Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry
Autor(a) principal: | |
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Data de Publicação: | 1999 |
Outros Autores: | , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Arquivos de neuro-psiquiatria (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1999000200002 |
Resumo: | Subacute sclerosing panencephalitis (SSPE) is an inflammatory neurodegenerative disease related to the persistence of measles virus. Although its frequency is declining because of measles eradication, we still have some cases being diagnosed. With the aim to describe epidemiological aspects of SSPE in Brazil, we sent a protocol to Child Neurologists around the country, 48 patients were registered, 27 (56 %) were from the southeast region, 34 (71%) were male and 35 (73%) white, 27 (56%) had measles, 9 (19%) had measles and were also immunized, 7 (14%) received only immunization, 1 patient had a probable neonatal form. Mean time between first symptoms and diagnosis was 12 months (22 started with myoclonus or tonic-clonic seizures, 7 (14%) with behavioral disturbances); 36 patients (75%) had EEG with pseudoperiodic complexes. Follow up performed in 28 (58 %) patients showed: 12 died, 2 had complete remission and the others had variable neurological disability Our data shows endemic regions in the country, a high incidence of post-immunization SSPE and a delay between first symptom and diagnosis. |
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Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registryimmunizationmeaslesseizuressubacute sclerosing panencephalitisSubacute sclerosing panencephalitis (SSPE) is an inflammatory neurodegenerative disease related to the persistence of measles virus. Although its frequency is declining because of measles eradication, we still have some cases being diagnosed. With the aim to describe epidemiological aspects of SSPE in Brazil, we sent a protocol to Child Neurologists around the country, 48 patients were registered, 27 (56 %) were from the southeast region, 34 (71%) were male and 35 (73%) white, 27 (56%) had measles, 9 (19%) had measles and were also immunized, 7 (14%) received only immunization, 1 patient had a probable neonatal form. Mean time between first symptoms and diagnosis was 12 months (22 started with myoclonus or tonic-clonic seizures, 7 (14%) with behavioral disturbances); 36 patients (75%) had EEG with pseudoperiodic complexes. Follow up performed in 28 (58 %) patients showed: 12 died, 2 had complete remission and the others had variable neurological disability Our data shows endemic regions in the country, a high incidence of post-immunization SSPE and a delay between first symptom and diagnosis.Academia Brasileira de Neurologia - ABNEURO1999-06-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1999000200002Arquivos de Neuro-Psiquiatria v.57 n.2A 1999reponame:Arquivos de neuro-psiquiatria (Online)instname:Academia Brasileira de Neurologiainstacron:ABNEURO10.1590/S0004-282X1999000200002info:eu-repo/semantics/openAccessNUNES,MAGDA LAHORGUECOSTA,JADERSON COSTA DASTANCHER,VANESSA M.DIAMENT,ARONARITA,FERNANDOROSEMBERG,SÉRGIODYKEN,PAULeng2000-12-06T00:00:00Zoai:scielo:S0004-282X1999000200002Revistahttp://www.scielo.br/anphttps://old.scielo.br/oai/scielo-oai.php||revista.arquivos@abneuro.org1678-42270004-282Xopendoar:2000-12-06T00:00Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologiafalse |
dc.title.none.fl_str_mv |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
title |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
spellingShingle |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry NUNES,MAGDA LAHORGUE immunization measles seizures subacute sclerosing panencephalitis |
title_short |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
title_full |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
title_fullStr |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
title_full_unstemmed |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
title_sort |
Subacute sclerosing panencephalitis: clinical aspects and prognosis. The Brazilian Registry |
author |
NUNES,MAGDA LAHORGUE |
author_facet |
NUNES,MAGDA LAHORGUE COSTA,JADERSON COSTA DA STANCHER,VANESSA M. DIAMENT,ARON ARITA,FERNANDO ROSEMBERG,SÉRGIO DYKEN,PAUL |
author_role |
author |
author2 |
COSTA,JADERSON COSTA DA STANCHER,VANESSA M. DIAMENT,ARON ARITA,FERNANDO ROSEMBERG,SÉRGIO DYKEN,PAUL |
author2_role |
author author author author author author |
dc.contributor.author.fl_str_mv |
NUNES,MAGDA LAHORGUE COSTA,JADERSON COSTA DA STANCHER,VANESSA M. DIAMENT,ARON ARITA,FERNANDO ROSEMBERG,SÉRGIO DYKEN,PAUL |
dc.subject.por.fl_str_mv |
immunization measles seizures subacute sclerosing panencephalitis |
topic |
immunization measles seizures subacute sclerosing panencephalitis |
description |
Subacute sclerosing panencephalitis (SSPE) is an inflammatory neurodegenerative disease related to the persistence of measles virus. Although its frequency is declining because of measles eradication, we still have some cases being diagnosed. With the aim to describe epidemiological aspects of SSPE in Brazil, we sent a protocol to Child Neurologists around the country, 48 patients were registered, 27 (56 %) were from the southeast region, 34 (71%) were male and 35 (73%) white, 27 (56%) had measles, 9 (19%) had measles and were also immunized, 7 (14%) received only immunization, 1 patient had a probable neonatal form. Mean time between first symptoms and diagnosis was 12 months (22 started with myoclonus or tonic-clonic seizures, 7 (14%) with behavioral disturbances); 36 patients (75%) had EEG with pseudoperiodic complexes. Follow up performed in 28 (58 %) patients showed: 12 died, 2 had complete remission and the others had variable neurological disability Our data shows endemic regions in the country, a high incidence of post-immunization SSPE and a delay between first symptom and diagnosis. |
publishDate |
1999 |
dc.date.none.fl_str_mv |
1999-06-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1999000200002 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X1999000200002 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S0004-282X1999000200002 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
dc.source.none.fl_str_mv |
Arquivos de Neuro-Psiquiatria v.57 n.2A 1999 reponame:Arquivos de neuro-psiquiatria (Online) instname:Academia Brasileira de Neurologia instacron:ABNEURO |
instname_str |
Academia Brasileira de Neurologia |
instacron_str |
ABNEURO |
institution |
ABNEURO |
reponame_str |
Arquivos de neuro-psiquiatria (Online) |
collection |
Arquivos de neuro-psiquiatria (Online) |
repository.name.fl_str_mv |
Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologia |
repository.mail.fl_str_mv |
||revista.arquivos@abneuro.org |
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1754212751463415808 |