Repairing rhinoplasty with costal cartilage graft in case of septal necrosis in a patient with Granilomatosis with Polyangiitis

• Autor(a) principal: MANDARIM DE LACERDA, MARIA ELENA
• Data de Publicação: 2019
• Outros Autores: Guimaraes, Leonardo Araujo, Souza, David de Almeida, Botelho, Lara Gomes, dos Santos, Julyane Alves de Assis, D’Oliveira, Leonardo Ferraz Marques
• Tipo de documento: Artigo
• Idioma: por
• Título da fonte: Revista Científica da Faculdade de Medicina de Campos
• Texto Completo: https://www.fmc.br/ojs/index.php/RCFMC/article/view/244
• topic: Cirurgia Plástica, Granulomatose com Poliangiite, Poliangiite Microscópica, Rinoplastia; Granulomatosis with Polyangiitis, Microscopic Polyangiitis, Rhinoplasty, Plastic,Surgery

ABSTRACT Described in 1937 by Friedrich Wegener, Granulomatosis with Polyangeitis (GPA) – formerly known as Wergener's granulomatosis – is a rare autoimmune condition. It is a vasculitis that affects small to medium vessels and necrotizing granulomatous inflammation. Vessels of great caliber are rarely affected. It attacks head and neck regions regularly. It has predilection for the upper respiratory tract, lungs and kidneys, however it can affect any organ. The ear, nose and throat regions are the most common in primary manifestations of the disease. Objective: To report the surgical approach to repairing nasal deformity in a patient diagnosed with GPA 25 years ago. Descriptions: Female patient, 41 years of age with diagnosis of GPA 25 years ago. She presented a picture of nasal deformity about 19 years ago. It presents collapse of the cartilaginous framework triggered by nasal septal necrosis. No functional complaints were reported. Scheduled open rhinoplasty with L neosepto preparation from costal cartilage graft. Currently, the patient has nasal tip support, complete reversal of the nose frame in the saddle, without functional complaints. Conclusion: GPA is a rare disease that in nasal attacks, septum perforation is a common event. Rarely, with a long time of illness, it can cause more extensive destruction of the nasal cartilage, generating deformities. This article presents a rare case of a patient with a long period of disease, presenting nasal deformity. A repair rhinoplasty with costal cartilage graft was performed. The surgery was performed at the Plastic Surgery Service of University Hospital Pedro Ernesto.