Perioral pigmentation: What is your diagnosis?

Detalhes bibliográficos
Autor(a) principal: Santos, P.
Data de Publicação: 2008
Outros Autores: Neto, C., Machado, S., Lobo, I., Soares, J., Selores, M.
Tipo de documento: Artigo
Idioma: eng
Título da fonte: Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)
Texto Completo: http://hdl.handle.net/10400.16/1668
Resumo: Pigmented spots in the skin and mucosa (lentigines) can be found in various diseases called familial lentiginosis syndromes; Peutz-Jeghers syndrome (PJS) is one of them. It is characterized by the association of mucocutaneous melanin pigmentation and hamartomatous gastrointestinal polyps. Patients with PJS are at increased risk of intussusception and cancer development (gastrointestinal and non-gastrointestinal tumors). We present a 5-year-old girl with pigmented macules of perioral and perinasal skin, lips, and buccal mucosa and review lentiginoses and the surveillance of PJS.
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spelling Perioral pigmentation: What is your diagnosis?Pigmented spots in the skin and mucosa (lentigines) can be found in various diseases called familial lentiginosis syndromes; Peutz-Jeghers syndrome (PJS) is one of them. It is characterized by the association of mucocutaneous melanin pigmentation and hamartomatous gastrointestinal polyps. Patients with PJS are at increased risk of intussusception and cancer development (gastrointestinal and non-gastrointestinal tumors). We present a 5-year-old girl with pigmented macules of perioral and perinasal skin, lips, and buccal mucosa and review lentiginoses and the surveillance of PJS.University of CaliforniaRepositório Científico do Centro Hospitalar Universitário de Santo AntónioSantos, P.Neto, C.Machado, S.Lobo, I.Soares, J.Selores, M.2014-09-02T11:42:02Z20082008-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.16/1668engDermatology Online Journal 14 (11): 161087-2108info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-10-20T10:56:58Zoai:repositorio.chporto.pt:10400.16/1668Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T20:38:02.594906Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse
dc.title.none.fl_str_mv Perioral pigmentation: What is your diagnosis?
title Perioral pigmentation: What is your diagnosis?
spellingShingle Perioral pigmentation: What is your diagnosis?
Santos, P.
title_short Perioral pigmentation: What is your diagnosis?
title_full Perioral pigmentation: What is your diagnosis?
title_fullStr Perioral pigmentation: What is your diagnosis?
title_full_unstemmed Perioral pigmentation: What is your diagnosis?
title_sort Perioral pigmentation: What is your diagnosis?
author Santos, P.
author_facet Santos, P.
Neto, C.
Machado, S.
Lobo, I.
Soares, J.
Selores, M.
author_role author
author2 Neto, C.
Machado, S.
Lobo, I.
Soares, J.
Selores, M.
author2_role author
author
author
author
author
dc.contributor.none.fl_str_mv Repositório Científico do Centro Hospitalar Universitário de Santo António
dc.contributor.author.fl_str_mv Santos, P.
Neto, C.
Machado, S.
Lobo, I.
Soares, J.
Selores, M.
description Pigmented spots in the skin and mucosa (lentigines) can be found in various diseases called familial lentiginosis syndromes; Peutz-Jeghers syndrome (PJS) is one of them. It is characterized by the association of mucocutaneous melanin pigmentation and hamartomatous gastrointestinal polyps. Patients with PJS are at increased risk of intussusception and cancer development (gastrointestinal and non-gastrointestinal tumors). We present a 5-year-old girl with pigmented macules of perioral and perinasal skin, lips, and buccal mucosa and review lentiginoses and the surveillance of PJS.
publishDate 2008
dc.date.none.fl_str_mv 2008
2008-01-01T00:00:00Z
2014-09-02T11:42:02Z
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dc.identifier.uri.fl_str_mv http://hdl.handle.net/10400.16/1668
url http://hdl.handle.net/10400.16/1668
dc.language.iso.fl_str_mv eng
language eng
dc.relation.none.fl_str_mv Dermatology Online Journal 14 (11): 16
1087-2108
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dc.format.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv University of California
publisher.none.fl_str_mv University of California
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