Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease
Autor(a) principal: | |
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Data de Publicação: | 2003 |
Outros Autores: | , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Arquivos de neuro-psiquiatria (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000200018 |
Resumo: | OBJECTIVE: The aim of this report is to describe a fatal disseminated thrombotic micoangiopathy with renal, pancreatic, and cerebral involvement in a patient with recently diagnosed adult's Still disease (ASD). CASE REPORT: A previously healthy 15 year old girl was admitted to our hospital. According to the clinical and laboratory data the diagnosis of adult's still Disease was established. The treatment was begun and few days after an initial improvement a sudden neurologic deterioration with coma and seizures has occurred. Hours later the patient died. Clinical, laboratorial, and pathologic data will be presented. CONCLUSION: To our knowledge this is the second description of a fatal disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease, but with a much more fulminating evolution than previously reported. Some etiopathogenic mechanisms could be shared in these two disorders explaining this coexistence. |
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Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still diseaseadult's Still diseasecerebral thrombotic microangiopathythrombotic thrombocitopenic purpuraOBJECTIVE: The aim of this report is to describe a fatal disseminated thrombotic micoangiopathy with renal, pancreatic, and cerebral involvement in a patient with recently diagnosed adult's Still disease (ASD). CASE REPORT: A previously healthy 15 year old girl was admitted to our hospital. According to the clinical and laboratory data the diagnosis of adult's still Disease was established. The treatment was begun and few days after an initial improvement a sudden neurologic deterioration with coma and seizures has occurred. Hours later the patient died. Clinical, laboratorial, and pathologic data will be presented. CONCLUSION: To our knowledge this is the second description of a fatal disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease, but with a much more fulminating evolution than previously reported. Some etiopathogenic mechanisms could be shared in these two disorders explaining this coexistence.Academia Brasileira de Neurologia - ABNEURO2003-06-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000200018Arquivos de Neuro-Psiquiatria v.61 n.2A 2003reponame:Arquivos de neuro-psiquiatria (Online)instname:Academia Brasileira de Neurologiainstacron:ABNEURO10.1590/S0004-282X2003000200018info:eu-repo/semantics/openAccessDomingues,Renan B.Gama,Ana Maria Casati daCaser,Eliana B.Musso,CarlosSantos,Maria Carmen S.eng2003-06-09T00:00:00Zoai:scielo:S0004-282X2003000200018Revistahttp://www.scielo.br/anphttps://old.scielo.br/oai/scielo-oai.php||revista.arquivos@abneuro.org1678-42270004-282Xopendoar:2003-06-09T00:00Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologiafalse |
dc.title.none.fl_str_mv |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
title |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
spellingShingle |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease Domingues,Renan B. adult's Still disease cerebral thrombotic microangiopathy thrombotic thrombocitopenic purpura |
title_short |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
title_full |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
title_fullStr |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
title_full_unstemmed |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
title_sort |
Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease |
author |
Domingues,Renan B. |
author_facet |
Domingues,Renan B. Gama,Ana Maria Casati da Caser,Eliana B. Musso,Carlos Santos,Maria Carmen S. |
author_role |
author |
author2 |
Gama,Ana Maria Casati da Caser,Eliana B. Musso,Carlos Santos,Maria Carmen S. |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Domingues,Renan B. Gama,Ana Maria Casati da Caser,Eliana B. Musso,Carlos Santos,Maria Carmen S. |
dc.subject.por.fl_str_mv |
adult's Still disease cerebral thrombotic microangiopathy thrombotic thrombocitopenic purpura |
topic |
adult's Still disease cerebral thrombotic microangiopathy thrombotic thrombocitopenic purpura |
description |
OBJECTIVE: The aim of this report is to describe a fatal disseminated thrombotic micoangiopathy with renal, pancreatic, and cerebral involvement in a patient with recently diagnosed adult's Still disease (ASD). CASE REPORT: A previously healthy 15 year old girl was admitted to our hospital. According to the clinical and laboratory data the diagnosis of adult's still Disease was established. The treatment was begun and few days after an initial improvement a sudden neurologic deterioration with coma and seizures has occurred. Hours later the patient died. Clinical, laboratorial, and pathologic data will be presented. CONCLUSION: To our knowledge this is the second description of a fatal disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease, but with a much more fulminating evolution than previously reported. Some etiopathogenic mechanisms could be shared in these two disorders explaining this coexistence. |
publishDate |
2003 |
dc.date.none.fl_str_mv |
2003-06-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000200018 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2003000200018 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S0004-282X2003000200018 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
publisher.none.fl_str_mv |
Academia Brasileira de Neurologia - ABNEURO |
dc.source.none.fl_str_mv |
Arquivos de Neuro-Psiquiatria v.61 n.2A 2003 reponame:Arquivos de neuro-psiquiatria (Online) instname:Academia Brasileira de Neurologia instacron:ABNEURO |
instname_str |
Academia Brasileira de Neurologia |
instacron_str |
ABNEURO |
institution |
ABNEURO |
reponame_str |
Arquivos de neuro-psiquiatria (Online) |
collection |
Arquivos de neuro-psiquiatria (Online) |
repository.name.fl_str_mv |
Arquivos de neuro-psiquiatria (Online) - Academia Brasileira de Neurologia |
repository.mail.fl_str_mv |
||revista.arquivos@abneuro.org |
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1754212755452198912 |