Central retinal vein prethrombosis as an initial manifestation of protein S deficiency

Detalhes bibliográficos
Autor(a) principal: Pierre-Filho, Paulo de Tarso Ponte
Data de Publicação: 2004
Outros Autores: Pierre, Alessandra Maria Mont’Alverne, Nascimento, Maurício Abujamra, Marcondes, Ana Maria
Tipo de documento: Artigo
Idioma: eng
Título da fonte: São Paulo medical journal (Online)
Texto Completo: https://periodicosapm.emnuvens.com.br/spmj/article/view/2504
Resumo: CONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients.
id APM-1_08638c686905a77fad45f65a4d9cb3b8
oai_identifier_str oai:ojs.diagnosticoetratamento.emnuvens.com.br:article/2504
network_acronym_str APM-1
network_name_str São Paulo medical journal (Online)
repository_id_str
spelling Central retinal vein prethrombosis as an initial manifestation of protein S deficiencyPré-trombose da veia central da retina como manifestação inicial da deficiência de proteína SVeia retinianaDeficiência de proteína SDoenças vascularesRelatos de casosRetinal veinProtein S deficiencyVascular diseasesCase reportsCONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients.CONTEXTO: Trombose venosa retiniana é mais comum em pessoas idosas e freqüentemente está associada com doença vascular sistêmica. Uma causa sistêmica rara é a deficiência de proteína S. RELATO DE CASO: Um caso de paciente branca, de 21 anos, com pré-trombose de veia central da retina associada à deficiência isolada de proteína S é descrito. Ela apresentou súbito embaçamento visual e escotoma central em olho esquerdo. Terapia cumarínica foi iniciada e completa remissão dos achados oftalmoscópicos foi observada. Este caso mostra que deficiência de proteína S deve ser um fator que deve ser considerado em casos de oclusão venosa retiniana, particularmente em pacientes jovens.São Paulo Medical JournalSão Paulo Medical Journal2004-05-05info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://periodicosapm.emnuvens.com.br/spmj/article/view/2504São Paulo Medical Journal; Vol. 122 No. 3 (2004); 134-135São Paulo Medical Journal; v. 122 n. 3 (2004); 134-1351806-9460reponame:São Paulo medical journal (Online)instname:Associação Paulista de Medicinainstacron:APMenghttps://periodicosapm.emnuvens.com.br/spmj/article/view/2504/2390https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessPierre-Filho, Paulo de Tarso PontePierre, Alessandra Maria Mont’AlverneNascimento, Maurício AbujamraMarcondes, Ana Maria2023-10-05T18:22:39Zoai:ojs.diagnosticoetratamento.emnuvens.com.br:article/2504Revistahttp://www.scielo.br/spmjPUBhttps://old.scielo.br/oai/scielo-oai.phprevistas@apm.org.br1806-94601516-3180opendoar:2023-10-05T18:22:39São Paulo medical journal (Online) - Associação Paulista de Medicinafalse
dc.title.none.fl_str_mv Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
Pré-trombose da veia central da retina como manifestação inicial da deficiência de proteína S
title Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
spellingShingle Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
Pierre-Filho, Paulo de Tarso Ponte
Veia retiniana
Deficiência de proteína S
Doenças vasculares
Relatos de casos
Retinal vein
Protein S deficiency
Vascular diseases
Case reports
title_short Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
title_full Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
title_fullStr Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
title_full_unstemmed Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
title_sort Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
author Pierre-Filho, Paulo de Tarso Ponte
author_facet Pierre-Filho, Paulo de Tarso Ponte
Pierre, Alessandra Maria Mont’Alverne
Nascimento, Maurício Abujamra
Marcondes, Ana Maria
author_role author
author2 Pierre, Alessandra Maria Mont’Alverne
Nascimento, Maurício Abujamra
Marcondes, Ana Maria
author2_role author
author
author
dc.contributor.author.fl_str_mv Pierre-Filho, Paulo de Tarso Ponte
Pierre, Alessandra Maria Mont’Alverne
Nascimento, Maurício Abujamra
Marcondes, Ana Maria
dc.subject.por.fl_str_mv Veia retiniana
Deficiência de proteína S
Doenças vasculares
Relatos de casos
Retinal vein
Protein S deficiency
Vascular diseases
Case reports
topic Veia retiniana
Deficiência de proteína S
Doenças vasculares
Relatos de casos
Retinal vein
Protein S deficiency
Vascular diseases
Case reports
description CONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients.
publishDate 2004
dc.date.none.fl_str_mv 2004-05-05
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://periodicosapm.emnuvens.com.br/spmj/article/view/2504
url https://periodicosapm.emnuvens.com.br/spmj/article/view/2504
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://periodicosapm.emnuvens.com.br/spmj/article/view/2504/2390
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv São Paulo Medical Journal
São Paulo Medical Journal
publisher.none.fl_str_mv São Paulo Medical Journal
São Paulo Medical Journal
dc.source.none.fl_str_mv São Paulo Medical Journal; Vol. 122 No. 3 (2004); 134-135
São Paulo Medical Journal; v. 122 n. 3 (2004); 134-135
1806-9460
reponame:São Paulo medical journal (Online)
instname:Associação Paulista de Medicina
instacron:APM
instname_str Associação Paulista de Medicina
instacron_str APM
institution APM
reponame_str São Paulo medical journal (Online)
collection São Paulo medical journal (Online)
repository.name.fl_str_mv São Paulo medical journal (Online) - Associação Paulista de Medicina
repository.mail.fl_str_mv revistas@apm.org.br
_version_ 1825135076128587776