
Oliveira, Ana Clara Silva
Dantas, Bruna Matos Santos
Sampaio, Lorena Moura de Assis
Monção, Maurício Mitsuo da
Mercês, Magno Conceição das
Conceição, Sarah dos Santos
Silva, Roberta Borges
França, Lyvia Mirelle Carneiro de
Coelho, Julita Maria Freitas
author2_role author
author
author
author
author
author
author
author
author
author
author
author
dc.contributor.author.fl_str_mv Silva, Ruanna Caribé Ribeiro da
Barbosa, Suane Pereira de Oliveira Rios
Silva, Maria Emília Cirqueira
Galvão, Caroline Ramalho
Oliveira, Ana Clara Silva
Dantas, Bruna Matos Santos
Sampaio, Lorena Moura de Assis
Monção, Maurício Mitsuo da
Mercês, Magno Conceição das
Conceição, Sarah dos Santos
Silva, Roberta Borges
França, Lyvia Mirelle Carneiro de
Coelho, Julita Maria Freitas
dc.subject.por.fl_str_mv Anemia Falciforme;
Hemoglobina Falciforme
Traço Falciforme
Epidemiologia.
Drepanocito
El rasgo de células falciformes
Anemia
Epidemiología.
Anemia
Sickle cell
Sickle cell trait
Epidemiology.
topic Anemia Falciforme;
Hemoglobina Falciforme
Traço Falciforme
Epidemiologia.
Drepanocito
El rasgo de células falciformes
Anemia
Epidemiología.
Anemia
Sickle cell
Sickle cell trait
Epidemiology.
description Sickle cell disease (SCD) is a hemoglobinopathy of predominance of hemoglobin S in red blood cells, of a genetic character. The objective of this study was to describe the epidemiological and clinical profile of 64 users with DF from the Municipal Reference Center for people with DF in the municipality of Feira de Santana / BA, from November 2016 to March 2017. The present study was submitted and approved by a research ethics committee. The predominance was female, race / color was brown / black, education less than 8 years of study, income less than or equal to a minimum wage and without occupation. As for clinical conditions, most had a medical diagnosis of sickle cell anemia and the disease was discovered through the heel prick test. Although the majority did not have comorbidities, a high number of participants presented some type of complication related to the disease, with more frequent pain attacks, pneumonia, acute chest syndrome and splenic sequestration. The results presented can be used by the service as an instrument to outline a care plan for this population according to the epidemiological and clinical profile of users, as well as reinforcing the importance of strategies such as health education, to minimize the occurrence of complications.
publishDate 2021
dc.date.none.fl_str_mv 2021-06-18
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/16510
10.33448/rsd-v10i7.16510
url https://rsdjournal.org/index.php/rsd/article/view/16510
identifier_str_mv 10.33448/rsd-v10i7.16510
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rsdjournal.org/index.php/rsd/article/view/16510/18116
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Research, Society and Development
publisher.none.fl_str_mv Research, Society and Development
dc.source.none.fl_str_mv Research, Society and Development; Vol. 10 No. 7; e22510716510
Research, Society and Development; Vol. 10 Núm. 7; e22510716510
Research, Society and Development; v. 10 n. 7; e22510716510
2525-3409
reponame:Research, Society and Development
instname:Universidade Federal de Itajubá (UNIFEI)
instacron:UNIFEI
instname_str Universidade Federal de Itajubá (UNIFEI)
instacron_str UNIFEI
institution UNIFEI
reponame_str Research, Society and Development
collection Research, Society and Development
repository.name.fl_str_mv Research, Society and Development - Universidade Federal de Itajubá (UNIFEI)
repository.mail.fl_str_mv rsd.articles@gmail.com
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