Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report

Detalhes bibliográficos
Autor(a) principal: Monção, Carlos Rafael Lima
Data de Publicação: 2020
Outros Autores: Dias, Levindo Tadeu Freitas de Figueiredo, Alcântara, Cecília Barbosa, Versiani, Thereza Cristina Abreu, Correia, Autieri Alves
Tipo de documento: Artigo
Idioma: por
eng
Título da fonte: Revista Brasileira de Cancerologia (Online)
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/826
Resumo: Introduction: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor) is a neoplasm extremely rare that represents less than 1% of all the pancreatic tumors. Case report: 48 years old female patient was hospitalized with intra-abdominal mass of etiology hard to define. She was submitted to surgical treatment with successful laparotomy tumor resection and there were no postoperative complications. The patients usually become symptomatic only after long time of evolution, when they have discomfort or abdominal pain or palpation of abdominal masses during physical examination. Complementary exams like ultrasound and computed tomography are necessary to diagnosis and usually they show heterogeneous large intra-abdominal masses. It is necessary the confirmation with anatomopathological study which usually has histological characteristics compatible with low-grade malignancy. The surgical resection is the recommended treatment and even large size tumors has a considerable chance of cure if free surgical margins are obtained. It is known that complete tumoral resection is associated with long-term survival. Conclusion: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor), although rare, should be considered in differential diagnosis of pancreatic neoplasms because surgical treatment usually has good chances of cure even in large size tumors.
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spelling Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case ReportNeoplasia Sólida-Pseudopapilar de Páncreas (Tumor de Frantz): Relato de CasoNeoplasia Pseudopapilífera Sólida de Pâncreas (Tumor de Frantz): Relato de CasoNeoplasias PancreáticasNeoplasias AbdominaisPâncreasMulheresRelatos de CasosPancreatic NeoplasmsAbdominal NeoplasmsPancreasWomenCase ReportsNeoplasias PancreáticasNeoplasias AbdominalesPáncreasMujeresInformes de CasosIntroduction: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor) is a neoplasm extremely rare that represents less than 1% of all the pancreatic tumors. Case report: 48 years old female patient was hospitalized with intra-abdominal mass of etiology hard to define. She was submitted to surgical treatment with successful laparotomy tumor resection and there were no postoperative complications. The patients usually become symptomatic only after long time of evolution, when they have discomfort or abdominal pain or palpation of abdominal masses during physical examination. Complementary exams like ultrasound and computed tomography are necessary to diagnosis and usually they show heterogeneous large intra-abdominal masses. It is necessary the confirmation with anatomopathological study which usually has histological characteristics compatible with low-grade malignancy. The surgical resection is the recommended treatment and even large size tumors has a considerable chance of cure if free surgical margins are obtained. It is known that complete tumoral resection is associated with long-term survival. Conclusion: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor), although rare, should be considered in differential diagnosis of pancreatic neoplasms because surgical treatment usually has good chances of cure even in large size tumors.Introducción: La neoplasia sólida-pseudopapilar de páncreas (tumor de Frantz) es muy extraordinaria y representa menos de 1% de todos los tumores pancreáticos. Relato del caso: Paciente do sexo femenino, 48 años, internada para investigación de masa intraabdominal de etiología a esclarecer. Fue sometida al tratamiento quirúrgico con éxito en la resección tumoral y no presentó complicaciones en el postoperatorio. Los pacientes por lo general se convierten en sintomáticos solamente después de largos períodos de evolución, cuando presentan incomodidad o dolor abdominal o existe palpación de masas abdominales en el examen físico. Para el diagnóstico son necesarios exámenes de imagen como ecografía y tomografía computarizada que generalmente demuestran voluminosas masas heterogéneas intraabdominales. Es necesaria la confirmación con examen anatomopatológico y generalmente tienen características histológicas compatibles con tumores de poco grado de malignidad. La resección quirúrgica es el tratamiento indicado y mismo tumores de grandes dimensiones poseen posibilidades de curas considerables se sea posible obtener márgenes quirúrgicas libres. Se sabe que a resección tumoral completa es asociada a largos períodos de sobrevida. Conclusión: La neoplasia sólida-pseudopapilar de páncreas o tumor de Frantz: a pesar de extraordinaria, debe ser considerada en el diagnóstico diferencial de tumores de páncreas y a que el tratamiento quirúrgico presenta buenas posibilidades de cura, mismo en tumores de grandes proporciones.Introdução: A neoplasia pseudopapilífera sólida de pâncreas (tumor de Frantz) é muito rara e representa menos de 1% de todos os tumores pancreáticos. Relato do caso: Paciente do sexo feminino, 48 anos, internada para investigação de massa intra-abdominal de etiologia a esclarecer. Foi submetida a tratamento cirúrgico com sucesso na ressecção tumoral e não apresentou complicações no pós-operatório. Os pacientes usualmente tornam-se sintomáticos somente após longos períodos de evolução, quando então apresentam desconforto ou dor abdominal, ou a palpação de massas abdominais no exame físico. Para o diagnóstico, são necessários exames de imagem como ultrassonografia e tomografia computadorizada, que geralmente evidenciam volumosas massas heterogêneas intra-abdominais. É necessária a confirmação com estudo anatomopatológico e comumente estas possuem características histológicas compatíveis com tumores de baixo grau de malignidade. A ressecção cirúrgica é o tratamento recomendado e mesmo os tumores de grandes dimensões possuem chances de curas consideráveis, se for possível obter margens cirúrgicas livres. Sabe-se que a ressecção tumoral completa é associada a longos períodos de sobrevida. Conclusão: A neoplasia pseudopapilífera sólida de pâncreas (tumor de Frantz), apesar de rara, deve ser considerada no diagnóstico diferencial de tumores de pâncreas, já que o tratamento cirúrgico apresenta boas chances de cura mesmo em tumores de grandes dimensões.INCA2020-10-23info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/82610.32635/2176-9745.RBC.2020v66n4.826Revista Brasileira de Cancerologia; Vol. 66 No. 4 (2020): Oct./Nov./Dec.; e-11826Revista Brasileira de Cancerologia; Vol. 66 Núm. 4 (2020): oct./nov./dic.; e-11826Revista Brasileira de Cancerologia; v. 66 n. 4 (2020): out./nov./dez.; e-118262176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporenghttps://rbc.inca.gov.br/index.php/revista/article/view/826/758https://rbc.inca.gov.br/index.php/revista/article/view/826/890Copyright (c) 2020 Revista Brasileira de Cancerologiainfo:eu-repo/semantics/openAccessMonção, Carlos Rafael LimaDias, Levindo Tadeu Freitas de Figueiredo Alcântara, Cecília Barbosa Versiani, Thereza Cristina Abreu Correia, Autieri Alves 2021-11-29T18:29:37Zoai:rbc.inca.gov.br:article/826Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T18:29:37Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
Neoplasia Sólida-Pseudopapilar de Páncreas (Tumor de Frantz): Relato de Caso
Neoplasia Pseudopapilífera Sólida de Pâncreas (Tumor de Frantz): Relato de Caso
title Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
spellingShingle Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
Monção, Carlos Rafael Lima
Neoplasias Pancreáticas
Neoplasias Abdominais
Pâncreas
Mulheres
Relatos de Casos
Pancreatic Neoplasms
Abdominal Neoplasms
Pancreas
Women
Case Reports
Neoplasias Pancreáticas
Neoplasias Abdominales
Páncreas
Mujeres
Informes de Casos
title_short Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
title_full Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
title_fullStr Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
title_full_unstemmed Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
title_sort Solid Pseudopapillary Tumor of the Pancreas (Frantz’s Tumor): Case Report
author Monção, Carlos Rafael Lima
author_facet Monção, Carlos Rafael Lima
Dias, Levindo Tadeu Freitas de Figueiredo
Alcântara, Cecília Barbosa
Versiani, Thereza Cristina Abreu
Correia, Autieri Alves
author_role author
author2 Dias, Levindo Tadeu Freitas de Figueiredo
Alcântara, Cecília Barbosa
Versiani, Thereza Cristina Abreu
Correia, Autieri Alves
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Monção, Carlos Rafael Lima
Dias, Levindo Tadeu Freitas de Figueiredo
Alcântara, Cecília Barbosa
Versiani, Thereza Cristina Abreu
Correia, Autieri Alves
dc.subject.por.fl_str_mv Neoplasias Pancreáticas
Neoplasias Abdominais
Pâncreas
Mulheres
Relatos de Casos
Pancreatic Neoplasms
Abdominal Neoplasms
Pancreas
Women
Case Reports
Neoplasias Pancreáticas
Neoplasias Abdominales
Páncreas
Mujeres
Informes de Casos
topic Neoplasias Pancreáticas
Neoplasias Abdominais
Pâncreas
Mulheres
Relatos de Casos
Pancreatic Neoplasms
Abdominal Neoplasms
Pancreas
Women
Case Reports
Neoplasias Pancreáticas
Neoplasias Abdominales
Páncreas
Mujeres
Informes de Casos
description Introduction: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor) is a neoplasm extremely rare that represents less than 1% of all the pancreatic tumors. Case report: 48 years old female patient was hospitalized with intra-abdominal mass of etiology hard to define. She was submitted to surgical treatment with successful laparotomy tumor resection and there were no postoperative complications. The patients usually become symptomatic only after long time of evolution, when they have discomfort or abdominal pain or palpation of abdominal masses during physical examination. Complementary exams like ultrasound and computed tomography are necessary to diagnosis and usually they show heterogeneous large intra-abdominal masses. It is necessary the confirmation with anatomopathological study which usually has histological characteristics compatible with low-grade malignancy. The surgical resection is the recommended treatment and even large size tumors has a considerable chance of cure if free surgical margins are obtained. It is known that complete tumoral resection is associated with long-term survival. Conclusion: The solid pseudopapillary tumor of the pancreas (Frantz’s tumor), although rare, should be considered in differential diagnosis of pancreatic neoplasms because surgical treatment usually has good chances of cure even in large size tumors.
publishDate 2020
dc.date.none.fl_str_mv 2020-10-23
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Relato de Caso
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/826
10.32635/2176-9745.RBC.2020v66n4.826
url https://rbc.inca.gov.br/index.php/revista/article/view/826
identifier_str_mv 10.32635/2176-9745.RBC.2020v66n4.826
dc.language.iso.fl_str_mv por
eng
language por
eng
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/826/758
https://rbc.inca.gov.br/index.php/revista/article/view/826/890
dc.rights.driver.fl_str_mv Copyright (c) 2020 Revista Brasileira de Cancerologia
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2020 Revista Brasileira de Cancerologia
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 66 No. 4 (2020): Oct./Nov./Dec.; e-11826
Revista Brasileira de Cancerologia; Vol. 66 Núm. 4 (2020): oct./nov./dic.; e-11826
Revista Brasileira de Cancerologia; v. 66 n. 4 (2020): out./nov./dez.; e-11826
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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