IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis

Detalhes bibliográficos
Autor(a) principal: Proença, AL
Data de Publicação: 2019
Outros Autores: Lopes Dias, J
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10400.17/4182
Resumo: IgG4 related disease (IgG4 RD) is a newly recognized entity that includes a group of immune-mediated fibro-inflammatory conditions. It can affect a wide range of organs, producing a broad spectrum of presentations. The selection of imaging modality is based on patient symptoms and the organs under evaluation. The diagnosis is based on a combination of radiological findings, serum IgG4 elevation levels, histopathological features, association with other IgG4-related diseases and response to steroids. We report a rare case of an IgG4-related sclerosing mesenteritis in a man who presented with an incidental right lower quadrant mesenteric mass and was unsuccessfully treated with corticoids. Isolated mesentery involvement is a rare presentation of IgG4-related disease and only few cases were reported in literature
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spelling IgG4-Related Disease Presenting as Mass-Like Sclerosing MesenteritisDoença Relacionada à IgG4 Apresentando-se como Massa de Mesenterite EsclerosanteIgG4-related diseaseSclerosing mesenteritisComputed tomographyHCC IMAHSJ IMAIgG4 related disease (IgG4 RD) is a newly recognized entity that includes a group of immune-mediated fibro-inflammatory conditions. It can affect a wide range of organs, producing a broad spectrum of presentations. The selection of imaging modality is based on patient symptoms and the organs under evaluation. The diagnosis is based on a combination of radiological findings, serum IgG4 elevation levels, histopathological features, association with other IgG4-related diseases and response to steroids. We report a rare case of an IgG4-related sclerosing mesenteritis in a man who presented with an incidental right lower quadrant mesenteric mass and was unsuccessfully treated with corticoids. Isolated mesentery involvement is a rare presentation of IgG4-related disease and only few cases were reported in literatureSociedade Portuguesa de Radiologia e Medicina NuclearRepositório do Centro Hospitalar Universitário de Lisboa Central, EPEProença, ALLopes Dias, J2022-08-04T11:11:05Z20192019-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/4182engActa Radiol Port. 2019; 31(3):25-27info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-10T09:45:43Zoai:repositorio.chlc.min-saude.pt:10400.17/4182Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:21:30.935653Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
Doença Relacionada à IgG4 Apresentando-se como Massa de Mesenterite Esclerosante
title IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
spellingShingle IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
Proença, AL
IgG4-related disease
Sclerosing mesenteritis
Computed tomography
HCC IMA
HSJ IMA
title_short IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
title_full IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
title_fullStr IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
title_full_unstemmed IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
title_sort IgG4-Related Disease Presenting as Mass-Like Sclerosing Mesenteritis
author Proença, AL
author_facet Proença, AL
Lopes Dias, J
author_role author
author2 Lopes Dias, J
author2_role author
dc.contributor.none.fl_str_mv Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE
dc.contributor.author.fl_str_mv Proença, AL
Lopes Dias, J
dc.subject.por.fl_str_mv IgG4-related disease
Sclerosing mesenteritis
Computed tomography
HCC IMA
HSJ IMA
topic IgG4-related disease
Sclerosing mesenteritis
Computed tomography
HCC IMA
HSJ IMA
description IgG4 related disease (IgG4 RD) is a newly recognized entity that includes a group of immune-mediated fibro-inflammatory conditions. It can affect a wide range of organs, producing a broad spectrum of presentations. The selection of imaging modality is based on patient symptoms and the organs under evaluation. The diagnosis is based on a combination of radiological findings, serum IgG4 elevation levels, histopathological features, association with other IgG4-related diseases and response to steroids. We report a rare case of an IgG4-related sclerosing mesenteritis in a man who presented with an incidental right lower quadrant mesenteric mass and was unsuccessfully treated with corticoids. Isolated mesentery involvement is a rare presentation of IgG4-related disease and only few cases were reported in literature
publishDate 2019
dc.date.none.fl_str_mv 2019
2019-01-01T00:00:00Z
2022-08-04T11:11:05Z
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.17/4182
url http://hdl.handle.net/10400.17/4182
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv Acta Radiol Port. 2019; 31(3):25-27
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Sociedade Portuguesa de Radiologia e Medicina Nuclear
publisher.none.fl_str_mv Sociedade Portuguesa de Radiologia e Medicina Nuclear
dc.source.none.fl_str_mv reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
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