Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding
Autor(a) principal: | |
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Data de Publicação: | 2018 |
Outros Autores: | , , , , , , , |
Tipo de documento: | Artigo |
Idioma: | eng |
Título da fonte: | Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
Texto Completo: | http://hdl.handle.net/10400.26/33553 |
Resumo: | Infantile hepatic haemangioma (IHH) is a rare vascular tumour that is potentially lethal due to its associated complications, including heart failure, hepatic failure, hypothyroidism and abdominal compartment syndrome. The authors report a case of an asymptomatic diffuse IHH in a newborn male, which was presented as an incidental finding at the time that the patient was diagnosed with pyloric stenosis. The patient was treated with increasing doses of propranolol that were well tolerated. With the regression of the IHH by the time that the patient reached one year of age, there was a significant imagiologic improvement. Because there is no consensus on the optimal approach for the treatment of liver tumours in newborns, it is important to adopt a systematic approach. After the diagnosis of diffuse IHH has been established, the decision to initiate treatment and the therapeutic of choice is often controversial. Regular follow-up is recommended to monitor possible complications. |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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7160 |
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Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal findingdiffuse infantile hepatic haemangiomachildcomplicationsinsuficiência hepáticapylori stenosisPortugalRegião Autónoma da Madeiraestenose pilóricacriançaInfantile hepatic haemangioma (IHH) is a rare vascular tumour that is potentially lethal due to its associated complications, including heart failure, hepatic failure, hypothyroidism and abdominal compartment syndrome. The authors report a case of an asymptomatic diffuse IHH in a newborn male, which was presented as an incidental finding at the time that the patient was diagnosed with pyloric stenosis. The patient was treated with increasing doses of propranolol that were well tolerated. With the regression of the IHH by the time that the patient reached one year of age, there was a significant imagiologic improvement. Because there is no consensus on the optimal approach for the treatment of liver tumours in newborns, it is important to adopt a systematic approach. After the diagnosis of diffuse IHH has been established, the decision to initiate treatment and the therapeutic of choice is often controversial. Regular follow-up is recommended to monitor possible complications.Oxford University Press.Repositório ComumRodrigues, AlexandraForno, AndreiaCosta, EditeBerenguer, AlbertoPilar, CarlaLoureiro, RuiRufino, DuarteBarros, AndreiaTeixeira, Filomena2020-10-13T16:00:51Z20182018-01-01T00:00:00Zinfo:eu-repo/semantics/publishedVersioninfo:eu-repo/semantics/articleapplication/pdfhttp://hdl.handle.net/10400.26/33553engOxford Medical Case Reports, 2018;8, 268–27010.1093/omcr/omy05410.1093/omcr/omy054info:eu-repo/semantics/openAccessreponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos)instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãoinstacron:RCAAP2023-11-10T02:17:00Zoai:comum.rcaap.pt:10400.26/33553Portal AgregadorONGhttps://www.rcaap.pt/oai/openaireopendoar:71602024-03-19T22:34:28.616197Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informaçãofalse |
dc.title.none.fl_str_mv |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
title |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
spellingShingle |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding Rodrigues, Alexandra diffuse infantile hepatic haemangioma child complications insuficiência hepática pylori stenosis Portugal Região Autónoma da Madeira estenose pilórica criança |
title_short |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
title_full |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
title_fullStr |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
title_full_unstemmed |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
title_sort |
Diffuse infantile hepatic haemangioma—how to manage an incidental but potentially lethal finding |
author |
Rodrigues, Alexandra |
author_facet |
Rodrigues, Alexandra Forno, Andreia Costa, Edite Berenguer, Alberto Pilar, Carla Loureiro, Rui Rufino, Duarte Barros, Andreia Teixeira, Filomena |
author_role |
author |
author2 |
Forno, Andreia Costa, Edite Berenguer, Alberto Pilar, Carla Loureiro, Rui Rufino, Duarte Barros, Andreia Teixeira, Filomena |
author2_role |
author author author author author author author author |
dc.contributor.none.fl_str_mv |
Repositório Comum |
dc.contributor.author.fl_str_mv |
Rodrigues, Alexandra Forno, Andreia Costa, Edite Berenguer, Alberto Pilar, Carla Loureiro, Rui Rufino, Duarte Barros, Andreia Teixeira, Filomena |
dc.subject.por.fl_str_mv |
diffuse infantile hepatic haemangioma child complications insuficiência hepática pylori stenosis Portugal Região Autónoma da Madeira estenose pilórica criança |
topic |
diffuse infantile hepatic haemangioma child complications insuficiência hepática pylori stenosis Portugal Região Autónoma da Madeira estenose pilórica criança |
description |
Infantile hepatic haemangioma (IHH) is a rare vascular tumour that is potentially lethal due to its associated complications, including heart failure, hepatic failure, hypothyroidism and abdominal compartment syndrome. The authors report a case of an asymptomatic diffuse IHH in a newborn male, which was presented as an incidental finding at the time that the patient was diagnosed with pyloric stenosis. The patient was treated with increasing doses of propranolol that were well tolerated. With the regression of the IHH by the time that the patient reached one year of age, there was a significant imagiologic improvement. Because there is no consensus on the optimal approach for the treatment of liver tumours in newborns, it is important to adopt a systematic approach. After the diagnosis of diffuse IHH has been established, the decision to initiate treatment and the therapeutic of choice is often controversial. Regular follow-up is recommended to monitor possible complications. |
publishDate |
2018 |
dc.date.none.fl_str_mv |
2018 2018-01-01T00:00:00Z 2020-10-13T16:00:51Z |
dc.type.status.fl_str_mv |
info:eu-repo/semantics/publishedVersion |
dc.type.driver.fl_str_mv |
info:eu-repo/semantics/article |
format |
article |
status_str |
publishedVersion |
dc.identifier.uri.fl_str_mv |
http://hdl.handle.net/10400.26/33553 |
url |
http://hdl.handle.net/10400.26/33553 |
dc.language.iso.fl_str_mv |
eng |
language |
eng |
dc.relation.none.fl_str_mv |
Oxford Medical Case Reports, 2018;8, 268–270 10.1093/omcr/omy054 10.1093/omcr/omy054 |
dc.rights.driver.fl_str_mv |
info:eu-repo/semantics/openAccess |
eu_rights_str_mv |
openAccess |
dc.format.none.fl_str_mv |
application/pdf |
dc.publisher.none.fl_str_mv |
Oxford University Press. |
publisher.none.fl_str_mv |
Oxford University Press. |
dc.source.none.fl_str_mv |
reponame:Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) instname:Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação instacron:RCAAP |
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Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
instacron_str |
RCAAP |
institution |
RCAAP |
reponame_str |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
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Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) |
repository.name.fl_str_mv |
Repositório Científico de Acesso Aberto de Portugal (Repositórios Cientìficos) - Agência para a Sociedade do Conhecimento (UMIC) - FCT - Sociedade da Informação |
repository.mail.fl_str_mv |
|
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1799134907054686208 |