POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report

Detalhes bibliográficos
Autor(a) principal: Leite, Ana Claudia Celestino
Data de Publicação: 2007
Outros Autores: Nascimento, Osvaldo J. M., Lima, Marco Antonio, Andrada-Serpa, Maria José
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Institucional da FIOCRUZ (ARCA)
Texto Completo: https://www.arca.fiocruz.br/handle/icict/57128
Resumo: A síndrome POEMS, também conhecida como síndrome de Crow-Fukase é uma desordem sistêmica rara descrita principalmente em asiáticos. Ela é caracterizada pela presença de (P) polineuropatia, (O) organomegalia, (E) endocrinopatia, (M) proteína M e (S) alterações de pele. Diversas outras manifestações, tais como lesões osteoescleróticas, doença de Castleman, febre baixa, edema e distúrbios hematológicos são freqüentemente observados. Apresentamos cinco pacientes brasileiros com esta síndrome. Dois pacientes apresentaram diagnóstico de doença de Castleman, um paciente com mieloma osteoesclerótico e em dois pacientes, nenhuma condição associada foi encontrada.
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spelling Leite, Ana Claudia CelestinoNascimento, Osvaldo J. M.Lima, Marco AntonioAndrada-Serpa, Maria José2023-02-26T02:10:21Z2023-02-26T02:10:21Z2007LEITE, Ana Claudia Celestino et al. POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report. Arquivos de Neuro-Psiquiatria, São Paulo, v. 65, n. 2b, p. 516-520, June 2007.0004-282Xhttps://www.arca.fiocruz.br/handle/icict/5712810.1590/S0004-282X20070003000301678-4227A síndrome POEMS, também conhecida como síndrome de Crow-Fukase é uma desordem sistêmica rara descrita principalmente em asiáticos. Ela é caracterizada pela presença de (P) polineuropatia, (O) organomegalia, (E) endocrinopatia, (M) proteína M e (S) alterações de pele. Diversas outras manifestações, tais como lesões osteoescleróticas, doença de Castleman, febre baixa, edema e distúrbios hematológicos são freqüentemente observados. Apresentamos cinco pacientes brasileiros com esta síndrome. Dois pacientes apresentaram diagnóstico de doença de Castleman, um paciente com mieloma osteoesclerótico e em dois pacientes, nenhuma condição associada foi encontrada.The POEMS syndrome, also known as Crow-Fukase syndrome, is an unusual systemic disorder described mainly in Asian individuals. It is characterized by the presence of (P)polyneuropathy, (O)organomegaly, (E)endocrinopathy, (M) M-protein, and (S) skin changes. Several other associated condictions such as sclerotic bone lesions, Castleman disease, low-grade fever, edema and hematologic disorders are usually seen. We describe five Brazilian patients with this syndrome. Two patients presented Castleman disease, one patient presented osteosclerotic myeloma and in two patients no associated conditions were found.Universidade Federal Fluminense. Program on Neurology. Niterói, RJ, Brasil / Instituto de Hematologia do Estado do Rio de Janeiro. Rio de Janeiro, RJ, Brasil.Universidade Federal Fluminense. Program on Neurology. Niterói, RJ, Brasil.National Institute of Cancer. Rio de Janeiro, RJ, Brasil.Oswaldo Cruz Foundation. Evandro Chagas Research Institute. Rio de Janeiro, RJ, Brazil.engAcademia Brasileira de Neurologia - ABNEURONeuropatia periféricaPOEMSProteína monoclonalPeripheral neuropathyPOEMSMonoclonal proteinPOEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's reportPOEMS (polineuropatia, organomegalia, endocrinopatia, proteína M, alterações de pele): relato sul-americanoPOEMS (polineuropatia, organomegalia, endocrinopatia, proteína M, alterações de pele): relato sul-americanoinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleinfo:eu-repo/semantics/openAccessreponame:Repositório Institucional da FIOCRUZ (ARCA)instname:Fundação Oswaldo Cruz (FIOCRUZ)instacron:FIOCRUZLICENSElicense.txtlicense.txttext/plain; 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dc.title.en_US.fl_str_mv POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
dc.title.alternative.en_US.fl_str_mv POEMS (polineuropatia, organomegalia, endocrinopatia, proteína M, alterações de pele): relato sul-americano
POEMS (polineuropatia, organomegalia, endocrinopatia, proteína M, alterações de pele): relato sul-americano
title POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
spellingShingle POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
Leite, Ana Claudia Celestino
Neuropatia periférica
POEMS
Proteína monoclonal
Peripheral neuropathy
POEMS
Monoclonal protein
title_short POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
title_full POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
title_fullStr POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
title_full_unstemmed POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
title_sort POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report
author Leite, Ana Claudia Celestino
author_facet Leite, Ana Claudia Celestino
Nascimento, Osvaldo J. M.
Lima, Marco Antonio
Andrada-Serpa, Maria José
author_role author
author2 Nascimento, Osvaldo J. M.
Lima, Marco Antonio
Andrada-Serpa, Maria José
author2_role author
author
author
dc.contributor.author.fl_str_mv Leite, Ana Claudia Celestino
Nascimento, Osvaldo J. M.
Lima, Marco Antonio
Andrada-Serpa, Maria José
dc.subject.other.en_US.fl_str_mv Neuropatia periférica
POEMS
Proteína monoclonal
topic Neuropatia periférica
POEMS
Proteína monoclonal
Peripheral neuropathy
POEMS
Monoclonal protein
dc.subject.en.en_US.fl_str_mv Peripheral neuropathy
POEMS
Monoclonal protein
description A síndrome POEMS, também conhecida como síndrome de Crow-Fukase é uma desordem sistêmica rara descrita principalmente em asiáticos. Ela é caracterizada pela presença de (P) polineuropatia, (O) organomegalia, (E) endocrinopatia, (M) proteína M e (S) alterações de pele. Diversas outras manifestações, tais como lesões osteoescleróticas, doença de Castleman, febre baixa, edema e distúrbios hematológicos são freqüentemente observados. Apresentamos cinco pacientes brasileiros com esta síndrome. Dois pacientes apresentaram diagnóstico de doença de Castleman, um paciente com mieloma osteoesclerótico e em dois pacientes, nenhuma condição associada foi encontrada.
publishDate 2007
dc.date.issued.fl_str_mv 2007
dc.date.accessioned.fl_str_mv 2023-02-26T02:10:21Z
dc.date.available.fl_str_mv 2023-02-26T02:10:21Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.citation.fl_str_mv LEITE, Ana Claudia Celestino et al. POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report. Arquivos de Neuro-Psiquiatria, São Paulo, v. 65, n. 2b, p. 516-520, June 2007.
dc.identifier.uri.fl_str_mv https://www.arca.fiocruz.br/handle/icict/57128
dc.identifier.issn.en_US.fl_str_mv 0004-282X
dc.identifier.doi.none.fl_str_mv 10.1590/S0004-282X2007000300030
dc.identifier.eissn.none.fl_str_mv 1678-4227
identifier_str_mv LEITE, Ana Claudia Celestino et al. POEMS (polyneuropathy, organomegaly, endocrinopathy, M protein, skin lesions) syndrome: a South America's report. Arquivos de Neuro-Psiquiatria, São Paulo, v. 65, n. 2b, p. 516-520, June 2007.
0004-282X
10.1590/S0004-282X2007000300030
1678-4227
url https://www.arca.fiocruz.br/handle/icict/57128
dc.language.iso.fl_str_mv eng
language eng
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
publisher.none.fl_str_mv Academia Brasileira de Neurologia - ABNEURO
dc.source.none.fl_str_mv reponame:Repositório Institucional da FIOCRUZ (ARCA)
instname:Fundação Oswaldo Cruz (FIOCRUZ)
instacron:FIOCRUZ
instname_str Fundação Oswaldo Cruz (FIOCRUZ)
instacron_str FIOCRUZ
institution FIOCRUZ
reponame_str Repositório Institucional da FIOCRUZ (ARCA)
collection Repositório Institucional da FIOCRUZ (ARCA)
bitstream.url.fl_str_mv https://www.arca.fiocruz.br/bitstream/icict/57128/1/license.txt
https://www.arca.fiocruz.br/bitstream/icict/57128/2/ve_Leite_Ana_etal_INI_2007.pdf
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