Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
Autor(a) principal: | |
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Data de Publicação: | 2020 |
Outros Autores: | , , , |
Tipo de documento: | Relatório |
Idioma: | eng |
Título da fonte: | Einstein (São Paulo) |
Texto Completo: | http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503 |
Resumo: | ABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura. |
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Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature reviewSitus inversusPurpura, thrombocytopenicPlatelet countExomeHematologic diseasesABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.Instituto Israelita de Ensino e Pesquisa Albert Einstein2020-01-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503einstein (São Paulo) v.18 2020reponame:Einstein (São Paulo)instname:Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)instacron:IIEPAE10.31744/einstein_journal/2020rc5111info:eu-repo/semantics/openAccessBo,Carolina Rodrigues DalDevito,Beatriz PiovesanaDevito,Leticia PiovesanaPapa,Gabriella Paes delHamerschlak,Nelsoneng2020-01-06T00:00:00Zoai:scielo:S1679-45082020000100503Revistahttps://journal.einstein.br/pt-br/ONGhttps://old.scielo.br/oai/scielo-oai.php||revista@einstein.br2317-63851679-4508opendoar:2020-01-06T00:00Einstein (São Paulo) - Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)false |
dc.title.none.fl_str_mv |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
title |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
spellingShingle |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review Bo,Carolina Rodrigues Dal Situs inversus Purpura, thrombocytopenic Platelet count Exome Hematologic diseases |
title_short |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
title_full |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
title_fullStr |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
title_full_unstemmed |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
title_sort |
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review |
author |
Bo,Carolina Rodrigues Dal |
author_facet |
Bo,Carolina Rodrigues Dal Devito,Beatriz Piovesana Devito,Leticia Piovesana Papa,Gabriella Paes del Hamerschlak,Nelson |
author_role |
author |
author2 |
Devito,Beatriz Piovesana Devito,Leticia Piovesana Papa,Gabriella Paes del Hamerschlak,Nelson |
author2_role |
author author author author |
dc.contributor.author.fl_str_mv |
Bo,Carolina Rodrigues Dal Devito,Beatriz Piovesana Devito,Leticia Piovesana Papa,Gabriella Paes del Hamerschlak,Nelson |
dc.subject.por.fl_str_mv |
Situs inversus Purpura, thrombocytopenic Platelet count Exome Hematologic diseases |
topic |
Situs inversus Purpura, thrombocytopenic Platelet count Exome Hematologic diseases |
description |
ABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura. |
publishDate |
2020 |
dc.date.none.fl_str_mv |
2020-01-01 |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/report |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
report |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503 |
url |
http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.31744/einstein_journal/2020rc5111 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Instituto Israelita de Ensino e Pesquisa Albert Einstein |
publisher.none.fl_str_mv |
Instituto Israelita de Ensino e Pesquisa Albert Einstein |
dc.source.none.fl_str_mv |
einstein (São Paulo) v.18 2020 reponame:Einstein (São Paulo) instname:Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE) instacron:IIEPAE |
instname_str |
Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE) |
instacron_str |
IIEPAE |
institution |
IIEPAE |
reponame_str |
Einstein (São Paulo) |
collection |
Einstein (São Paulo) |
repository.name.fl_str_mv |
Einstein (São Paulo) - Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE) |
repository.mail.fl_str_mv |
||revista@einstein.br |
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1752129910470606848 |