Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
Autor(a) principal: | |
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Data de Publicação: | 2018 |
Outros Autores: | , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Revista da Associação Médica Brasileira (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195 |
Resumo: | Summary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely. |
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Pseudomyxoma peritonei in a pediatric patient: A case report and literature reviewPseudomyxoma PeritoneiChildTomography, X-ray ComputedMagnetic Resonance SpectroscopySummary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely.Associação Médica Brasileira2018-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195Revista da Associação Médica Brasileira v.64 n.2 2018reponame:Revista da Associação Médica Brasileira (Online)instname:Associação Médica Brasileira (AMB)instacron:AMB10.1590/1806-9282.64.02.195info:eu-repo/semantics/openAccessFernandes,Ana Claudia de OliveiraRocha,Gustavo Ricardo Martins daOliveira,Alex Dias deGuimarães,Marcos DuarteCarvalho,Stefane Cajango deChojniak,Rubenseng2018-04-02T00:00:00Zoai:scielo:S0104-42302018000200195Revistahttps://ramb.amb.org.br/ultimas-edicoes/#https://old.scielo.br/oai/scielo-oai.php||ramb@amb.org.br1806-92820104-4230opendoar:2018-04-02T00:00Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB)false |
dc.title.none.fl_str_mv |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
title |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
spellingShingle |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review Fernandes,Ana Claudia de Oliveira Pseudomyxoma Peritonei Child Tomography, X-ray Computed Magnetic Resonance Spectroscopy |
title_short |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
title_full |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
title_fullStr |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
title_full_unstemmed |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
title_sort |
Pseudomyxoma peritonei in a pediatric patient: A case report and literature review |
author |
Fernandes,Ana Claudia de Oliveira |
author_facet |
Fernandes,Ana Claudia de Oliveira Rocha,Gustavo Ricardo Martins da Oliveira,Alex Dias de Guimarães,Marcos Duarte Carvalho,Stefane Cajango de Chojniak,Rubens |
author_role |
author |
author2 |
Rocha,Gustavo Ricardo Martins da Oliveira,Alex Dias de Guimarães,Marcos Duarte Carvalho,Stefane Cajango de Chojniak,Rubens |
author2_role |
author author author author author |
dc.contributor.author.fl_str_mv |
Fernandes,Ana Claudia de Oliveira Rocha,Gustavo Ricardo Martins da Oliveira,Alex Dias de Guimarães,Marcos Duarte Carvalho,Stefane Cajango de Chojniak,Rubens |
dc.subject.por.fl_str_mv |
Pseudomyxoma Peritonei Child Tomography, X-ray Computed Magnetic Resonance Spectroscopy |
topic |
Pseudomyxoma Peritonei Child Tomography, X-ray Computed Magnetic Resonance Spectroscopy |
description |
Summary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely. |
publishDate |
2018 |
dc.date.none.fl_str_mv |
2018-02-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/1806-9282.64.02.195 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Associação Médica Brasileira |
publisher.none.fl_str_mv |
Associação Médica Brasileira |
dc.source.none.fl_str_mv |
Revista da Associação Médica Brasileira v.64 n.2 2018 reponame:Revista da Associação Médica Brasileira (Online) instname:Associação Médica Brasileira (AMB) instacron:AMB |
instname_str |
Associação Médica Brasileira (AMB) |
instacron_str |
AMB |
institution |
AMB |
reponame_str |
Revista da Associação Médica Brasileira (Online) |
collection |
Revista da Associação Médica Brasileira (Online) |
repository.name.fl_str_mv |
Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB) |
repository.mail.fl_str_mv |
||ramb@amb.org.br |
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1754212833074085888 |