Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report
Autor(a) principal: | |
---|---|
Data de Publicação: | 2013 |
Outros Autores: | , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Arquivos brasileiros de oftalmologia (Online) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492013000300013 |
Resumo: | We report the case of a 24-year-old man presenting with sudden visual loss in the left eye from a central retinal artery occlusion. An extensive clinical investigation revealed no etiology. Three weeks later, however, the patient developed hearing loss followed by encephalopathy and multiple branch retinal artery occlusions in the right eye. Fluorescein angiography confirmed retinal vascular occlusions with no sign of vasculitis. The neurological examination revealed a diffuse encephalopathy while the MRI scan disclosed several small areas of infarcts in the brain. Bilateral sensorineural hearing loss was confirmed on audiometry. The patient was diagnosed with Susac syndrome and treated with methylprednisolone and cyclophosphamide, resulting in slight improvement and stabilization. This case shows that Susac syndrome may be diagnosed late due to the absence at onset of one or more of the symptoms of the classic triad (encephalopathy, multiple branch retinal artery occlusions and hearing loss). This case also serves to emphasize that Susac syndrome should be considered in the differential diagnosis of central retinal artery occlusion, even in apparently healthy young men. |
id |
CBO-2_2a4ef0661a386498a4dd3cde2c405674 |
---|---|
oai_identifier_str |
oai:scielo:S0004-27492013000300013 |
network_acronym_str |
CBO-2 |
network_name_str |
Arquivos brasileiros de oftalmologia (Online) |
repository_id_str |
|
spelling |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case reportRetinal artery occlusionSusac syndrome/diagnosisSusac syndrome/drug therapyMethylprednisolone/therapeutic useCyclophosphamide/therapeutic useHearing lossEncephalopathyCase reportWe report the case of a 24-year-old man presenting with sudden visual loss in the left eye from a central retinal artery occlusion. An extensive clinical investigation revealed no etiology. Three weeks later, however, the patient developed hearing loss followed by encephalopathy and multiple branch retinal artery occlusions in the right eye. Fluorescein angiography confirmed retinal vascular occlusions with no sign of vasculitis. The neurological examination revealed a diffuse encephalopathy while the MRI scan disclosed several small areas of infarcts in the brain. Bilateral sensorineural hearing loss was confirmed on audiometry. The patient was diagnosed with Susac syndrome and treated with methylprednisolone and cyclophosphamide, resulting in slight improvement and stabilization. This case shows that Susac syndrome may be diagnosed late due to the absence at onset of one or more of the symptoms of the classic triad (encephalopathy, multiple branch retinal artery occlusions and hearing loss). This case also serves to emphasize that Susac syndrome should be considered in the differential diagnosis of central retinal artery occlusion, even in apparently healthy young men.Conselho Brasileiro de Oftalmologia2013-06-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492013000300013Arquivos Brasileiros de Oftalmologia v.76 n.3 2013reponame:Arquivos brasileiros de oftalmologia (Online)instname:Conselho Brasileiro de Oftalmologia (CBO)instacron:CBO10.1590/S0004-27492013000300013info:eu-repo/semantics/openAccessApóstolos-Pereira,Samira Luiza dosKara-José,Lúcia B. PassosMarchiori,Paulo EuripedesMonteiro,Mário Luiz Ribeiroeng2013-08-06T00:00:00Zoai:scielo:S0004-27492013000300013Revistahttp://aboonline.org.br/https://old.scielo.br/oai/scielo-oai.phpaboonline@cbo.com.br||abo@cbo.com.br1678-29250004-2749opendoar:2013-08-06T00:00Arquivos brasileiros de oftalmologia (Online) - Conselho Brasileiro de Oftalmologia (CBO)false |
dc.title.none.fl_str_mv |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
title |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
spellingShingle |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report Apóstolos-Pereira,Samira Luiza dos Retinal artery occlusion Susac syndrome/diagnosis Susac syndrome/drug therapy Methylprednisolone/therapeutic use Cyclophosphamide/therapeutic use Hearing loss Encephalopathy Case report |
title_short |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
title_full |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
title_fullStr |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
title_full_unstemmed |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
title_sort |
Unilateral central retinal artery occlusion as the sole presenting sign of Susac syndrome in a young man: case report |
author |
Apóstolos-Pereira,Samira Luiza dos |
author_facet |
Apóstolos-Pereira,Samira Luiza dos Kara-José,Lúcia B. Passos Marchiori,Paulo Euripedes Monteiro,Mário Luiz Ribeiro |
author_role |
author |
author2 |
Kara-José,Lúcia B. Passos Marchiori,Paulo Euripedes Monteiro,Mário Luiz Ribeiro |
author2_role |
author author author |
dc.contributor.author.fl_str_mv |
Apóstolos-Pereira,Samira Luiza dos Kara-José,Lúcia B. Passos Marchiori,Paulo Euripedes Monteiro,Mário Luiz Ribeiro |
dc.subject.por.fl_str_mv |
Retinal artery occlusion Susac syndrome/diagnosis Susac syndrome/drug therapy Methylprednisolone/therapeutic use Cyclophosphamide/therapeutic use Hearing loss Encephalopathy Case report |
topic |
Retinal artery occlusion Susac syndrome/diagnosis Susac syndrome/drug therapy Methylprednisolone/therapeutic use Cyclophosphamide/therapeutic use Hearing loss Encephalopathy Case report |
description |
We report the case of a 24-year-old man presenting with sudden visual loss in the left eye from a central retinal artery occlusion. An extensive clinical investigation revealed no etiology. Three weeks later, however, the patient developed hearing loss followed by encephalopathy and multiple branch retinal artery occlusions in the right eye. Fluorescein angiography confirmed retinal vascular occlusions with no sign of vasculitis. The neurological examination revealed a diffuse encephalopathy while the MRI scan disclosed several small areas of infarcts in the brain. Bilateral sensorineural hearing loss was confirmed on audiometry. The patient was diagnosed with Susac syndrome and treated with methylprednisolone and cyclophosphamide, resulting in slight improvement and stabilization. This case shows that Susac syndrome may be diagnosed late due to the absence at onset of one or more of the symptoms of the classic triad (encephalopathy, multiple branch retinal artery occlusions and hearing loss). This case also serves to emphasize that Susac syndrome should be considered in the differential diagnosis of central retinal artery occlusion, even in apparently healthy young men. |
publishDate |
2013 |
dc.date.none.fl_str_mv |
2013-06-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492013000300013 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0004-27492013000300013 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1590/S0004-27492013000300013 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Conselho Brasileiro de Oftalmologia |
publisher.none.fl_str_mv |
Conselho Brasileiro de Oftalmologia |
dc.source.none.fl_str_mv |
Arquivos Brasileiros de Oftalmologia v.76 n.3 2013 reponame:Arquivos brasileiros de oftalmologia (Online) instname:Conselho Brasileiro de Oftalmologia (CBO) instacron:CBO |
instname_str |
Conselho Brasileiro de Oftalmologia (CBO) |
instacron_str |
CBO |
institution |
CBO |
reponame_str |
Arquivos brasileiros de oftalmologia (Online) |
collection |
Arquivos brasileiros de oftalmologia (Online) |
repository.name.fl_str_mv |
Arquivos brasileiros de oftalmologia (Online) - Conselho Brasileiro de Oftalmologia (CBO) |
repository.mail.fl_str_mv |
aboonline@cbo.com.br||abo@cbo.com.br |
_version_ |
1754209027721527296 |