Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review

Detalhes bibliográficos
Autor(a) principal: Bo,Carolina Rodrigues Dal
Data de Publicação: 2020
Outros Autores: Devito,Beatriz Piovesana, Devito,Leticia Piovesana, Papa,Gabriella Paes del, Hamerschlak,Nelson
Tipo de documento: Relatório
Idioma: eng
Título da fonte: Einstein (São Paulo)
Texto Completo: http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503
Resumo: ABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.
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spelling Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature reviewSitus inversusPurpura, thrombocytopenicPlatelet countExomeHematologic diseasesABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.Instituto Israelita de Ensino e Pesquisa Albert Einstein2020-01-01info:eu-repo/semantics/reportinfo:eu-repo/semantics/publishedVersiontext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1679-45082020000100503einstein (São Paulo) v.18 2020reponame:Einstein (São Paulo)instname:Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)instacron:IIEPAE10.31744/einstein_journal/2020rc5111info:eu-repo/semantics/openAccessBo,Carolina Rodrigues DalDevito,Beatriz PiovesanaDevito,Leticia PiovesanaPapa,Gabriella Paes delHamerschlak,Nelsoneng2020-01-06T00:00:00Zoai:scielo:S1679-45082020000100503Revistahttps://journal.einstein.br/pt-br/ONGhttps://old.scielo.br/oai/scielo-oai.php||revista@einstein.br2317-63851679-4508opendoar:2020-01-06T00:00Einstein (São Paulo) - Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)false
dc.title.none.fl_str_mv Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
spellingShingle Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
Bo,Carolina Rodrigues Dal
Situs inversus
Purpura, thrombocytopenic
Platelet count
Exome
Hematologic diseases
title_short Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_full Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_fullStr Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_full_unstemmed Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_sort Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
author Bo,Carolina Rodrigues Dal
author_facet Bo,Carolina Rodrigues Dal
Devito,Beatriz Piovesana
Devito,Leticia Piovesana
Papa,Gabriella Paes del
Hamerschlak,Nelson
author_role author
author2 Devito,Beatriz Piovesana
Devito,Leticia Piovesana
Papa,Gabriella Paes del
Hamerschlak,Nelson
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Bo,Carolina Rodrigues Dal
Devito,Beatriz Piovesana
Devito,Leticia Piovesana
Papa,Gabriella Paes del
Hamerschlak,Nelson
dc.subject.por.fl_str_mv Situs inversus
Purpura, thrombocytopenic
Platelet count
Exome
Hematologic diseases
topic Situs inversus
Purpura, thrombocytopenic
Platelet count
Exome
Hematologic diseases
description ABSTRACT Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.
publishDate 2020
dc.date.none.fl_str_mv 2020-01-01
dc.type.driver.fl_str_mv info:eu-repo/semantics/report
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dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv 10.31744/einstein_journal/2020rc5111
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dc.publisher.none.fl_str_mv Instituto Israelita de Ensino e Pesquisa Albert Einstein
publisher.none.fl_str_mv Instituto Israelita de Ensino e Pesquisa Albert Einstein
dc.source.none.fl_str_mv einstein (São Paulo) v.18 2020
reponame:Einstein (São Paulo)
instname:Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)
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reponame_str Einstein (São Paulo)
collection Einstein (São Paulo)
repository.name.fl_str_mv Einstein (São Paulo) - Instituto Israelita de Ensino e Pesquisa Albert Einstein (IIEPAE)
repository.mail.fl_str_mv ||revista@einstein.br
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