Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management
Autor(a) principal: | |
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Data de Publicação: | 2014 |
Outros Autores: | , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.22/5327 |
Resumo: | Among aminoacidopathies, phenylketonuria (PKU) is the most prevalent one. Early diagnosis in the neonatal period with a prompt nutritional therapy (low natural-protein and phenylalanine diet, supplemented with phenylalanine-free amino acid mixtures and special low-protein foods) remains the mainstay of the treatment. Data considering nutrient contents of cooked dishes is lacking. In this study, fourteen dishes specifically prepared for PKU individuals were analysed, regarding the lipid profile and iron and zinc contents. These dishes are poor sources of essential nutrients like Fe, Zn or n-3 fatty acids, reinforcing the need for adequate supplementation to cover individual patients’ needs. This study can contribute to a more accurate adjustment of PKU diets and supplementation in order to prevent eventual nutritional deficiencies. This study contributes to a better understanding of nutrient intake from PKU patients’ meals, showing the need for dietary supplementation. |
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Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary managementAmong aminoacidopathies, phenylketonuria (PKU) is the most prevalent one. Early diagnosis in the neonatal period with a prompt nutritional therapy (low natural-protein and phenylalanine diet, supplemented with phenylalanine-free amino acid mixtures and special low-protein foods) remains the mainstay of the treatment. Data considering nutrient contents of cooked dishes is lacking. In this study, fourteen dishes specifically prepared for PKU individuals were analysed, regarding the lipid profile and iron and zinc contents. These dishes are poor sources of essential nutrients like Fe, Zn or n-3 fatty acids, reinforcing the need for adequate supplementation to cover individual patients’ needs. This study can contribute to a more accurate adjustment of PKU diets and supplementation in order to prevent eventual nutritional deficiencies. This study contributes to a better understanding of nutrient intake from PKU patients’ meals, showing the need for dietary supplementation.The Royal Society of ChemistryRepositório Científico do Instituto Politécnico do PortoPimentel, Filipa B.Alves, Rita C.Oliva-Teles, M. TeresaCosta, Anabela S. G.Fernandes, Telmo J. R.Almeida, Manuela F.Torres, DuarteDelerue-Matos, CristinaOliveira, M. Beatriz P. P.2015-01-07T11:59:18Z2014-12-012014-12-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.22/5327eng10.1039/c4fo00555dinfo:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-03-13T12:45:22Zoai:recipp.ipp.pt:10400.22/5327Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T17:26:00.009398Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
title |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
spellingShingle |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management Pimentel, Filipa B. |
title_short |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
title_full |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
title_fullStr |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
title_full_unstemmed |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
title_sort |
Targeting specific nutrient deficiencies in proteinrestricted diets: some practical facts in PKU dietary management |
author |
Pimentel, Filipa B. |
author_facet |
Pimentel, Filipa B. Alves, Rita C. Oliva-Teles, M. Teresa Costa, Anabela S. G. Fernandes, Telmo J. R. Almeida, Manuela F. Torres, Duarte Delerue-Matos, Cristina Oliveira, M. Beatriz P. P. |
author_role |
author |
author2 |
Alves, Rita C. Oliva-Teles, M. Teresa Costa, Anabela S. G. Fernandes, Telmo J. R. Almeida, Manuela F. Torres, Duarte Delerue-Matos, Cristina Oliveira, M. Beatriz P. P. |
author2_role |
author author author author author author author author |
dc.contributor.none.fl_str_mv |
Repositório Científico do Instituto Politécnico do Porto |
dc.contributor.author.fl_str_mv |
Pimentel, Filipa B. Alves, Rita C. Oliva-Teles, M. Teresa Costa, Anabela S. G. Fernandes, Telmo J. R. Almeida, Manuela F. Torres, Duarte Delerue-Matos, Cristina Oliveira, M. Beatriz P. P. |
description |
Among aminoacidopathies, phenylketonuria (PKU) is the most prevalent one. Early diagnosis in the neonatal period with a prompt nutritional therapy (low natural-protein and phenylalanine diet, supplemented with phenylalanine-free amino acid mixtures and special low-protein foods) remains the mainstay of the treatment. Data considering nutrient contents of cooked dishes is lacking. In this study, fourteen dishes specifically prepared for PKU individuals were analysed, regarding the lipid profile and iron and zinc contents. These dishes are poor sources of essential nutrients like Fe, Zn or n-3 fatty acids, reinforcing the need for adequate supplementation to cover individual patients’ needs. This study can contribute to a more accurate adjustment of PKU diets and supplementation in order to prevent eventual nutritional deficiencies. This study contributes to a better understanding of nutrient intake from PKU patients’ meals, showing the need for dietary supplementation. |
publishDate |
2014 |
dc.date.none.fl_str_mv |
2014-12-01 2014-12-01T00:00:00Z 2015-01-07T11:59:18Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.22/5327 |
url |
http://hdl.handle.net/10400.22/5327 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
10.1039/c4fo00555d |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
The Royal Society of Chemistry |
publisher.none.fl_str_mv |
The Royal Society of Chemistry |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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RCAAP |
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RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
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1799131354682621952 |