Coexistence of pheochromocytoma and renal artery stenosis in a pediatric patient with hypertension

• Autor(a) principal: Serras,Inês
• Data de Publicação: 2018
• Outros Autores: Baptista,Rute Baeta, Francisco,Telma, Casimiro,Anaxore, Lito,David, Alves,Rui, Abranches,Margarida
• Tipo de documento: Relatório
• Idioma: eng
• Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
• Texto Completo: http://scielo.pt/scielo.php?script=sci_arttext&pid=S0872-01692018000100013
• topic: Child; hypertension; pheochromocytoma; posterior reversible encephalopathy syndrome; renal artery stenosis

Pheochromocytoma and renal artery stenosis are surgically treatable causes of hypertension. Although rare, the coexistence of pheochromocytoma and renal artery stenosis has been described in case reports. Common pathophysiological mechanisms other than extrinsic compression may be involved in this association, such as catecholamine-induced vasospasm. The early recognition of the association of pheochromocytoma with renal artery stenosis is essential for appropriate treatment planning. We present the case of a previously healthy tenyear-old boy who presented with hypertensive encephalopathy, tachycardia and diaphoresis. Hypertension was found to be secondary to a catecholamine-producing tumor associated with coexisting renal artery stenosis. Hypertension resolved a few months after successful pheochromocytoma excision, without renal artery revascularization