Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.

Detalhes bibliográficos
Autor(a) principal: Gomes, H
Data de Publicação: 1997
Outros Autores: Lebre, R, Fonseca, J, Borralho, P, Duarte, R
Tipo de documento: Artigo
Idioma: por
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506
Resumo: Von Recklinghausen's Neurofibromatosis is an autosomal dominant disease of variable manifestations. Association with gastrointestinal and hepatobiliary tumours is well documented, most of them being benign neurofibromas. Other tumours, such as leiomyomas, sarcomas, ganglioneuromas and carcinoids are less frequent. Much rarer is the development of epithelial malignancies and an ontogenic relation is not clear. The authors reports a case of adenocarcinoma of Vater's Ampulla and duodenal neurofibromas, in a patient with Von Recklinghausen's disease, presenting obstructive jaundice.
id RCAP_1df479eaf0c98a6d87377011924ac4ff
oai_identifier_str oai:ojs.www.actamedicaportuguesa.com:article/2506
network_acronym_str RCAP
network_name_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository_id_str 7160
spelling Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.Adenocarcinoma da ampola de Vater associado com neurofibromatose de von Recklinghausen.Von Recklinghausen's Neurofibromatosis is an autosomal dominant disease of variable manifestations. Association with gastrointestinal and hepatobiliary tumours is well documented, most of them being benign neurofibromas. Other tumours, such as leiomyomas, sarcomas, ganglioneuromas and carcinoids are less frequent. Much rarer is the development of epithelial malignancies and an ontogenic relation is not clear. The authors reports a case of adenocarcinoma of Vater's Ampulla and duodenal neurofibromas, in a patient with Von Recklinghausen's disease, presenting obstructive jaundice.Von Recklinghausen's Neurofibromatosis is an autosomal dominant disease of variable manifestations. Association with gastrointestinal and hepatobiliary tumours is well documented, most of them being benign neurofibromas. Other tumours, such as leiomyomas, sarcomas, ganglioneuromas and carcinoids are less frequent. Much rarer is the development of epithelial malignancies and an ontogenic relation is not clear. The authors reports a case of adenocarcinoma of Vater's Ampulla and duodenal neurofibromas, in a patient with Von Recklinghausen's disease, presenting obstructive jaundice.Ordem dos Médicos1997-12-01info:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506oai:ojs.www.actamedicaportuguesa.com:article/2506Acta Médica Portuguesa; Vol. 10 No. 11 (1997): Novembro; 832-6Acta Médica Portuguesa; Vol. 10 N.º 11 (1997): Novembro; 832-61646-07580870-399Xreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPporhttps://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506/1920Gomes, HLebre, RFonseca, JBorralho, PDuarte, Rinfo:eu-repo/semantics/openAccess2022-12-20T11:00:41Zoai:ojs.www.actamedicaportuguesa.com:article/2506Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:17:47.678808Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
Adenocarcinoma da ampola de Vater associado com neurofibromatose de von Recklinghausen.
title Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
spellingShingle Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
Gomes, H
title_short Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
title_full Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
title_fullStr Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
title_full_unstemmed Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
title_sort Adenocarcinoma of the Vater's ampulla associated with Von Recklinghausen's neurofibromatosis.
author Gomes, H
author_facet Gomes, H
Lebre, R
Fonseca, J
Borralho, P
Duarte, R
author_role author
author2 Lebre, R
Fonseca, J
Borralho, P
Duarte, R
author2_role author
author
author
author
dc.contributor.author.fl_str_mv Gomes, H
Lebre, R
Fonseca, J
Borralho, P
Duarte, R
description Von Recklinghausen's Neurofibromatosis is an autosomal dominant disease of variable manifestations. Association with gastrointestinal and hepatobiliary tumours is well documented, most of them being benign neurofibromas. Other tumours, such as leiomyomas, sarcomas, ganglioneuromas and carcinoids are less frequent. Much rarer is the development of epithelial malignancies and an ontogenic relation is not clear. The authors reports a case of adenocarcinoma of Vater's Ampulla and duodenal neurofibromas, in a patient with Von Recklinghausen's disease, presenting obstructive jaundice.
publishDate 1997
dc.date.none.fl_str_mv 1997-12-01
dc.type.status.fl_str_mv info:eu-repo/semantics/publishedVersion
dc.type.driver.fl_str_mv info:eu-repo/semantics/article
format article
status_str publishedVersion
dc.identifier.uri.fl_str_mv https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506
oai:ojs.www.actamedicaportuguesa.com:article/2506
url https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506
identifier_str_mv oai:ojs.www.actamedicaportuguesa.com:article/2506
dc.language.iso.fl_str_mv por
language por
dc.relation.none.fl_str_mv https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506
https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/2506/1920
dc.rights.driver.fl_str_mv info:eu-repo/semantics/openAccess
eu_rights_str_mv openAccess
dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Ordem dos Médicos
publisher.none.fl_str_mv Ordem dos Médicos
dc.source.none.fl_str_mv Acta Médica Portuguesa; Vol. 10 No. 11 (1997): Novembro; 832-6
Acta Médica Portuguesa; Vol. 10 N.º 11 (1997): Novembro; 832-6
1646-0758
0870-399X
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron:RCAAP
instname_str Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
instacron_str RCAAP
institution RCAAP
reponame_str Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
collection Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
repository.name.fl_str_mv Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação
repository.mail.fl_str_mv
_version_ 1799130630786646016

Registros relacionados