Primary tracheobronchial amyloidosis: Two case reports
Autor(a) principal: | |
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Data de Publicação: | 2008 |
Outros Autores: | , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007 |
Resumo: | Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features. The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed. |
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Primary tracheobronchial amyloidosis: Two case reportsAmyloidosistracheobronchialPrimary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features. The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed.Sociedade Portuguesa de Pneumologia2008-07-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articletext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007Revista Portuguesa de Pneumologia v.14 n.4 2008reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttp://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007Saleiro,SandraHespanhol,Venceslau PintoMagalhães,Adrianainfo:eu-repo/semantics/openAccess2024-02-06T17:09:45Zoai:scielo:S0873-21592008000400007Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-20T02:21:36.774795Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Primary tracheobronchial amyloidosis: Two case reports |
title |
Primary tracheobronchial amyloidosis: Two case reports |
spellingShingle |
Primary tracheobronchial amyloidosis: Two case reports Saleiro,Sandra Amyloidosis tracheobronchial |
title_short |
Primary tracheobronchial amyloidosis: Two case reports |
title_full |
Primary tracheobronchial amyloidosis: Two case reports |
title_fullStr |
Primary tracheobronchial amyloidosis: Two case reports |
title_full_unstemmed |
Primary tracheobronchial amyloidosis: Two case reports |
title_sort |
Primary tracheobronchial amyloidosis: Two case reports |
author |
Saleiro,Sandra |
author_facet |
Saleiro,Sandra Hespanhol,Venceslau Pinto Magalhães,Adriana |
author_role |
author |
author2 |
Hespanhol,Venceslau Pinto Magalhães,Adriana |
author2_role |
author author |
dc.contributor.author.fl_str_mv |
Saleiro,Sandra Hespanhol,Venceslau Pinto Magalhães,Adriana |
dc.subject.por.fl_str_mv |
Amyloidosis tracheobronchial |
topic |
Amyloidosis tracheobronchial |
description |
Primary tracheobronchial amyloidosis is a form of respiratory amyloidosis, characterised by insoluble amyloid fibril proteins deposits along the airways wall. It is an uncommon disease, requiring a tissue sample to establish the definite diagnosis based on specific pathological features. The authors report two cases of tracheobronchial amyloidosis, describing their symptoms and the diagnostic and therapeutic procedures that were performed. |
publishDate |
2008 |
dc.date.none.fl_str_mv |
2008-07-01 |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007 |
url |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
http://scielo.pt/scielo.php?script=sci_arttext&pid=S0873-21592008000400007 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
text/html |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Pneumologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Pneumologia |
dc.source.none.fl_str_mv |
Revista Portuguesa de Pneumologia v.14 n.4 2008 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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|
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1799137301678260224 |