Pseudomyxoma peritonei in a pediatric patient: A case report and literature review

Detalhes bibliográficos
Autor(a) principal: Fernandes,Ana Claudia de Oliveira
Data de Publicação: 2018
Outros Autores: Rocha,Gustavo Ricardo Martins da, Oliveira,Alex Dias de, Guimarães,Marcos Duarte, Carvalho,Stefane Cajango de, Chojniak,Rubens
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Revista da Associação Médica Brasileira (Online)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195
Resumo: Summary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely.
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spelling Pseudomyxoma peritonei in a pediatric patient: A case report and literature reviewPseudomyxoma PeritoneiChildTomography, X-ray ComputedMagnetic Resonance SpectroscopySummary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely.Associação Médica Brasileira2018-02-01info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0104-42302018000200195Revista da Associação Médica Brasileira v.64 n.2 2018reponame:Revista da Associação Médica Brasileira (Online)instname:Associação Médica Brasileira (AMB)instacron:AMB10.1590/1806-9282.64.02.195info:eu-repo/semantics/openAccessFernandes,Ana Claudia de OliveiraRocha,Gustavo Ricardo Martins daOliveira,Alex Dias deGuimarães,Marcos DuarteCarvalho,Stefane Cajango deChojniak,Rubenseng2018-04-02T00:00:00Zoai:scielo:S0104-42302018000200195Revistahttps://ramb.amb.org.br/ultimas-edicoes/#https://old.scielo.br/oai/scielo-oai.php||ramb@amb.org.br1806-92820104-4230opendoar:2018-04-02T00:00Revista da Associação Médica Brasileira (Online) - Associação Médica Brasileira (AMB)false
dc.title.none.fl_str_mv Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
title Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
spellingShingle Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
Fernandes,Ana Claudia de Oliveira
Pseudomyxoma Peritonei
Child
Tomography, X-ray Computed
Magnetic Resonance Spectroscopy
title_short Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
title_full Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
title_fullStr Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
title_full_unstemmed Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
title_sort Pseudomyxoma peritonei in a pediatric patient: A case report and literature review
author Fernandes,Ana Claudia de Oliveira
author_facet Fernandes,Ana Claudia de Oliveira
Rocha,Gustavo Ricardo Martins da
Oliveira,Alex Dias de
Guimarães,Marcos Duarte
Carvalho,Stefane Cajango de
Chojniak,Rubens
author_role author
author2 Rocha,Gustavo Ricardo Martins da
Oliveira,Alex Dias de
Guimarães,Marcos Duarte
Carvalho,Stefane Cajango de
Chojniak,Rubens
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Fernandes,Ana Claudia de Oliveira
Rocha,Gustavo Ricardo Martins da
Oliveira,Alex Dias de
Guimarães,Marcos Duarte
Carvalho,Stefane Cajango de
Chojniak,Rubens
dc.subject.por.fl_str_mv Pseudomyxoma Peritonei
Child
Tomography, X-ray Computed
Magnetic Resonance Spectroscopy
topic Pseudomyxoma Peritonei
Child
Tomography, X-ray Computed
Magnetic Resonance Spectroscopy
description Summary Introduction: Pseudomyxoma peritonei (PMP) is a rare clinical condition, with an incidence of 1-2 cases per million, characterized by the dissemination of mucinous implants on the peritoneal surface and progressive gelatinous ascites. Although it usually presents an indolent behavior, its non-specific clinical presentation contributes to many cases remaining undiagnosed until a laparotomy is performed. With late diagnosis, performed after a long period of clinical deterioration and disease progression, it is common to find complications such as the formation of intestinal fistulas and obstruction. Method: Review of the medical record and search for references in the Medline, Lilacs, SciELO and MD Consult databases. Results: There are rare case reports found in the literature demonstrating atypical PMP presentations. Our report is that of a 17-year-old adolescent with a sporadic tumor diagnosed in a primary site in the transverse colon, contrary to data commonly found in the literature that mention a more frequent occurrence in women in the fifth decade of life and with a primary site in the ovary and appendix. The development of mucinous adenocarcinoma is rare in the pediatric population, and topography in the transverse colon and non-familial sporadic pattern are unusual. Conclusion: The case reported not only raises awareness about the atypical presentations of the disease, but also emphasizes the use of imaging examinations for diagnosis, which has an important impact on prognosis and survival if performed timely.
publishDate 2018
dc.date.none.fl_str_mv 2018-02-01
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dc.publisher.none.fl_str_mv Associação Médica Brasileira
publisher.none.fl_str_mv Associação Médica Brasileira
dc.source.none.fl_str_mv Revista da Associação Médica Brasileira v.64 n.2 2018
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