Frantz's Tumor: Report of a case

Detalhes bibliográficos
Autor(a) principal: Macedo, Thiago Andrade de
Data de Publicação: 2004
Outros Autores: Vieira, Sabas Carlos, Oliveira, Adriano Machado de, Coelho, Eid Gonçalves, Santos, Lina Gomes dos, Santana, Jerúsia Oliveira Ibiapina de
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista Brasileira de Cancerologia (Online)
DOI: 10.32635/2176-9745.RBC.2004v50n1.2054
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/2054
Resumo: Frantz´s tumor is a rare neoplasia of the pancreas that occur mainly in teenage patients with a good prognosis. A little over 300 cases have been reported in the literature worldwide. The autors present a case of Frantz's tumor on a female patient, whose presentation was palpable abdominal mass. CT scans and ultrasound imaging showed a solid cystic mass. Two thirds of these tumors occur at the body or tail of the pancreas, and in spite of the excessive growth around the pancreas, it rarely invades vascular structures or adjacent organs, what could have been seen intraoperatively in this case. The patient was submitted to a partial pancreatectomy of body and tail with preservation of the spleen. Microscopic examination displayed evident cystic cavities with occasional papillary structures. The patient is disease-free 24 months after the operation. We emphasize the need to consider tumor of Frantz as a differential diagnosis for abdominal masses in youngsters.
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spelling Frantz's Tumor: Report of a caseTumor de Frantz: Relato de um CasoTumor de FrantzNeoplasias PancreáticasDiagnóstico DiferencialCirurgiaPrognósticoFrantz's TumorPancreatic NeoplasmsDifferential DiagnosisSurgeryPrognosisFrantz´s tumor is a rare neoplasia of the pancreas that occur mainly in teenage patients with a good prognosis. A little over 300 cases have been reported in the literature worldwide. The autors present a case of Frantz's tumor on a female patient, whose presentation was palpable abdominal mass. CT scans and ultrasound imaging showed a solid cystic mass. Two thirds of these tumors occur at the body or tail of the pancreas, and in spite of the excessive growth around the pancreas, it rarely invades vascular structures or adjacent organs, what could have been seen intraoperatively in this case. The patient was submitted to a partial pancreatectomy of body and tail with preservation of the spleen. Microscopic examination displayed evident cystic cavities with occasional papillary structures. The patient is disease-free 24 months after the operation. We emphasize the need to consider tumor of Frantz as a differential diagnosis for abdominal masses in youngsters.O tumor de Frantz é uma neoplasia rara do pâncreas. Ocorre principalmente em pacientes jovens e apresenta um bom prognóstico. Pouco mais de 300 casos foram relatados na literatura mundial. Os autores apresentam um caso de Tumor de Frantz, em uma paciente do sexo feminino cuja apresentação clínica foi de massa abdominal palpável. A tomografia computadorizada (TC) associada à ultrassonografia (US) evidenciaram presença de massa sólidocística. Dois terços destes tumores ocorrem no corpo e cauda do pâncreas, e apesar do crescimento excessivo para fora dos limites pancreáticos, raramente invadem estruturas vasculares ou órgãos adjacentes, o que correspondeu aos achados intraoperatórios do caso. A paciente foi submetida a pancreatectomia corpo-caudal com preservação do baço. À microscopia foram evidenciadas cavidades císticas com ocasionais estruturas papilíferas. A paciente encontra-se sem evidência da doença 24 meses após a operação. Enfatiza-se a necessidade de se considerar o tumor de Frantz no diagnóstico diferencial de massa abdominal em pacientes jovens.INCA2004-03-31info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRelato de Casoapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/205410.32635/2176-9745.RBC.2004v50n1.2054Revista Brasileira de Cancerologia; Vol. 50 No. 1 (2004): Jan./Feb./Mar.; 33-35Revista Brasileira de Cancerologia; Vol. 50 Núm. 1 (2004): ene./feb./mar.; 33-35Revista Brasileira de Cancerologia; v. 50 n. 1 (2004): jan./fev./mar.; 33-352176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/2054/1272Macedo, Thiago Andrade de Vieira, Sabas Carlos Oliveira, Adriano Machado de Coelho, Eid Gonçalves Santos, Lina Gomes dos Santana, Jerúsia Oliveira Ibiapina de info:eu-repo/semantics/openAccess2021-11-29T20:34:02Zoai:rbc.inca.gov.br:article/2054Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2021-11-29T20:34:02Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Frantz's Tumor: Report of a case
Tumor de Frantz: Relato de um Caso
title Frantz's Tumor: Report of a case
spellingShingle Frantz's Tumor: Report of a case
Frantz's Tumor: Report of a case
Macedo, Thiago Andrade de
Tumor de Frantz
Neoplasias Pancreáticas
Diagnóstico Diferencial
Cirurgia
Prognóstico
Frantz's Tumor
Pancreatic Neoplasms
Differential Diagnosis
Surgery
Prognosis
Macedo, Thiago Andrade de
Tumor de Frantz
Neoplasias Pancreáticas
Diagnóstico Diferencial
Cirurgia
Prognóstico
Frantz's Tumor
Pancreatic Neoplasms
Differential Diagnosis
Surgery
Prognosis
title_short Frantz's Tumor: Report of a case
title_full Frantz's Tumor: Report of a case
title_fullStr Frantz's Tumor: Report of a case
Frantz's Tumor: Report of a case
title_full_unstemmed Frantz's Tumor: Report of a case
Frantz's Tumor: Report of a case
title_sort Frantz's Tumor: Report of a case
author Macedo, Thiago Andrade de
author_facet Macedo, Thiago Andrade de
Macedo, Thiago Andrade de
Vieira, Sabas Carlos
Oliveira, Adriano Machado de
Coelho, Eid Gonçalves
Santos, Lina Gomes dos
Santana, Jerúsia Oliveira Ibiapina de
Vieira, Sabas Carlos
Oliveira, Adriano Machado de
Coelho, Eid Gonçalves
Santos, Lina Gomes dos
Santana, Jerúsia Oliveira Ibiapina de
author_role author
author2 Vieira, Sabas Carlos
Oliveira, Adriano Machado de
Coelho, Eid Gonçalves
Santos, Lina Gomes dos
Santana, Jerúsia Oliveira Ibiapina de
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Macedo, Thiago Andrade de
Vieira, Sabas Carlos
Oliveira, Adriano Machado de
Coelho, Eid Gonçalves
Santos, Lina Gomes dos
Santana, Jerúsia Oliveira Ibiapina de
dc.subject.por.fl_str_mv Tumor de Frantz
Neoplasias Pancreáticas
Diagnóstico Diferencial
Cirurgia
Prognóstico
Frantz's Tumor
Pancreatic Neoplasms
Differential Diagnosis
Surgery
Prognosis
topic Tumor de Frantz
Neoplasias Pancreáticas
Diagnóstico Diferencial
Cirurgia
Prognóstico
Frantz's Tumor
Pancreatic Neoplasms
Differential Diagnosis
Surgery
Prognosis
description Frantz´s tumor is a rare neoplasia of the pancreas that occur mainly in teenage patients with a good prognosis. A little over 300 cases have been reported in the literature worldwide. The autors present a case of Frantz's tumor on a female patient, whose presentation was palpable abdominal mass. CT scans and ultrasound imaging showed a solid cystic mass. Two thirds of these tumors occur at the body or tail of the pancreas, and in spite of the excessive growth around the pancreas, it rarely invades vascular structures or adjacent organs, what could have been seen intraoperatively in this case. The patient was submitted to a partial pancreatectomy of body and tail with preservation of the spleen. Microscopic examination displayed evident cystic cavities with occasional papillary structures. The patient is disease-free 24 months after the operation. We emphasize the need to consider tumor of Frantz as a differential diagnosis for abdominal masses in youngsters.
publishDate 2004
dc.date.none.fl_str_mv 2004-03-31
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Relato de Caso
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status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2054
10.32635/2176-9745.RBC.2004v50n1.2054
url https://rbc.inca.gov.br/index.php/revista/article/view/2054
identifier_str_mv 10.32635/2176-9745.RBC.2004v50n1.2054
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2054/1272
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 50 No. 1 (2004): Jan./Feb./Mar.; 33-35
Revista Brasileira de Cancerologia; Vol. 50 Núm. 1 (2004): ene./feb./mar.; 33-35
Revista Brasileira de Cancerologia; v. 50 n. 1 (2004): jan./fev./mar.; 33-35
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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dc.identifier.doi.none.fl_str_mv 10.32635/2176-9745.RBC.2004v50n1.2054