Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies

Detalhes bibliográficos
Autor(a) principal: Fontenele,J.P.U.
Data de Publicação: 2016
Outros Autores: Schenka,A.A., Hessel,G., Jarry,V.M., Escanhoela,C.A.F.
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Brazilian Journal of Medical and Biological Research
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-879X2016000300501
Resumo: Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
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spelling Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studiesKasai operationCholestatic syndromeInfantsBiliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.Associação Brasileira de Divulgação Científica2016-03-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-879X2016000300501Brazilian Journal of Medical and Biological Research v.49 n.3 2016reponame:Brazilian Journal of Medical and Biological Researchinstname:Associação Brasileira de Divulgação Científica (ABDC)instacron:ABDC10.1590/1414-431X20154808info:eu-repo/semantics/openAccessFontenele,J.P.U.Schenka,A.A.Hessel,G.Jarry,V.M.Escanhoela,C.A.F.eng2016-02-18T00:00:00Zoai:scielo:S0100-879X2016000300501Revistahttps://www.bjournal.org/https://old.scielo.br/oai/scielo-oai.phpbjournal@terra.com.br||bjournal@terra.com.br1414-431X0100-879Xopendoar:2016-02-18T00:00Brazilian Journal of Medical and Biological Research - Associação Brasileira de Divulgação Científica (ABDC)false
dc.title.none.fl_str_mv Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
title Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
spellingShingle Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
Fontenele,J.P.U.
Kasai operation
Cholestatic syndrome
Infants
title_short Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
title_full Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
title_fullStr Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
title_full_unstemmed Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
title_sort Clinical and pathological challenges in the diagnosis of late-onset biliary atresia: four case studies
author Fontenele,J.P.U.
author_facet Fontenele,J.P.U.
Schenka,A.A.
Hessel,G.
Jarry,V.M.
Escanhoela,C.A.F.
author_role author
author2 Schenka,A.A.
Hessel,G.
Jarry,V.M.
Escanhoela,C.A.F.
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Fontenele,J.P.U.
Schenka,A.A.
Hessel,G.
Jarry,V.M.
Escanhoela,C.A.F.
dc.subject.por.fl_str_mv Kasai operation
Cholestatic syndrome
Infants
topic Kasai operation
Cholestatic syndrome
Infants
description Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
publishDate 2016
dc.date.none.fl_str_mv 2016-03-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-879X2016000300501
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0100-879X2016000300501
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1414-431X20154808
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Associação Brasileira de Divulgação Científica
publisher.none.fl_str_mv Associação Brasileira de Divulgação Científica
dc.source.none.fl_str_mv Brazilian Journal of Medical and Biological Research v.49 n.3 2016
reponame:Brazilian Journal of Medical and Biological Research
instname:Associação Brasileira de Divulgação Científica (ABDC)
instacron:ABDC
instname_str Associação Brasileira de Divulgação Científica (ABDC)
instacron_str ABDC
institution ABDC
reponame_str Brazilian Journal of Medical and Biological Research
collection Brazilian Journal of Medical and Biological Research
repository.name.fl_str_mv Brazilian Journal of Medical and Biological Research - Associação Brasileira de Divulgação Científica (ABDC)
repository.mail.fl_str_mv bjournal@terra.com.br||bjournal@terra.com.br
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