Multiple and Superimposed Mongolian Spots in a Caucasian Child
Autor(a) principal: | |
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Data de Publicação: | 2018 |
Outros Autores: | , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | https://doi.org/10.29021/spdv.75.3.820 |
Resumo: | Mongolian spots are common birthmarks in newborns and their incidence and prevalence vary considerably between races, being the lowest in caucasian infants. Although traditionally regarded as benign, some reports suggested that extensive and multiple mongolian spots at aberrant locations and persistent beyond early childhood may co-exist with inborn errors of metabolism. However, this association is not well established. Besides, very few cases in literature reported a particular type of superimposed mongolian spots, whose physiopathological mechanism and clinical significance are unknown. We report a case of a 7-months-old caucasian male infant with multiple, extensive and progressive mongolian spots and also a superimposed mongolian spot located on the right hip. |
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Multiple and Superimposed Mongolian Spots in a Caucasian ChildManchas Mongólicas Múltiplas e Sobrepostas numa Criança CaucasianaEuropean Continental Ancestry GroupInfantNevusPigmentedMongolian SpotGrupo de Ascendência do Continente EuropeuLactenteMancha MongólicaNevo PigmentadoMongolian spots are common birthmarks in newborns and their incidence and prevalence vary considerably between races, being the lowest in caucasian infants. Although traditionally regarded as benign, some reports suggested that extensive and multiple mongolian spots at aberrant locations and persistent beyond early childhood may co-exist with inborn errors of metabolism. However, this association is not well established. Besides, very few cases in literature reported a particular type of superimposed mongolian spots, whose physiopathological mechanism and clinical significance are unknown. We report a case of a 7-months-old caucasian male infant with multiple, extensive and progressive mongolian spots and also a superimposed mongolian spot located on the right hip.A mancha mongólica é uma forma de melanose dérmica comum em recém- nascidos, tendo uma incidência e prevalência variável consoante a raça, sendo menos frequente em crianças caucasianas. Apesar de tradicionalmente interpretadas como benignas, várias publicações têm vindo a sugerir que manchas mongólicas extensas, múltiplas, presentes em locais atípicos e persistentes ao longo da primeira infância podem estar associadas a algumas doenças metabólicas. Contudo, esta associação não está ainda bem esclarecida. Por outro lado, casos pontuais reportados na literatura têm descrito um tipo particular de mancha mongólica sobreposta a outra de pigmentação diferente, não sendo conhecido o mecanismo fisiopatológico e a relevância clínica deste achado. Os autores reportam o caso de um rapaz caucasiano com 7 meses de idade com manchas mongólicas múltiplas, extensas, de agravamento progressivo nos primeiros meses de vida, uma das quais mais pigmentada sobreposta a outra, localizada na anca direita.Sociedade Portuguesa de Dermatologia e Venereologia2018-01-22T00:00:00Zjournal articleinfo:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionapplication/pdfhttps://doi.org/10.29021/spdv.75.3.820oai:ojs.revista.spdv.com.pt:article/820Journal of the Portuguese Society of Dermatology and Venereology; Vol 75 No 3 (2017): Julho - Setembro; 293-296Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 75 n. 3 (2017): Julho - Setembro; 293-2962182-24092182-2395reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAPenghttps://revista.spdv.com.pt/index.php/spdv/article/view/820https://doi.org/10.29021/spdv.75.3.820https://revista.spdv.com.pt/index.php/spdv/article/view/820/515António, Ana MartaCostin, AdelinaCunha, Henriquetainfo:eu-repo/semantics/openAccess2022-10-06T12:35:04Zoai:ojs.revista.spdv.com.pt:article/820Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T16:11:04.056086Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Multiple and Superimposed Mongolian Spots in a Caucasian Child Manchas Mongólicas Múltiplas e Sobrepostas numa Criança Caucasiana |
title |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
spellingShingle |
Multiple and Superimposed Mongolian Spots in a Caucasian Child António, Ana Marta European Continental Ancestry Group Infant Nevus Pigmented Mongolian Spot Grupo de Ascendência do Continente Europeu Lactente Mancha Mongólica Nevo Pigmentado |
title_short |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
title_full |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
title_fullStr |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
title_full_unstemmed |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
title_sort |
Multiple and Superimposed Mongolian Spots in a Caucasian Child |
author |
António, Ana Marta |
author_facet |
António, Ana Marta Costin, Adelina Cunha, Henriqueta |
author_role |
author |
author2 |
Costin, Adelina Cunha, Henriqueta |
author2_role |
author author |
dc.contributor.author.fl_str_mv |
António, Ana Marta Costin, Adelina Cunha, Henriqueta |
dc.subject.por.fl_str_mv |
European Continental Ancestry Group Infant Nevus Pigmented Mongolian Spot Grupo de Ascendência do Continente Europeu Lactente Mancha Mongólica Nevo Pigmentado |
topic |
European Continental Ancestry Group Infant Nevus Pigmented Mongolian Spot Grupo de Ascendência do Continente Europeu Lactente Mancha Mongólica Nevo Pigmentado |
description |
Mongolian spots are common birthmarks in newborns and their incidence and prevalence vary considerably between races, being the lowest in caucasian infants. Although traditionally regarded as benign, some reports suggested that extensive and multiple mongolian spots at aberrant locations and persistent beyond early childhood may co-exist with inborn errors of metabolism. However, this association is not well established. Besides, very few cases in literature reported a particular type of superimposed mongolian spots, whose physiopathological mechanism and clinical significance are unknown. We report a case of a 7-months-old caucasian male infant with multiple, extensive and progressive mongolian spots and also a superimposed mongolian spot located on the right hip. |
publishDate |
2018 |
dc.date.none.fl_str_mv |
2018-01-22T00:00:00Z |
dc.type.driver.fl_str_mv |
journal article info:eu-repo/semantics/article |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
https://doi.org/10.29021/spdv.75.3.820 oai:ojs.revista.spdv.com.pt:article/820 |
url |
https://doi.org/10.29021/spdv.75.3.820 |
identifier_str_mv |
oai:ojs.revista.spdv.com.pt:article/820 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
https://revista.spdv.com.pt/index.php/spdv/article/view/820 https://doi.org/10.29021/spdv.75.3.820 https://revista.spdv.com.pt/index.php/spdv/article/view/820/515 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Dermatologia e Venereologia |
dc.source.none.fl_str_mv |
Journal of the Portuguese Society of Dermatology and Venereology; Vol 75 No 3 (2017): Julho - Setembro; 293-296 Revista da Sociedade Portuguesa de Dermatologia e Venereologia; v. 75 n. 3 (2017): Julho - Setembro; 293-296 2182-2409 2182-2395 reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
instname_str |
Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
collection |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
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1799130566723895296 |