Extramammary Paget's Disease in Perineo-inguinoscrotal Region

Detalhes bibliográficos
Autor(a) principal: Junqueira Júnior, Gérson
Data de Publicação: 2022
Outros Autores: Amaral, Renato Luiz, Vedovato, Julio Walter, Torres, Olavo Machado, Santos, Wellington Gemelli dos, Silva, Adriano de Lima e, Cartell, André
Tipo de documento: Artigo
Idioma: por
Título da fonte: Revista Brasileira de Cancerologia (Online)
DOI: 10.32635/2176-9745.RBC.1999v45n3.2784
Texto Completo: https://rbc.inca.gov.br/index.php/revista/article/view/2784
Resumo: Extramammary Paget’s Disease is a rare disease. There is a dose correlation with anorrectal carcinoma when the disease is perianal. It is also associated with internal malignancies and bad prognosis. The authors describe a case of extramammary Paget’s Disease in perineo-inguinoscrotal region of a 59-year-old-white man, who had a hyperpigmented and pruritic lesion of approximately 6 cm of diameter which has increased and was presenting minimum bleeding. Staging tests were normal, without evidence of metastasis. The anatomopathological test of the lesion revealed na aspect compatible with extramammary Paget’s Disease. The patient was submmited to an enlarged excision of the lesion and thin skin graft. The aspects related to epidemiology, pathology, staging, prognosis and treatment of this neoplasia are discussed in this article.
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spelling Extramammary Paget's Disease in Perineo-inguinoscrotal RegionDoença de Paget Extramamáría em Região Períneo-ínguino-escrotalDoença de PagetExtramamáriaPeleNeoplasias MalignasPaget’s DiseaseExtramammarySkinMalignant NeoplasmsExtramammary Paget’s Disease is a rare disease. There is a dose correlation with anorrectal carcinoma when the disease is perianal. It is also associated with internal malignancies and bad prognosis. The authors describe a case of extramammary Paget’s Disease in perineo-inguinoscrotal region of a 59-year-old-white man, who had a hyperpigmented and pruritic lesion of approximately 6 cm of diameter which has increased and was presenting minimum bleeding. Staging tests were normal, without evidence of metastasis. The anatomopathological test of the lesion revealed na aspect compatible with extramammary Paget’s Disease. The patient was submmited to an enlarged excision of the lesion and thin skin graft. The aspects related to epidemiology, pathology, staging, prognosis and treatment of this neoplasia are discussed in this article.A doença de Paget extramamária constitui-se numa patologia rara. Existe uma estreita correlação com carcinoma anorretal quando a doença é perianal. Também está associada com malignidades internas e mau prognóstico. Os autores relatam um caso de Doença de Paget extramamária em região perineo-inguino-escrotal, num homem branco de 59 anos, que apresentava uma lesão de aproximadamente 6 cm de diâmetro, hiperpigmentada e pruriginosa, lesão esta que aumentou de tamanho e que vinha apresentando mínimo sangramento. Os exames de estadiamento foram normais, sem evidência de metástases. O exame anátomo-patológico da lesão revelou aspecto compatível com Doença de Paget extramamária. A conduta então foi a excisão ampliada da lesão e enxerto de pele fina. São discutidos os aspectos referentes à epidemiologia, patologia, estadiamento, prognóstico e tratamento desta neoplasia.INCA2022-09-21info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionArtigos, Avaliado pelos paresapplication/pdfhttps://rbc.inca.gov.br/index.php/revista/article/view/278410.32635/2176-9745.RBC.1999v45n3.2784Revista Brasileira de Cancerologia; Vol. 45 No. 3 (1999): July/Aug./Sept.; 51-55Revista Brasileira de Cancerologia; Vol. 45 Núm. 3 (1999): jul./ago./sept.; 51-55Revista Brasileira de Cancerologia; v. 45 n. 3 (1999): jul./ago./set.; 51-552176-9745reponame:Revista Brasileira de Cancerologia (Online)instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)instacron:INCAporhttps://rbc.inca.gov.br/index.php/revista/article/view/2784/1661https://creativecommons.org/licenses/by/4.0info:eu-repo/semantics/openAccessJunqueira Júnior, GérsonAmaral, Renato LuizVedovato, Julio WalterTorres, Olavo MachadoSantos, Wellington Gemelli dos Silva, Adriano de Lima eCartell, André2023-01-18T15:15:10Zoai:rbc.inca.gov.br:article/2784Revistahttps://rbc.inca.gov.br/index.php/revistaPUBhttps://rbc.inca.gov.br/index.php/revista/oairbc@inca.gov.br0034-71162176-9745opendoar:2023-01-18T15:15:10Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)false
dc.title.none.fl_str_mv Extramammary Paget's Disease in Perineo-inguinoscrotal Region
Doença de Paget Extramamáría em Região Períneo-ínguino-escrotal
title Extramammary Paget's Disease in Perineo-inguinoscrotal Region
spellingShingle Extramammary Paget's Disease in Perineo-inguinoscrotal Region
Extramammary Paget's Disease in Perineo-inguinoscrotal Region
Junqueira Júnior, Gérson
Doença de Paget
Extramamária
Pele
Neoplasias Malignas
Paget’s Disease
Extramammary
Skin
Malignant Neoplasms
Junqueira Júnior, Gérson
Doença de Paget
Extramamária
Pele
Neoplasias Malignas
Paget’s Disease
Extramammary
Skin
Malignant Neoplasms
title_short Extramammary Paget's Disease in Perineo-inguinoscrotal Region
title_full Extramammary Paget's Disease in Perineo-inguinoscrotal Region
title_fullStr Extramammary Paget's Disease in Perineo-inguinoscrotal Region
Extramammary Paget's Disease in Perineo-inguinoscrotal Region
title_full_unstemmed Extramammary Paget's Disease in Perineo-inguinoscrotal Region
Extramammary Paget's Disease in Perineo-inguinoscrotal Region
title_sort Extramammary Paget's Disease in Perineo-inguinoscrotal Region
author Junqueira Júnior, Gérson
author_facet Junqueira Júnior, Gérson
Junqueira Júnior, Gérson
Amaral, Renato Luiz
Vedovato, Julio Walter
Torres, Olavo Machado
Santos, Wellington Gemelli dos
Silva, Adriano de Lima e
Cartell, André
Amaral, Renato Luiz
Vedovato, Julio Walter
Torres, Olavo Machado
Santos, Wellington Gemelli dos
Silva, Adriano de Lima e
Cartell, André
author_role author
author2 Amaral, Renato Luiz
Vedovato, Julio Walter
Torres, Olavo Machado
Santos, Wellington Gemelli dos
Silva, Adriano de Lima e
Cartell, André
author2_role author
author
author
author
author
author
dc.contributor.author.fl_str_mv Junqueira Júnior, Gérson
Amaral, Renato Luiz
Vedovato, Julio Walter
Torres, Olavo Machado
Santos, Wellington Gemelli dos
Silva, Adriano de Lima e
Cartell, André
dc.subject.por.fl_str_mv Doença de Paget
Extramamária
Pele
Neoplasias Malignas
Paget’s Disease
Extramammary
Skin
Malignant Neoplasms
topic Doença de Paget
Extramamária
Pele
Neoplasias Malignas
Paget’s Disease
Extramammary
Skin
Malignant Neoplasms
description Extramammary Paget’s Disease is a rare disease. There is a dose correlation with anorrectal carcinoma when the disease is perianal. It is also associated with internal malignancies and bad prognosis. The authors describe a case of extramammary Paget’s Disease in perineo-inguinoscrotal region of a 59-year-old-white man, who had a hyperpigmented and pruritic lesion of approximately 6 cm of diameter which has increased and was presenting minimum bleeding. Staging tests were normal, without evidence of metastasis. The anatomopathological test of the lesion revealed na aspect compatible with extramammary Paget’s Disease. The patient was submmited to an enlarged excision of the lesion and thin skin graft. The aspects related to epidemiology, pathology, staging, prognosis and treatment of this neoplasia are discussed in this article.
publishDate 2022
dc.date.none.fl_str_mv 2022-09-21
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Artigos, Avaliado pelos pares
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2784
10.32635/2176-9745.RBC.1999v45n3.2784
url https://rbc.inca.gov.br/index.php/revista/article/view/2784
identifier_str_mv 10.32635/2176-9745.RBC.1999v45n3.2784
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://rbc.inca.gov.br/index.php/revista/article/view/2784/1661
dc.rights.driver.fl_str_mv https://creativecommons.org/licenses/by/4.0
info:eu-repo/semantics/openAccess
rights_invalid_str_mv https://creativecommons.org/licenses/by/4.0
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv INCA
publisher.none.fl_str_mv INCA
dc.source.none.fl_str_mv Revista Brasileira de Cancerologia; Vol. 45 No. 3 (1999): July/Aug./Sept.; 51-55
Revista Brasileira de Cancerologia; Vol. 45 Núm. 3 (1999): jul./ago./sept.; 51-55
Revista Brasileira de Cancerologia; v. 45 n. 3 (1999): jul./ago./set.; 51-55
2176-9745
reponame:Revista Brasileira de Cancerologia (Online)
instname:Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron:INCA
instname_str Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
instacron_str INCA
institution INCA
reponame_str Revista Brasileira de Cancerologia (Online)
collection Revista Brasileira de Cancerologia (Online)
repository.name.fl_str_mv Revista Brasileira de Cancerologia (Online) - Instituto Nacional de Câncer José Alencar Gomes da Silva (INCA)
repository.mail.fl_str_mv rbc@inca.gov.br
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dc.identifier.doi.none.fl_str_mv 10.32635/2176-9745.RBC.1999v45n3.2784

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