Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome

Detalhes bibliográficos
Autor(a) principal: Oliveira,Alexandra Kolontai de Sousa
Data de Publicação: 2013
Outros Autores: Ferro,Lília Pereira Abreu, Silva,Jaiede Nicacio da, Okada,Daniel Mochida
Tipo de documento: Relatório
Idioma: eng
Título da fonte: International Archives of Otorhinolaryngology
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1809-48642013000200018
Resumo: INTRODUCTION: Treacher-Collins syndrome is characterized by craniofacial malformations, narrowing of the external auditory canal (EAC), and, in 30% of cases, agenesis of the canal and ossicular chain defects. The use of hearing aids (HA) is not possible in cases in which agenesis or stenosis of the EAC accompanies conductive deafness. In contrast, bone conduction implants such as the Bone Anchored Hearing Aid (BAHA®) allow direct stimulation of the cochlea and are thus superior to conventional hearing aids in cases of severe conductive hearing loss. OBJECTIVE: To present 2 cases of patients with Treacher-Collins syndrome who underwent implantation of BAHA®. CASES REPORTS: The first patient was a 52-year-old woman diagnosed with Treacher-Collins syndrome who presented with severe bilateral mixed hearing loss and a history of unsuccessful previous use of a bone contact conduction device. The BAHA® implantation was uneventful, and the post-operative results were good. The second patient was a 14-year-old girl who was also diagnosed with Treacher-Collins Syndrome with bilateral moderate conductive hearing loss by audiometry. The use of a bone vibrator contact device did not improve her hearing; however, implantation of a BAHA® resulted in a decreased gap postoperatively. FINAL COMMENTS: BAHA® hearing devices provide adequate rehabilitation and consequent improvement of the quality of life in patients with Treacher-Collins syndrome.
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spelling Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndromemandibulofacial dysostosishearing loss, conductivebone conductionINTRODUCTION: Treacher-Collins syndrome is characterized by craniofacial malformations, narrowing of the external auditory canal (EAC), and, in 30% of cases, agenesis of the canal and ossicular chain defects. The use of hearing aids (HA) is not possible in cases in which agenesis or stenosis of the EAC accompanies conductive deafness. In contrast, bone conduction implants such as the Bone Anchored Hearing Aid (BAHA®) allow direct stimulation of the cochlea and are thus superior to conventional hearing aids in cases of severe conductive hearing loss. OBJECTIVE: To present 2 cases of patients with Treacher-Collins syndrome who underwent implantation of BAHA®. CASES REPORTS: The first patient was a 52-year-old woman diagnosed with Treacher-Collins syndrome who presented with severe bilateral mixed hearing loss and a history of unsuccessful previous use of a bone contact conduction device. The BAHA® implantation was uneventful, and the post-operative results were good. The second patient was a 14-year-old girl who was also diagnosed with Treacher-Collins Syndrome with bilateral moderate conductive hearing loss by audiometry. The use of a bone vibrator contact device did not improve her hearing; however, implantation of a BAHA® resulted in a decreased gap postoperatively. FINAL COMMENTS: BAHA® hearing devices provide adequate rehabilitation and consequent improvement of the quality of life in patients with Treacher-Collins syndrome.Fundação Otorrinolaringologia2013-06-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1809-48642013000200018International Archives of Otorhinolaryngology v.17 n.2 2013reponame:International Archives of Otorhinolaryngologyinstname:Fundação Otorrinolaringologia (FORL)instacron:FORL10.7162/S1809-97772013000200018info:eu-repo/semantics/openAccessOliveira,Alexandra Kolontai de SousaFerro,Lília Pereira AbreuSilva,Jaiede Nicacio daOkada,Daniel Mochidaeng2013-04-03T00:00:00Zoai:scielo:S1809-48642013000200018Revistahttps://www.scielo.br/j/iao/https://old.scielo.br/oai/scielo-oai.php||iaorl@iaorl.org||archives@internationalarchivesent.org||arquivos@forl.org.br1809-48641809-4864opendoar:2013-04-03T00:00International Archives of Otorhinolaryngology - Fundação Otorrinolaringologia (FORL)false
dc.title.none.fl_str_mv Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
title Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
spellingShingle Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
Oliveira,Alexandra Kolontai de Sousa
mandibulofacial dysostosis
hearing loss, conductive
bone conduction
title_short Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
title_full Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
title_fullStr Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
title_full_unstemmed Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
title_sort Results of the implantation of bone-anchored hearing aids in patients with treacher-collins syndrome
author Oliveira,Alexandra Kolontai de Sousa
author_facet Oliveira,Alexandra Kolontai de Sousa
Ferro,Lília Pereira Abreu
Silva,Jaiede Nicacio da
Okada,Daniel Mochida
author_role author
author2 Ferro,Lília Pereira Abreu
Silva,Jaiede Nicacio da
Okada,Daniel Mochida
author2_role author
author
author
dc.contributor.author.fl_str_mv Oliveira,Alexandra Kolontai de Sousa
Ferro,Lília Pereira Abreu
Silva,Jaiede Nicacio da
Okada,Daniel Mochida
dc.subject.por.fl_str_mv mandibulofacial dysostosis
hearing loss, conductive
bone conduction
topic mandibulofacial dysostosis
hearing loss, conductive
bone conduction
description INTRODUCTION: Treacher-Collins syndrome is characterized by craniofacial malformations, narrowing of the external auditory canal (EAC), and, in 30% of cases, agenesis of the canal and ossicular chain defects. The use of hearing aids (HA) is not possible in cases in which agenesis or stenosis of the EAC accompanies conductive deafness. In contrast, bone conduction implants such as the Bone Anchored Hearing Aid (BAHA®) allow direct stimulation of the cochlea and are thus superior to conventional hearing aids in cases of severe conductive hearing loss. OBJECTIVE: To present 2 cases of patients with Treacher-Collins syndrome who underwent implantation of BAHA®. CASES REPORTS: The first patient was a 52-year-old woman diagnosed with Treacher-Collins syndrome who presented with severe bilateral mixed hearing loss and a history of unsuccessful previous use of a bone contact conduction device. The BAHA® implantation was uneventful, and the post-operative results were good. The second patient was a 14-year-old girl who was also diagnosed with Treacher-Collins Syndrome with bilateral moderate conductive hearing loss by audiometry. The use of a bone vibrator contact device did not improve her hearing; however, implantation of a BAHA® resulted in a decreased gap postoperatively. FINAL COMMENTS: BAHA® hearing devices provide adequate rehabilitation and consequent improvement of the quality of life in patients with Treacher-Collins syndrome.
publishDate 2013
dc.date.none.fl_str_mv 2013-06-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
format report
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1809-48642013000200018
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1809-48642013000200018
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.7162/S1809-97772013000200018
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv text/html
dc.publisher.none.fl_str_mv Fundação Otorrinolaringologia
publisher.none.fl_str_mv Fundação Otorrinolaringologia
dc.source.none.fl_str_mv International Archives of Otorhinolaryngology v.17 n.2 2013
reponame:International Archives of Otorhinolaryngology
instname:Fundação Otorrinolaringologia (FORL)
instacron:FORL
instname_str Fundação Otorrinolaringologia (FORL)
instacron_str FORL
institution FORL
reponame_str International Archives of Otorhinolaryngology
collection International Archives of Otorhinolaryngology
repository.name.fl_str_mv International Archives of Otorhinolaryngology - Fundação Otorrinolaringologia (FORL)
repository.mail.fl_str_mv ||iaorl@iaorl.org||archives@internationalarchivesent.org||arquivos@forl.org.br
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