Vulva Plexiform Fibrohistiocytic Tumor: Case Report

Detalhes bibliográficos
Autor(a) principal: Baumgartner, Aluisio Juliano
Data de Publicação: 2021
Outros Autores: Garcia, Fernanda Stefania Bastos, Ono, Lia Mizobe, Oliveira, Érica Condé Marques e, Fuzita, William Hiromi, Anjos, Caroline Souza dos
Tipo de documento: Artigo
Idioma: por
eng
Título da fonte: Revista Brasileira de Cancerologia (Online)
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/1269
Resumo: Introduction: Plexiform fibrohistiocytic tumor is a rare clinical condition, with about 150 cases described in the literature. Case report: 23-yearsold, female patient with nodular lesion in vulva without malignancy characteristics on ultrasound image. She underwent clinical follow-up and after an increase in the size of the lesion, surgical resection was opted. Histopathological findings suggested plexiform fibrohistiocytic tumor, with free surgical margins. In follow up, she was referred to oncological evaluation for screening complementary exams and rule out morphologically similar diagnoses. After the complementary exams confirming the initial diagnosis of plexiform fibrohistiocytic tumor and without evidence of metastatic disease after complete surgical excision with free margins, the patient is in clinical follow-up. Conclusion: Reporting the case is extremely important to disseminate the clinical presentation, diagnostic steps, proposed treatment and share information about the clinical evolution presented.
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spelling Vulva Plexiform Fibrohistiocytic Tumor: Case ReportTumor Fibrohistiocítico Plexiforme de la Vulva: Reporte de CasoTumor Fibro-histiocítico Plexiforme de Vulva: Relato de CasoSarcoma HistiocíticoNeoplasias VulvaresRelatos de CasosHistiocytic SarcomaVulvar NeoplasmsCase ReportsSarcoma HistiocíticoNeoplasias de la VulvaInformes de CasosIntroduction: Plexiform fibrohistiocytic tumor is a rare clinical condition, with about 150 cases described in the literature. Case report: 23-yearsold, female patient with nodular lesion in vulva without malignancy characteristics on ultrasound image. She underwent clinical follow-up and after an increase in the size of the lesion, surgical resection was opted. Histopathological findings suggested plexiform fibrohistiocytic tumor, with free surgical margins. In follow up, she was referred to oncological evaluation for screening complementary exams and rule out morphologically similar diagnoses. After the complementary exams confirming the initial diagnosis of plexiform fibrohistiocytic tumor and without evidence of metastatic disease after complete surgical excision with free margins, the patient is in clinical follow-up. Conclusion: Reporting the case is extremely important to disseminate the clinical presentation, diagnostic steps, proposed treatment and share information about the clinical evolution presented.Introducción: El tumor fibrohistiocítico plexiforme es una condición clínica poco frecuente, con unos 150 casos descritos en la literatura. Reporte del caso: Paciente de 23, sexo feminino, años con lesión nodular en una región vulvar sin características malignas en los exámenes de ultrasonido. Se sometió a un seguimiento clínico, habiendo presentado un aumento en el tamaño de la lesión inicial, y se decidió realizar la resección quirúrgica de la lesión. En un estudio histopatológico, se evidenció una lesión compatible con tumor fibrohistiocítico plexiforme con márgenes quirúrgicos libres. Fue referida para la evaluación oncológica, realizó pruebas complementarias para el cribado y para descartar diagnósticos morfológicamente similares. En vista de las pruebas complementarias que confirman el diagnóstico inicial y sin evidencia de enfermedad metastásica después de una escisión quirúrgica completa con márgenes libres, se inició el seguimiento clínico. Conclusión: Informar del caso es extremadamente importante para difundir la presentación clínica, etapas diagnósticas, tratamiento propuesto y compartir información sobre la evolución clínica presentada.Introdução: O tumor fibro-histiocítico plexiforme é uma condição clínica rara, com cerca de 150 casos descritos na literatura. Relato do caso: Paciente, 23 anos, sexo feminino, portadora de lesão nodular em região vulvar sem características de malignidade em exames de ultrassonografia. Realizou acompanhamento clínico, tendo apresentado aumento do tamanho da lesão inicial, sendo optado então por realização de ressecção cirúrgica da lesão. Em estudo histopatológico, evidenciou-se lesão compatível com tumor fibro-histiocítico plexiforme, com margens cirúrgicas livres. No seguimento, a paciente foi encaminhada para avaliação oncológica com a intenção de realizar exames complementares de rastreio e descartar diagnósticos morfologicamente semelhantes. Diante dos exames complementares confirmando o diagnóstico inicial e sem evidência de doença metastática após excisão cirúrgica completa com margens livres, foi iniciado seguimento clínico. Conclusão: Relatar o caso é de extrema importância para divulgar a apresentação clínica, etapas diagnósticas, tratamento proposto e compartilhar informações acerca de evolução clínica apresentada.INCA2021-03-26info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/126910.32635/2176-9745.RBC.2021v67n2.1269Revista Brasileira de Cancerologia; Vol. 67 No. 2 (2021): Apr./May/June; e-141269Revista Brasileira de Cancerologia; Vol. 67 Núm. 2 (2021): abr./mayo/jun.; e-141269Revista Brasileira de Cancerologia; v. 67 n. 2 (2021): abr./maio/jun.; e-1412692176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporenghttps://rbc.inca.gov.br/index.php/revista/article/view/1269/1054https://rbc.inca.gov.br/index.php/revista/article/view/1269/1352Copyright (c) 2021 Revista Brasileira de Cancerologiainfo:eu-repo/semantics/openAccessBaumgartner, Aluisio Juliano Garcia, Fernanda Stefania BastosOno, Lia Mizobe Oliveira, Érica Condé Marques e Fuzita, William Hiromi Anjos, Caroline Souza dos2021-11-29T18:27:28Zoai:rbc.inca.gov.br:article/1269Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T18:27:28Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Vulva Plexiform Fibrohistiocytic Tumor: Case Report
Tumor Fibrohistiocítico Plexiforme de la Vulva: Reporte de Caso
Tumor Fibro-histiocítico Plexiforme de Vulva: Relato de Caso
title Vulva Plexiform Fibrohistiocytic Tumor: Case Report
spellingShingle Vulva Plexiform Fibrohistiocytic Tumor: Case Report
Baumgartner, Aluisio Juliano
Sarcoma Histiocítico
Neoplasias Vulvares
Relatos de Casos
Histiocytic Sarcoma
Vulvar Neoplasms
Case Reports
Sarcoma Histiocítico
Neoplasias de la Vulva
Informes de Casos
title_short Vulva Plexiform Fibrohistiocytic Tumor: Case Report
title_full Vulva Plexiform Fibrohistiocytic Tumor: Case Report
title_fullStr Vulva Plexiform Fibrohistiocytic Tumor: Case Report
title_full_unstemmed Vulva Plexiform Fibrohistiocytic Tumor: Case Report
title_sort Vulva Plexiform Fibrohistiocytic Tumor: Case Report
author Baumgartner, Aluisio Juliano
author_facet Baumgartner, Aluisio Juliano
Garcia, Fernanda Stefania Bastos
Ono, Lia Mizobe
Oliveira, Érica Condé Marques e
Fuzita, William Hiromi
Anjos, Caroline Souza dos
author_role author
author2 Garcia, Fernanda Stefania Bastos
Ono, Lia Mizobe
Oliveira, Érica Condé Marques e
Fuzita, William Hiromi
Anjos, Caroline Souza dos
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Baumgartner, Aluisio Juliano
Garcia, Fernanda Stefania Bastos
Ono, Lia Mizobe
Oliveira, Érica Condé Marques e
Fuzita, William Hiromi
Anjos, Caroline Souza dos
dc.subject.por.fl_str_mv Sarcoma Histiocítico
Neoplasias Vulvares
Relatos de Casos
Histiocytic Sarcoma
Vulvar Neoplasms
Case Reports
Sarcoma Histiocítico
Neoplasias de la Vulva
Informes de Casos
topic Sarcoma Histiocítico
Neoplasias Vulvares
Relatos de Casos
Histiocytic Sarcoma
Vulvar Neoplasms
Case Reports
Sarcoma Histiocítico
Neoplasias de la Vulva
Informes de Casos
description Introduction: Plexiform fibrohistiocytic tumor is a rare clinical condition, with about 150 cases described in the literature. Case report: 23-yearsold, female patient with nodular lesion in vulva without malignancy characteristics on ultrasound image. She underwent clinical follow-up and after an increase in the size of the lesion, surgical resection was opted. Histopathological findings suggested plexiform fibrohistiocytic tumor, with free surgical margins. In follow up, she was referred to oncological evaluation for screening complementary exams and rule out morphologically similar diagnoses. After the complementary exams confirming the initial diagnosis of plexiform fibrohistiocytic tumor and without evidence of metastatic disease after complete surgical excision with free margins, the patient is in clinical follow-up. Conclusion: Reporting the case is extremely important to disseminate the clinical presentation, diagnostic steps, proposed treatment and share information about the clinical evolution presented.
publishDate 2021
dc.date.none.fl_str_mv 2021-03-26
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Relato de Caso
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/1269
10.32635/2176-9745.RBC.2021v67n2.1269
url https://rbc.inca.gov.br/index.php/revista/article/view/1269
identifier_str_mv 10.32635/2176-9745.RBC.2021v67n2.1269
dc.language.iso.fl_str_mv por
eng
language por
eng
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/1269/1054
https://rbc.inca.gov.br/index.php/revista/article/view/1269/1352
dc.rights.driver.fl_str_mv Copyright (c) 2021 Revista Brasileira de Cancerologia
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2021 Revista Brasileira de Cancerologia
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 67 No. 2 (2021): Apr./May/June; e-141269
Revista Brasileira de Cancerologia; Vol. 67 Núm. 2 (2021): abr./mayo/jun.; e-141269
Revista Brasileira de Cancerologia; v. 67 n. 2 (2021): abr./maio/jun.; e-141269
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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