Orofacial Findings and Dental Management of a Child with Williams Syndrome

Detalhes bibliográficos
Autor(a) principal: Pereira, Luciana
Data de Publicação: 2016
Outros Autores: Soares, Daniela Novaes, Pedro, Rafael de Lima, Fidalgo, Tatiana Kelly da Silva, Costa, Marcelo Castro, Castro, Gloria Fernanda Barbosa de Araújo
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Revista odonto ciência (Online)
Texto Completo: https://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/17770
Resumo: Williams syndrome (WS) is a multisystem, congenital and panethnic disorder characterized by developmental and physical abnormalities. Developmental abnormalities in dentition are frequently observed in various patients with craniofacial syndromes, however there are a few reports regarding dental management in patients with WS. The aim of the present report is to describe the case of a 6-year-old child with characteristic facial features of WS with remarkable orofacial findings and the ensuing dental management. An intraoral examination revealed a mixed dentition period, with tooth agenesis and caries requiring treatment such as extraction, restoration and fluoride application. The dental treatment was carried out under local anesthesia and was completed successfully. Since then clinical and radiographic evaluations have been conducted periodically. 
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spelling Orofacial Findings and Dental Management of a Child with Williams SyndromeManejo e características orofaciais de crianças portadoras da síndrome de WilliamsWilliams syndromeAgenesisChildrenPediatric DentistrySíndrome de WilliamsAgenesiaCriançasWilliams syndrome (WS) is a multisystem, congenital and panethnic disorder characterized by developmental and physical abnormalities. Developmental abnormalities in dentition are frequently observed in various patients with craniofacial syndromes, however there are a few reports regarding dental management in patients with WS. The aim of the present report is to describe the case of a 6-year-old child with characteristic facial features of WS with remarkable orofacial findings and the ensuing dental management. An intraoral examination revealed a mixed dentition period, with tooth agenesis and caries requiring treatment such as extraction, restoration and fluoride application. The dental treatment was carried out under local anesthesia and was completed successfully. Since then clinical and radiographic evaluations have been conducted periodically. A síndrome de Williams (SW) é uma doença congênita e pan-étnica caracterizada por anomalias do desenvolvimento e físicos. O desenvolvimento de anormalidades em dentição são frequentemente observadas em vários pacientes com síndromes craniofaciais, no entanto, existem poucos relatos sobre o manejo odontológico de pacientes com SW. O objetivo do presente relato é descrever as condutas de atendimento do caso de uma criança de 6 anos de idade, com traços faciais característicos de SW com características orofaciais relacionadas à SW. O exame bucal revelou uma dentição mista, com agenesia dentária e cáries que exigem tratamento, como extração, restauração e aplicação de flúor. O tratamento odontológico foi realizado sob anestesia local e foi concluída com êxito. Desde então, as avaliações clínicas e radiográficas têm sido realizadas periodicamente. EDIPUCRS - Editora Universitária da PUCRS2016-11-17info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionPeer-reviewed Articleapplication/pdfhttps://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/1777010.15448/http://dx.doi.org/10.15448/1980-6523.2016.1.17770Revista Odonto Ciência; Vol. 31 No. 1 (2016); 41-44Revista Odonto Ciência; v. 31 n. 1 (2016); 41-441980-65230102-946010.15448/1980-6523.2016.1reponame:Revista odonto ciência (Online)instname:Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS)instacron:PUC_RSenghttps://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/17770/14992Copyright (c) 2016 Revista Odonto Ciênciainfo:eu-repo/semantics/openAccessPereira, LucianaSoares, Daniela NovaesPedro, Rafael de LimaFidalgo, Tatiana Kelly da SilvaCosta, Marcelo CastroCastro, Gloria Fernanda Barbosa de Araújo2016-11-17T17:57:46Zoai:ojs.revistaseletronicas.pucrs.br:article/17770Revistahttps://revistaseletronicas.pucrs.br/ojs/index.php/foPRIhttps://revistaseletronicas.pucrs.br/ojs/index.php/fo/oai||odontociencia@pucrs.br1980-65230102-9460opendoar:2016-11-17T17:57:46Revista odonto ciência (Online) - Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS)false
dc.title.none.fl_str_mv Orofacial Findings and Dental Management of a Child with Williams Syndrome
Manejo e características orofaciais de crianças portadoras da síndrome de Williams
title Orofacial Findings and Dental Management of a Child with Williams Syndrome
spellingShingle Orofacial Findings and Dental Management of a Child with Williams Syndrome
Pereira, Luciana
Williams syndrome
Agenesis
Children
Pediatric Dentistry
Síndrome de Williams
Agenesia
Crianças
title_short Orofacial Findings and Dental Management of a Child with Williams Syndrome
title_full Orofacial Findings and Dental Management of a Child with Williams Syndrome
title_fullStr Orofacial Findings and Dental Management of a Child with Williams Syndrome
title_full_unstemmed Orofacial Findings and Dental Management of a Child with Williams Syndrome
title_sort Orofacial Findings and Dental Management of a Child with Williams Syndrome
author Pereira, Luciana
author_facet Pereira, Luciana
Soares, Daniela Novaes
Pedro, Rafael de Lima
Fidalgo, Tatiana Kelly da Silva
Costa, Marcelo Castro
Castro, Gloria Fernanda Barbosa de Araújo
author_role author
author2 Soares, Daniela Novaes
Pedro, Rafael de Lima
Fidalgo, Tatiana Kelly da Silva
Costa, Marcelo Castro
Castro, Gloria Fernanda Barbosa de Araújo
author2_role author
author
author
author
author
dc.contributor.author.fl_str_mv Pereira, Luciana
Soares, Daniela Novaes
Pedro, Rafael de Lima
Fidalgo, Tatiana Kelly da Silva
Costa, Marcelo Castro
Castro, Gloria Fernanda Barbosa de Araújo
dc.subject.por.fl_str_mv Williams syndrome
Agenesis
Children
Pediatric Dentistry
Síndrome de Williams
Agenesia
Crianças
topic Williams syndrome
Agenesis
Children
Pediatric Dentistry
Síndrome de Williams
Agenesia
Crianças
description Williams syndrome (WS) is a multisystem, congenital and panethnic disorder characterized by developmental and physical abnormalities. Developmental abnormalities in dentition are frequently observed in various patients with craniofacial syndromes, however there are a few reports regarding dental management in patients with WS. The aim of the present report is to describe the case of a 6-year-old child with characteristic facial features of WS with remarkable orofacial findings and the ensuing dental management. An intraoral examination revealed a mixed dentition period, with tooth agenesis and caries requiring treatment such as extraction, restoration and fluoride application. The dental treatment was carried out under local anesthesia and was completed successfully. Since then clinical and radiographic evaluations have been conducted periodically. 
publishDate 2016
dc.date.none.fl_str_mv 2016-11-17
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
Peer-reviewed Article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/17770
10.15448/http://dx.doi.org/10.15448/1980-6523.2016.1.17770
url https://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/17770
identifier_str_mv 10.15448/http://dx.doi.org/10.15448/1980-6523.2016.1.17770
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv https://revistaseletronicas.pucrs.br/ojs/index.php/fo/article/view/17770/14992
dc.rights.driver.fl_str_mv Copyright (c) 2016 Revista Odonto Ciência
info:eu-repo/semantics/openAccess
rights_invalid_str_mv Copyright (c) 2016 Revista Odonto Ciência
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv EDIPUCRS - Editora Universitária da PUCRS
publisher.none.fl_str_mv EDIPUCRS - Editora Universitária da PUCRS
dc.source.none.fl_str_mv Revista Odonto Ciência; Vol. 31 No. 1 (2016); 41-44
Revista Odonto Ciência; v. 31 n. 1 (2016); 41-44
1980-6523
0102-9460
10.15448/1980-6523.2016.1
reponame:Revista odonto ciência (Online)
instname:Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS)
instacron:PUC_RS
instname_str Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS)
instacron_str PUC_RS
institution PUC_RS
reponame_str Revista odonto ciência (Online)
collection Revista odonto ciência (Online)
repository.name.fl_str_mv Revista odonto ciência (Online) - Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS)
repository.mail.fl_str_mv ||odontociencia@pucrs.br
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