Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation
Autor(a) principal: | |
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Data de Publicação: | 2022 |
Outros Autores: | , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.17/4035 |
Resumo: | Hemophilia B is a coagulation disorder characterized by a deficiency of clotting factor IX. Women are often heterozygous carriers of the disease, however if their clotting factor levels are less than 60%, they may have an increased bleeding tendency. This is even higher if levels are under 40%. We presente a case of a 14-year-old female, with mild hemofilia B (hemofilia B carrier with factor IX level < 40%) who underwent a major surgery: a posterior spinal instrumentation from D6 to L1. The perioperative management was discussed, including the perioperative administration of blood products and coagulation adjuncts. This was coordinated by a multidisciplinar team (orthopedists, anesthesiologists, hematologists and nurses) to provide the best perioperative care and follow-up. Close collaboration and communication among/with the team members and the patient/family was vital throughout. |
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Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior InstrumentationAbordagem Perioperatória de uma Adolescente com Hemofilia B Submetida a Instrumentação Posterior da Coluna DorsolombarCHLC ANSAdolescentHemophilia BFactor IXSurgical Procedures, OperativeHemophilia B is a coagulation disorder characterized by a deficiency of clotting factor IX. Women are often heterozygous carriers of the disease, however if their clotting factor levels are less than 60%, they may have an increased bleeding tendency. This is even higher if levels are under 40%. We presente a case of a 14-year-old female, with mild hemofilia B (hemofilia B carrier with factor IX level < 40%) who underwent a major surgery: a posterior spinal instrumentation from D6 to L1. The perioperative management was discussed, including the perioperative administration of blood products and coagulation adjuncts. This was coordinated by a multidisciplinar team (orthopedists, anesthesiologists, hematologists and nurses) to provide the best perioperative care and follow-up. Close collaboration and communication among/with the team members and the patient/family was vital throughout.Sociedade Portuguesa de AnestesiologiaRepositório do Centro Hospitalar Universitário de Lisboa Central, EPEMartinho, LCâmara, LBatalha, SRodrigues, JCarioca, FMarques, J2022-04-06T12:23:29Z20222022-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.17/4035engRev Soc Port Anestesiol 2022;31(1):16-18https://dx.org/10.25751/rspa.25544info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-10T09:45:00Zoai:repositorio.chlc.min-saude.pt:10400.17/4035Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:21:20.562874Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation Abordagem Perioperatória de uma Adolescente com Hemofilia B Submetida a Instrumentação Posterior da Coluna Dorsolombar |
title |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
spellingShingle |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation Martinho, L CHLC ANS Adolescent Hemophilia B Factor IX Surgical Procedures, Operative |
title_short |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
title_full |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
title_fullStr |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
title_full_unstemmed |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
title_sort |
Perioperative Management of a Girl with Hemophilia B Undergoing Dorsolumbar Spine Posterior Instrumentation |
author |
Martinho, L |
author_facet |
Martinho, L Câmara, L Batalha, S Rodrigues, J Carioca, F Marques, J |
author_role |
author |
author2 |
Câmara, L Batalha, S Rodrigues, J Carioca, F Marques, J |
author2_role |
author author author author author |
dc.contributor.none.fl_str_mv |
Repositório do Centro Hospitalar Universitário de Lisboa Central, EPE |
dc.contributor.author.fl_str_mv |
Martinho, L Câmara, L Batalha, S Rodrigues, J Carioca, F Marques, J |
dc.subject.por.fl_str_mv |
CHLC ANS Adolescent Hemophilia B Factor IX Surgical Procedures, Operative |
topic |
CHLC ANS Adolescent Hemophilia B Factor IX Surgical Procedures, Operative |
description |
Hemophilia B is a coagulation disorder characterized by a deficiency of clotting factor IX. Women are often heterozygous carriers of the disease, however if their clotting factor levels are less than 60%, they may have an increased bleeding tendency. This is even higher if levels are under 40%. We presente a case of a 14-year-old female, with mild hemofilia B (hemofilia B carrier with factor IX level < 40%) who underwent a major surgery: a posterior spinal instrumentation from D6 to L1. The perioperative management was discussed, including the perioperative administration of blood products and coagulation adjuncts. This was coordinated by a multidisciplinar team (orthopedists, anesthesiologists, hematologists and nurses) to provide the best perioperative care and follow-up. Close collaboration and communication among/with the team members and the patient/family was vital throughout. |
publishDate |
2022 |
dc.date.none.fl_str_mv |
2022-04-06T12:23:29Z 2022 2022-01-01T00:00:00Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.17/4035 |
url |
http://hdl.handle.net/10400.17/4035 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
Rev Soc Port Anestesiol 2022;31(1):16-18 https://dx.org/10.25751/rspa.25544 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Sociedade Portuguesa de Anestesiologia |
publisher.none.fl_str_mv |
Sociedade Portuguesa de Anestesiologia |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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1799131309304446976 |