Central retinal vein prethrombosis as an initial manifestation of protein S deficiency
Autor(a) principal: | |
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Data de Publicação: | 2004 |
Outros Autores: | , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | São Paulo medical journal (Online) |
Texto Completo: | https://periodicosapm.emnuvens.com.br/spmj/article/view/2504 |
Resumo: | CONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients. |
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Central retinal vein prethrombosis as an initial manifestation of protein S deficiencyPré-trombose da veia central da retina como manifestação inicial da deficiência de proteína SVeia retinianaDeficiência de proteína SDoenças vascularesRelatos de casosRetinal veinProtein S deficiencyVascular diseasesCase reportsCONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients.CONTEXTO: Trombose venosa retiniana é mais comum em pessoas idosas e freqüentemente está associada com doença vascular sistêmica. Uma causa sistêmica rara é a deficiência de proteína S. RELATO DE CASO: Um caso de paciente branca, de 21 anos, com pré-trombose de veia central da retina associada à deficiência isolada de proteína S é descrito. Ela apresentou súbito embaçamento visual e escotoma central em olho esquerdo. Terapia cumarínica foi iniciada e completa remissão dos achados oftalmoscópicos foi observada. Este caso mostra que deficiência de proteína S deve ser um fator que deve ser considerado em casos de oclusão venosa retiniana, particularmente em pacientes jovens.São Paulo Medical JournalSão Paulo Medical Journal2004-05-05info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://periodicosapm.emnuvens.com.br/spmj/article/view/2504São Paulo Medical Journal; Vol. 122 No. 3 (2004); 134-135São Paulo Medical Journal; v. 122 n. 3 (2004); 134-1351806-9460reponame:São Paulo medical journal (Online)instname:Associação Paulista de Medicinainstacron:APMenghttps://periodicosapm.emnuvens.com.br/spmj/article/view/2504/2390https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessPierre-Filho, Paulo de Tarso PontePierre, Alessandra Maria Mont’AlverneNascimento, Maurício AbujamraMarcondes, Ana Maria2023-10-05T18:22:39Zoai:ojs.diagnosticoetratamento.emnuvens.com.br:article/2504Revistahttp://www.scielo.br/spmjPUBhttps://old.scielo.br/oai/scielo-oai.phprevistas@apm.org.br1806-94601516-3180opendoar:2023-10-05T18:22:39São Paulo medical journal (Online) - Associação Paulista de Medicinafalse |
dc.title.none.fl_str_mv |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency Pré-trombose da veia central da retina como manifestação inicial da deficiência de proteína S |
title |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
spellingShingle |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency Pierre-Filho, Paulo de Tarso Ponte Veia retiniana Deficiência de proteína S Doenças vasculares Relatos de casos Retinal vein Protein S deficiency Vascular diseases Case reports |
title_short |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
title_full |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
title_fullStr |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
title_full_unstemmed |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
title_sort |
Central retinal vein prethrombosis as an initial manifestation of protein S deficiency |
author |
Pierre-Filho, Paulo de Tarso Ponte |
author_facet |
Pierre-Filho, Paulo de Tarso Ponte Pierre, Alessandra Maria Mont’Alverne Nascimento, Maurício Abujamra Marcondes, Ana Maria |
author_role |
author |
author2 |
Pierre, Alessandra Maria Mont’Alverne Nascimento, Maurício Abujamra Marcondes, Ana Maria |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Pierre-Filho, Paulo de Tarso Ponte Pierre, Alessandra Maria Mont’Alverne Nascimento, Maurício Abujamra Marcondes, Ana Maria |
dc.subject.por.fl_str_mv |
Veia retiniana Deficiência de proteína S Doenças vasculares Relatos de casos Retinal vein Protein S deficiency Vascular diseases Case reports |
topic |
Veia retiniana Deficiência de proteína S Doenças vasculares Relatos de casos Retinal vein Protein S deficiency Vascular diseases Case reports |
description |
CONTEXT: Retinal vein thrombosis is most common in old people, and is often associated with systemic vascular disease. One of its rare systemic causes is protein S deficiency. CASE REPORT: A case of a 21-year-old woman with retinal vein prethrombosis associated only with protein S deficiency is described. She presented with acutely reduced visual acuity and a central scotoma in her left eye. Warfarin therapy was initiated, and complete improvement in ophthalmoscopic findings was subsequently observed. This case illustrates that protein S deficiency is a factor that should be considered in cases of retinal vein occlusion, particularly in young patients. |
publishDate |
2004 |
dc.date.none.fl_str_mv |
2004-05-05 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://periodicosapm.emnuvens.com.br/spmj/article/view/2504 |
url |
https://periodicosapm.emnuvens.com.br/spmj/article/view/2504 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://periodicosapm.emnuvens.com.br/spmj/article/view/2504/2390 |
dc.rights.driver.fl_str_mv |
https://creativecommons.org/licenses/by/4.0 info:eu-repo/semantics/openAccess |
rights_invalid_str_mv |
https://creativecommons.org/licenses/by/4.0 |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
São Paulo Medical Journal São Paulo Medical Journal |
publisher.none.fl_str_mv |
São Paulo Medical Journal São Paulo Medical Journal |
dc.source.none.fl_str_mv |
São Paulo Medical Journal; Vol. 122 No. 3 (2004); 134-135 São Paulo Medical Journal; v. 122 n. 3 (2004); 134-135 1806-9460 reponame:São Paulo medical journal (Online) instname:Associação Paulista de Medicina instacron:APM |
instname_str |
Associação Paulista de Medicina |
instacron_str |
APM |
institution |
APM |
reponame_str |
São Paulo medical journal (Online) |
collection |
São Paulo medical journal (Online) |
repository.name.fl_str_mv |
São Paulo medical journal (Online) - Associação Paulista de Medicina |
repository.mail.fl_str_mv |
revistas@apm.org.br |
_version_ |
1825135076128587776 |