Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease

Detalhes bibliográficos
Autor(a) principal: Brito-Marques,Janaina Mariana de Araujo Miranda
Data de Publicação: 2021
Outros Autores: Melo,Eduardo Sousa de, Medeiros,Fabíola Lys de, Carvalho,Cristiano Sobral de, Brito-Marques,Paulo Roberto de
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Dementia & Neuropsychologia
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642021000400548
Resumo: ABSTRACT. We reported a case of a 61-year-old male patient with anacusis, cerebellar syndrome, myoclonus, and frontal signs. The brain magnetic resonance imaging showed bilateral striated hyperintensity of the fluid-attenuated inversion recovery and restricted diffusion in the diffusion-weighted imaging and hypointense areas corresponding to the apparent diffusion coefficient in the cerebral cortex. The autopsy revealed positive immunohistochemistry for the PrPSc protein. Creutzfeldt–Jakob disease presenting with hearing loss is unusual.
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spelling Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob diseasedementiaprion diseasehypoacusisABSTRACT. We reported a case of a 61-year-old male patient with anacusis, cerebellar syndrome, myoclonus, and frontal signs. The brain magnetic resonance imaging showed bilateral striated hyperintensity of the fluid-attenuated inversion recovery and restricted diffusion in the diffusion-weighted imaging and hypointense areas corresponding to the apparent diffusion coefficient in the cerebral cortex. The autopsy revealed positive immunohistochemistry for the PrPSc protein. Creutzfeldt–Jakob disease presenting with hearing loss is unusual.Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento2021-12-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642021000400548Dementia & Neuropsychologia v.15 n.4 2021reponame:Dementia & Neuropsychologiainstname:Associação de Neurologia Cognitiva e do Comportamento (ANCC)instacron:ANCC10.1590/1980-57642021dn15-040016info:eu-repo/semantics/openAccessBrito-Marques,Janaina Mariana de Araujo MirandaMelo,Eduardo Sousa deMedeiros,Fabíola Lys deCarvalho,Cristiano Sobral deBrito-Marques,Paulo Roberto deeng2021-12-01T00:00:00Zoai:scielo:S1980-57642021000400548Revistahttp://www.demneuropsy.com.br/ONGhttps://old.scielo.br/oai/scielo-oai.php||demneuropsy@uol.com.br1980-57641980-5764opendoar:2021-12-01T00:00Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC)false
dc.title.none.fl_str_mv Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
title Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
spellingShingle Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
Brito-Marques,Janaina Mariana de Araujo Miranda
dementia
prion disease
hypoacusis
title_short Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
title_full Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
title_fullStr Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
title_full_unstemmed Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
title_sort Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease
author Brito-Marques,Janaina Mariana de Araujo Miranda
author_facet Brito-Marques,Janaina Mariana de Araujo Miranda
Melo,Eduardo Sousa de
Medeiros,Fabíola Lys de
Carvalho,Cristiano Sobral de
Brito-Marques,Paulo Roberto de
author_role author
author2 Melo,Eduardo Sousa de
Medeiros,Fabíola Lys de
Carvalho,Cristiano Sobral de
Brito-Marques,Paulo Roberto de
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Brito-Marques,Janaina Mariana de Araujo Miranda
Melo,Eduardo Sousa de
Medeiros,Fabíola Lys de
Carvalho,Cristiano Sobral de
Brito-Marques,Paulo Roberto de
dc.subject.por.fl_str_mv dementia
prion disease
hypoacusis
topic dementia
prion disease
hypoacusis
description ABSTRACT. We reported a case of a 61-year-old male patient with anacusis, cerebellar syndrome, myoclonus, and frontal signs. The brain magnetic resonance imaging showed bilateral striated hyperintensity of the fluid-attenuated inversion recovery and restricted diffusion in the diffusion-weighted imaging and hypointense areas corresponding to the apparent diffusion coefficient in the cerebral cortex. The autopsy revealed positive immunohistochemistry for the PrPSc protein. Creutzfeldt–Jakob disease presenting with hearing loss is unusual.
publishDate 2021
dc.date.none.fl_str_mv 2021-12-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642021000400548
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642021000400548
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.1590/1980-57642021dn15-040016
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
publisher.none.fl_str_mv Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
dc.source.none.fl_str_mv Dementia & Neuropsychologia v.15 n.4 2021
reponame:Dementia & Neuropsychologia
instname:Associação de Neurologia Cognitiva e do Comportamento (ANCC)
instacron:ANCC
instname_str Associação de Neurologia Cognitiva e do Comportamento (ANCC)
instacron_str ANCC
institution ANCC
reponame_str Dementia & Neuropsychologia
collection Dementia & Neuropsychologia
repository.name.fl_str_mv Dementia & Neuropsychologia - Associação de Neurologia Cognitiva e do Comportamento (ANCC)
repository.mail.fl_str_mv ||demneuropsy@uol.com.br
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