Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach

Detalhes bibliográficos
Autor(a) principal: Menegueti, Mayra Gonçalves
Data de Publicação: 2011
Outros Autores: Teixeira, Gil Cezar Alkmim, Casarini, Karin Aparecida, Cordeiro, Kátia Simone Muniz, Basile Filho, Aníbal, Martins Filho, Olindo Assis, Martins, Maria Auxiliadora
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da FIOCRUZ (ARCA)
Texto Completo: https://www.arca.fiocruz.br/handle/icict/8960
Resumo: Universidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, Brazil
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spelling Menegueti, Mayra GonçalvesTeixeira, Gil Cezar AlkmimCasarini, Karin AparecidaCordeiro, Kátia Simone MunizBasile Filho, AníbalMartins Filho, Olindo AssisMartins, Maria Auxiliadora2014-11-25T16:58:15Z2014-11-25T16:58:15Z2011MENEGUETI, Mayra Gonçalves et al. Acute Intermittent Porphyria associated with respiratory failure: a multidisciplinary approach. Critical Care Research and Practice, ID 283690, 2011.1062-3264https://www.arca.fiocruz.br/handle/icict/896010.1155/2011/283690engOxford University PressAcute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approachinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilFundação Oswaldo Cruz. Centro de Pesquisa René Rachou. Laboratório de Biomarcadores de Diagnóstico e Monitoração. Belo Horizonte, MG, BrazilUniversidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, BrazilDespite being challenging, delivery of effective nursing care to patients with acute intermittent porphyria is a matter of utmost importance. In this paper, the diversity of symptoms and the difficult diagnosis of this condition are emphasized, and details concerning the treatment of this disorder in the intensive care unit are presented. We believe that acute intermittent porphyria should be borne in mind during performance of differential diagnosis of neurological, psychiatric, and gastroenterological disorders on patients whose routine investigation tests are normal, especially when precipitating factors exist. Intensive care measures and a multidisciplinary team approach are essential.porphyriainfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da FIOCRUZ (ARCA)instname:Fundação Oswaldo Cruz (FIOCRUZ)instacron:FIOCRUZLICENSElicense.txtlicense.txttext/plain; charset=utf-81914https://www.arca.fiocruz.br/bitstream/icict/8960/1/license.txt7d48279ffeed55da8dfe2f8e81f3b81fMD51ORIGINALAcute Intermittent Porphyria Associated with Respiratory Failure.pdfAcute Intermittent Porphyria Associated with Respiratory Failure.pdfapplication/pdf1198097https://www.arca.fiocruz.br/bitstream/icict/8960/2/Acute%20Intermittent%20Porphyria%20Associated%20with%20Respiratory%20Failure.pdf6014ad6e38f8699d9b5ac1f4f74e13bfMD52TEXTAcute Intermittent Porphyria Associated with Respiratory Failure.pdf.txtAcute Intermittent Porphyria Associated with Respiratory Failure.pdf.txtExtracted texttext/plain22701https://www.arca.fiocruz.br/bitstream/icict/8960/3/Acute%20Intermittent%20Porphyria%20Associated%20with%20Respiratory%20Failure.pdf.txt311f0f3d47e367407b120d267be57e8cMD53icict/89602019-06-19 10:07:58.197oai:www.arca.fiocruz.br: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ório InstitucionalPUBhttps://www.arca.fiocruz.br/oai/requestrepositorio.arca@fiocruz.bropendoar:21352019-06-19T13:07:58Repositório Institucional da FIOCRUZ (ARCA) - Fundação Oswaldo Cruz (FIOCRUZ)false
dc.title.pt_BR.fl_str_mv Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
spellingShingle Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
Menegueti, Mayra Gonçalves
porphyria
title_short Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_full Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_fullStr Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_full_unstemmed Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
title_sort Acute Intermittent Porphyria Associated with Respiratory Failure: A Multidisciplinary Approach
author Menegueti, Mayra Gonçalves
author_facet Menegueti, Mayra Gonçalves
Teixeira, Gil Cezar Alkmim
Casarini, Karin Aparecida
Cordeiro, Kátia Simone Muniz
Basile Filho, Aníbal
Martins Filho, Olindo Assis
Martins, Maria Auxiliadora
author_role author
author2 Teixeira, Gil Cezar Alkmim
Casarini, Karin Aparecida
Cordeiro, Kátia Simone Muniz
Basile Filho, Aníbal
Martins Filho, Olindo Assis
Martins, Maria Auxiliadora
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv Menegueti, Mayra Gonçalves
Teixeira, Gil Cezar Alkmim
Casarini, Karin Aparecida
Cordeiro, Kátia Simone Muniz
Basile Filho, Aníbal
Martins Filho, Olindo Assis
Martins, Maria Auxiliadora
dc.subject.en.pt_BR.fl_str_mv porphyria
topic porphyria
description Universidade de São Paulo. Faculdade de Medicina de Ribeirão Preto. Hospital das Clínicas. Departamento de Cirurgia e Anatomia. Divisão de Terapia Intensiva. Ribeirão Preto, SP, Brazil
publishDate 2011
dc.date.issued.fl_str_mv 2011
dc.date.accessioned.fl_str_mv 2014-11-25T16:58:15Z
dc.date.available.fl_str_mv 2014-11-25T16:58:15Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
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dc.identifier.citation.fl_str_mv MENEGUETI, Mayra Gonçalves et al. Acute Intermittent Porphyria associated with respiratory failure: a multidisciplinary approach. Critical Care Research and Practice, ID 283690, 2011.
dc.identifier.uri.fl_str_mv https://www.arca.fiocruz.br/handle/icict/8960
dc.identifier.issn.none.fl_str_mv 1062-3264
dc.identifier.doi.none.fl_str_mv 10.1155/2011/283690
identifier_str_mv MENEGUETI, Mayra Gonçalves et al. Acute Intermittent Porphyria associated with respiratory failure: a multidisciplinary approach. Critical Care Research and Practice, ID 283690, 2011.
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url https://www.arca.fiocruz.br/handle/icict/8960
dc.language.iso.fl_str_mv eng
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dc.publisher.none.fl_str_mv Oxford University Press
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